Anesthetic management for surgery of esophagus atresia in a newborn with Goldenhar's syndrome
<sec><title>BACKGROUND AND OBJECTIVES:</title><p> Goldenhar's syndrome is a polymalformative condition consisting of a craniofacial dysostosis that determines difficult airway in up to 40% of cases. We described a case of a newborn with Goldenhar's syndrome with eso...
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Sociedade Brasileira de Anestesiologia
2015-08-01
|
| Series: | Revista Brasileira de Anestesiologia |
| Subjects: | |
| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0034-70942015000400298&lng=en&tlng=en |
| _version_ | 1818127938621538304 |
|---|---|
| author | Rosana Guerrero-Domínguez Daniel López-Herrera-Rodríguez Inmaculada Benítez-Linero Antonio Ontanilla |
| author_facet | Rosana Guerrero-Domínguez Daniel López-Herrera-Rodríguez Inmaculada Benítez-Linero Antonio Ontanilla |
| author_sort | Rosana Guerrero-Domínguez |
| collection | DOAJ |
| description | <sec><title>BACKGROUND AND OBJECTIVES:</title><p> Goldenhar's syndrome is a polymalformative condition consisting of a craniofacial dysostosis that determines difficult airway in up to 40% of cases. We described a case of a newborn with Goldenhar's syndrome with esophageal atresia and tracheoesophageal fistula who underwent repair surgery.</p></sec><sec><title>CASE REPORT:</title><p> We report the case of a 24-h-old newborn with Goldenhar's syndrome. He had esophageal atresia with distal tracheoesophageal fistula. It was decided that an emergency surgery would be performed for repairing it. It was carried out under sedation, intubation with fibrobronchoscope distal to the fistula, to limit the air flow into the esophagus, and possible abdominal distension. Following complete repair of the esophageal atresia and fistula ligation, the patient was transferred to the intensive care unit and intubated under sedation and analgesia.</p></sec><sec><title>CONCLUSIONS:</title><p> The finding of a patient with Goldenhar's syndrome and esophageal atresia assumes an exceptional situation and a challenge for anesthesiologists, since the anesthetic management depends on the patient comorbidity, the type of tracheoesophageal fistula, the usual hospital practice and the skills of the anesthesiologist in charge, with the main peculiarity being maintenance of adequate pulmonary ventilation in the presence of a communication between the airway and the esophagus. Intubation with fibrobronchoscope distal to the fistula deals with the management of a probably difficult airway and limits the passage of air to the esophagus through the fistula.</p></sec> |
| first_indexed | 2024-12-11T07:25:18Z |
| format | Article |
| id | doaj.art-3151cdc33aac4197b957187aa095b5ec |
| institution | Directory Open Access Journal |
| issn | 1806-907X |
| language | English |
| last_indexed | 2024-12-11T07:25:18Z |
| publishDate | 2015-08-01 |
| publisher | Sociedade Brasileira de Anestesiologia |
| record_format | Article |
| series | Revista Brasileira de Anestesiologia |
| spelling | doaj.art-3151cdc33aac4197b957187aa095b5ec2022-12-22T01:15:59ZengSociedade Brasileira de AnestesiologiaRevista Brasileira de Anestesiologia1806-907X2015-08-0165429830110.1016/j.bjane.2013.07.011S0034-70942015000400298Anesthetic management for surgery of esophagus atresia in a newborn with Goldenhar's syndromeRosana Guerrero-DomínguezDaniel López-Herrera-RodríguezInmaculada Benítez-LineroAntonio Ontanilla<sec><title>BACKGROUND AND OBJECTIVES:</title><p> Goldenhar's syndrome is a polymalformative condition consisting of a craniofacial dysostosis that determines difficult airway in up to 40% of cases. We described a case of a newborn with Goldenhar's syndrome with esophageal atresia and tracheoesophageal fistula who underwent repair surgery.</p></sec><sec><title>CASE REPORT:</title><p> We report the case of a 24-h-old newborn with Goldenhar's syndrome. He had esophageal atresia with distal tracheoesophageal fistula. It was decided that an emergency surgery would be performed for repairing it. It was carried out under sedation, intubation with fibrobronchoscope distal to the fistula, to limit the air flow into the esophagus, and possible abdominal distension. Following complete repair of the esophageal atresia and fistula ligation, the patient was transferred to the intensive care unit and intubated under sedation and analgesia.</p></sec><sec><title>CONCLUSIONS:</title><p> The finding of a patient with Goldenhar's syndrome and esophageal atresia assumes an exceptional situation and a challenge for anesthesiologists, since the anesthetic management depends on the patient comorbidity, the type of tracheoesophageal fistula, the usual hospital practice and the skills of the anesthesiologist in charge, with the main peculiarity being maintenance of adequate pulmonary ventilation in the presence of a communication between the airway and the esophagus. Intubation with fibrobronchoscope distal to the fistula deals with the management of a probably difficult airway and limits the passage of air to the esophagus through the fistula.</p></sec>http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0034-70942015000400298&lng=en&tlng=enSíndrome de GoldenharFístula traqueoesofágicaAtresia de esófagoVía aérea difícilFibrobroncoscopio |
| spellingShingle | Rosana Guerrero-Domínguez Daniel López-Herrera-Rodríguez Inmaculada Benítez-Linero Antonio Ontanilla Anesthetic management for surgery of esophagus atresia in a newborn with Goldenhar's syndrome Revista Brasileira de Anestesiologia Síndrome de Goldenhar Fístula traqueoesofágica Atresia de esófago Vía aérea difícil Fibrobroncoscopio |
| title | Anesthetic management for surgery of esophagus atresia in a newborn with Goldenhar's syndrome |
| title_full | Anesthetic management for surgery of esophagus atresia in a newborn with Goldenhar's syndrome |
| title_fullStr | Anesthetic management for surgery of esophagus atresia in a newborn with Goldenhar's syndrome |
| title_full_unstemmed | Anesthetic management for surgery of esophagus atresia in a newborn with Goldenhar's syndrome |
| title_short | Anesthetic management for surgery of esophagus atresia in a newborn with Goldenhar's syndrome |
| title_sort | anesthetic management for surgery of esophagus atresia in a newborn with goldenhar s syndrome |
| topic | Síndrome de Goldenhar Fístula traqueoesofágica Atresia de esófago Vía aérea difícil Fibrobroncoscopio |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0034-70942015000400298&lng=en&tlng=en |
| work_keys_str_mv | AT rosanaguerrerodominguez anestheticmanagementforsurgeryofesophagusatresiainanewbornwithgoldenharssyndrome AT daniellopezherrerarodriguez anestheticmanagementforsurgeryofesophagusatresiainanewbornwithgoldenharssyndrome AT inmaculadabenitezlinero anestheticmanagementforsurgeryofesophagusatresiainanewbornwithgoldenharssyndrome AT antonioontanilla anestheticmanagementforsurgeryofesophagusatresiainanewbornwithgoldenharssyndrome |