Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report

Background: Complete Congenital Heart Block (CCHB) is a rare disease of the newborn that carries significant morbidity and mortality. CCHB can be diagnosed early or late in life. In newborns, it is usually associated with maternal autoantibodies or a congenital cardiac structural abnormality. The mo...

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Main Authors: Mahmoud A. Kiblawi, Alina Naeem, Elham A. Al Attrash, Subhranshu Kar, B. K. M. Goud
Format: Article
Language:English
Published: University Library System, University of Pittsburgh 2013-12-01
Series:International Journal of Medical Students
Subjects:
Online Access:http://ijms.info/IJMS/article/view/220
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author Mahmoud A. Kiblawi
Alina Naeem
Elham A. Al Attrash
Subhranshu Kar
B. K. M. Goud
author_facet Mahmoud A. Kiblawi
Alina Naeem
Elham A. Al Attrash
Subhranshu Kar
B. K. M. Goud
author_sort Mahmoud A. Kiblawi
collection DOAJ
description Background: Complete Congenital Heart Block (CCHB) is a rare disease of the newborn that carries significant morbidity and mortality. CCHB can be diagnosed early or late in life. In newborns, it is usually associated with maternal autoantibodies or a congenital cardiac structural abnormality. The most common presentation of CCHB is bradycardia that can be diagnosed by an electrocardiogram. Results: This is a case report of a male infant born to a mother with an autoimmune disease, Systemic Lupus Erythematosus (SLE), who was found to have third degree heart block at birth. Conclusion: Early diagnosis and prompt management of the case is important for a better prog­nosis and prevention of associated complications. Neonates with CCHB should be managed at a tertiary care center and the only definite treatment is insertion of a pacemaker. Moreover, prenatal diagnosis and specific obstetric counseling of pregnant women with SLE along with careful monitoring with serial ultrasonography and echocardiography are of paramount importance in prevention of the disease in subsequent offspring.
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spelling doaj.art-30c31c4e548b42c08948dfab4e7381232023-09-03T01:54:17ZengUniversity Library System, University of PittsburghInternational Journal of Medical Students2076-63272013-12-011312813110.5195/ijms.2013.220220Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case ReportMahmoud A. Kiblawi0Alina Naeem1Elham A. Al Attrash2Subhranshu Kar3B. K. M. Goud4RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.Background: Complete Congenital Heart Block (CCHB) is a rare disease of the newborn that carries significant morbidity and mortality. CCHB can be diagnosed early or late in life. In newborns, it is usually associated with maternal autoantibodies or a congenital cardiac structural abnormality. The most common presentation of CCHB is bradycardia that can be diagnosed by an electrocardiogram. Results: This is a case report of a male infant born to a mother with an autoimmune disease, Systemic Lupus Erythematosus (SLE), who was found to have third degree heart block at birth. Conclusion: Early diagnosis and prompt management of the case is important for a better prog­nosis and prevention of associated complications. Neonates with CCHB should be managed at a tertiary care center and the only definite treatment is insertion of a pacemaker. Moreover, prenatal diagnosis and specific obstetric counseling of pregnant women with SLE along with careful monitoring with serial ultrasonography and echocardiography are of paramount importance in prevention of the disease in subsequent offspring.http://ijms.info/IJMS/article/view/220congenital heart blocksystemic lupus erythematosusbradycardiass-a antibodies
spellingShingle Mahmoud A. Kiblawi
Alina Naeem
Elham A. Al Attrash
Subhranshu Kar
B. K. M. Goud
Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report
International Journal of Medical Students
congenital heart block
systemic lupus erythematosus
bradycardia
ss-a antibodies
title Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report
title_full Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report
title_fullStr Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report
title_full_unstemmed Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report
title_short Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report
title_sort complete congenital heart block in a newborn associated with maternal systemic lupus erythematosus a case report
topic congenital heart block
systemic lupus erythematosus
bradycardia
ss-a antibodies
url http://ijms.info/IJMS/article/view/220
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