Restorative treatment in patient with Williams Syndrome: case report

ABSTRACT In Dentistry, any user with one or more limitations, of temporary or permanent mental nature, of physical, sensory, emotional or medical growth, is considered to be a Patient with Special Needs, preventing him from being subjected to a conventional dental situation. These patients form a gr...

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Main Authors: Alessandra RECH, Isadora Caron RINALDI, Tatiane MAREGA
Format: Article
Language:English
Published: Faculdade São Leopoldo Mandic 2022-09-01
Series:RGO: Revista Gaúcha de Odontologia
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372022000100809&tlng=en
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author Alessandra RECH
Isadora Caron RINALDI
Tatiane MAREGA
author_facet Alessandra RECH
Isadora Caron RINALDI
Tatiane MAREGA
author_sort Alessandra RECH
collection DOAJ
description ABSTRACT In Dentistry, any user with one or more limitations, of temporary or permanent mental nature, of physical, sensory, emotional or medical growth, is considered to be a Patient with Special Needs, preventing him from being subjected to a conventional dental situation. These patients form a group which may be considered at high risk for the development of oral diseases, according to the kind of pathogen. Among them, is the Williams-Beuren Syndrome, a rare congenital disease with cardiovascular involvement, mental retardation, dysmorphic face, idiopathic hypercalcemia, musculoskeletal problems, dental and growth anomalies. Familial and sporadic cases are thought to result from deletion of genetic material from adjacent genes located on the long arm of chromosome 7. This article reports a clinical case involving a four-year-old boy with Williams-Beuren Syndrome, referred to the clinic of the Specialization Course for Patients with Special Needs, at the São Leopoldo Mandic Dental Research Center, Campinas (SP). As the patient was resistant to dental care, in order to reduce anxiety and increase collaboration in clinical sessions, the Hixizine® medication was administered. For atraumatic restorative treatment and restorations, the following materials were used: Cleanjoy®, Futurabond DC®, Ionofil Plus® Grandioso®, Grandio® and Profluorid®. As result, it was possible to reach a level of excellence using the indicated materials and specific protocols. Based on this work and the lived experience, it can be observed that these patients can receive welcoming dental care in specialized clinics.
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spelling doaj.art-31c700ed71df438e8623575d37858c592023-06-28T23:16:43ZengFaculdade São Leopoldo MandicRGO: Revista Gaúcha de Odontologia1981-86372022-09-017010.1590/1981-86372022002620200155Restorative treatment in patient with Williams Syndrome: case reportAlessandra RECHhttps://orcid.org/0000-0002-7115-4846Isadora Caron RINALDIhttps://orcid.org/0000-0003-1864-5985Tatiane MAREGAhttps://orcid.org/0000-0002-0647-945XABSTRACT In Dentistry, any user with one or more limitations, of temporary or permanent mental nature, of physical, sensory, emotional or medical growth, is considered to be a Patient with Special Needs, preventing him from being subjected to a conventional dental situation. These patients form a group which may be considered at high risk for the development of oral diseases, according to the kind of pathogen. Among them, is the Williams-Beuren Syndrome, a rare congenital disease with cardiovascular involvement, mental retardation, dysmorphic face, idiopathic hypercalcemia, musculoskeletal problems, dental and growth anomalies. Familial and sporadic cases are thought to result from deletion of genetic material from adjacent genes located on the long arm of chromosome 7. This article reports a clinical case involving a four-year-old boy with Williams-Beuren Syndrome, referred to the clinic of the Specialization Course for Patients with Special Needs, at the São Leopoldo Mandic Dental Research Center, Campinas (SP). As the patient was resistant to dental care, in order to reduce anxiety and increase collaboration in clinical sessions, the Hixizine® medication was administered. For atraumatic restorative treatment and restorations, the following materials were used: Cleanjoy®, Futurabond DC®, Ionofil Plus® Grandioso®, Grandio® and Profluorid®. As result, it was possible to reach a level of excellence using the indicated materials and specific protocols. Based on this work and the lived experience, it can be observed that these patients can receive welcoming dental care in specialized clinics.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372022000100809&tlng=enDental atraumatic restorative treatmentPediatric dentistryWilliams Syndrome
spellingShingle Alessandra RECH
Isadora Caron RINALDI
Tatiane MAREGA
Restorative treatment in patient with Williams Syndrome: case report
RGO: Revista Gaúcha de Odontologia
Dental atraumatic restorative treatment
Pediatric dentistry
Williams Syndrome
title Restorative treatment in patient with Williams Syndrome: case report
title_full Restorative treatment in patient with Williams Syndrome: case report
title_fullStr Restorative treatment in patient with Williams Syndrome: case report
title_full_unstemmed Restorative treatment in patient with Williams Syndrome: case report
title_short Restorative treatment in patient with Williams Syndrome: case report
title_sort restorative treatment in patient with williams syndrome case report
topic Dental atraumatic restorative treatment
Pediatric dentistry
Williams Syndrome
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372022000100809&tlng=en
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AT tatianemarega restorativetreatmentinpatientwithwilliamssyndromecasereport