Desmoplastic Small Round Cell Tumor of the testis: A rare tumor at an uncommon location

Desmoplastic Small Round Cell Tumor (DSRCT) is an aggressive neoplasm that classically grows in the peritoneal cavity and has poor prognosis. We describe a 13-year-old boy with testicular DSRCT, treated with orchiectomy and chemotherapy who is free of disease 102 months after diagnosis. This is the...

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Bibliographic Details
Main Authors: Fabrício Tera Romagnol, Maria Teresa de Seixas Alves, Marília Aparecida Silva Oliveira, Eny Guimarães Carvalho, Ana Maria Marinho da Silva, Eliana Maria Monteiro Caran
Format: Article
Language:English
Published: Elsevier 2021-09-01
Series:Pediatric Hematology Oncology Journal
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Online Access:http://www.sciencedirect.com/science/article/pii/S2468124521002084
Description
Summary:Desmoplastic Small Round Cell Tumor (DSRCT) is an aggressive neoplasm that classically grows in the peritoneal cavity and has poor prognosis. We describe a 13-year-old boy with testicular DSRCT, treated with orchiectomy and chemotherapy who is free of disease 102 months after diagnosis. This is the fifth case of primary DSRCT of the testis described in literature. Moreover, we present a literature review of 28 cases of testicular and paratesticular DSRCT.
ISSN:2468-1245