“What lies beneath” – macrophage activation syndrome unveiled systemic lupus erythematosus
Macrophage activation syndrome (MAS) is a potentially fatal condition characterized by massive systemic inflammatory response in the setting of a myriad of systemic disorders such as autoimmune collagen vascular disease, infections, drug-induced, and malignancies. It falls under a group of disorders...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2021-01-01
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| Series: | Clinical Dermatology Review |
| Subjects: | |
| Online Access: | http://www.cdriadvlkn.org/article.asp?issn=2542-551X;year=2021;volume=5;issue=2;spage=236;epage=239;aulast= |
| _version_ | 1818727736430034944 |
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| author | J P Prathibha Vivek Pai P Ishwara Bhat |
| author_facet | J P Prathibha Vivek Pai P Ishwara Bhat |
| author_sort | J P Prathibha |
| collection | DOAJ |
| description | Macrophage activation syndrome (MAS) is a potentially fatal condition characterized by massive systemic inflammatory response in the setting of a myriad of systemic disorders such as autoimmune collagen vascular disease, infections, drug-induced, and malignancies. It falls under a group of disorders known as hemophagocytic lymphohistiocytosis of which familial and acquired types have been described. Here, we report a case of acquired MAS secondary to acute systemic lupus erythematosus (SLE). Early diagnosis and timely intervention resulted in a favorable outcome. |
| first_indexed | 2024-12-17T22:18:50Z |
| format | Article |
| id | doaj.art-31baaf2de1e04bb2a284129a004221cb |
| institution | Directory Open Access Journal |
| issn | 2542-551X 2542-5528 |
| language | English |
| last_indexed | 2024-12-17T22:18:50Z |
| publishDate | 2021-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Clinical Dermatology Review |
| spelling | doaj.art-31baaf2de1e04bb2a284129a004221cb2022-12-21T21:30:31ZengWolters Kluwer Medknow PublicationsClinical Dermatology Review2542-551X2542-55282021-01-015223623910.4103/CDR.CDR_87_20“What lies beneath” – macrophage activation syndrome unveiled systemic lupus erythematosusJ P PrathibhaVivek PaiP Ishwara BhatMacrophage activation syndrome (MAS) is a potentially fatal condition characterized by massive systemic inflammatory response in the setting of a myriad of systemic disorders such as autoimmune collagen vascular disease, infections, drug-induced, and malignancies. It falls under a group of disorders known as hemophagocytic lymphohistiocytosis of which familial and acquired types have been described. Here, we report a case of acquired MAS secondary to acute systemic lupus erythematosus (SLE). Early diagnosis and timely intervention resulted in a favorable outcome.http://www.cdriadvlkn.org/article.asp?issn=2542-551X;year=2021;volume=5;issue=2;spage=236;epage=239;aulast=hemophagocytic lymphohistiocytosismacrophage activation syndromesystemic lupus erythematosus (sle) |
| spellingShingle | J P Prathibha Vivek Pai P Ishwara Bhat “What lies beneath” – macrophage activation syndrome unveiled systemic lupus erythematosus Clinical Dermatology Review hemophagocytic lymphohistiocytosis macrophage activation syndrome systemic lupus erythematosus (sle) |
| title | “What lies beneath” – macrophage activation syndrome unveiled systemic lupus erythematosus |
| title_full | “What lies beneath” – macrophage activation syndrome unveiled systemic lupus erythematosus |
| title_fullStr | “What lies beneath” – macrophage activation syndrome unveiled systemic lupus erythematosus |
| title_full_unstemmed | “What lies beneath” – macrophage activation syndrome unveiled systemic lupus erythematosus |
| title_short | “What lies beneath” – macrophage activation syndrome unveiled systemic lupus erythematosus |
| title_sort | what lies beneath macrophage activation syndrome unveiled systemic lupus erythematosus |
| topic | hemophagocytic lymphohistiocytosis macrophage activation syndrome systemic lupus erythematosus (sle) |
| url | http://www.cdriadvlkn.org/article.asp?issn=2542-551X;year=2021;volume=5;issue=2;spage=236;epage=239;aulast= |
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