Herlyn-Werner-Wunderlich syndrome in a young female presenting with dysmenorrhea: A case report
Herlyn-Werner-Wunderlich (HWW) syndrome, popularly known by acronym of obstructed hemivagina with ipsilateral renal agenesis (OHVIRA) is a rare Müllerian and Wolffian duct anomaly. The syndrome is classically described as triad of uterine didelphy, obstructed hemivagina, and ipsilateral renal agenes...
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| Format: | Article |
| Language: | English |
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Elsevier
2024-01-01
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| Series: | Radiology Case Reports |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043323006672 |
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| author | Prajwal Dahal, MD Ongden Yonjen Tamang, MD Rudra Prasad Upadhyaya, MD Kapil Dawadi, MD Prajina Pradhan, MD Sabina Parajuli, MBBS |
| author_facet | Prajwal Dahal, MD Ongden Yonjen Tamang, MD Rudra Prasad Upadhyaya, MD Kapil Dawadi, MD Prajina Pradhan, MD Sabina Parajuli, MBBS |
| author_sort | Prajwal Dahal, MD |
| collection | DOAJ |
| description | Herlyn-Werner-Wunderlich (HWW) syndrome, popularly known by acronym of obstructed hemivagina with ipsilateral renal agenesis (OHVIRA) is a rare Müllerian and Wolffian duct anomaly. The syndrome is classically described as triad of uterine didelphy, obstructed hemivagina, and ipsilateral renal agenesis. The symptoms are seen after menarche. Clinically, the patients present with dysmenorrhea, palpable paravaginal mass, increased frequency of micturition heaviness in pelvis and sometimes with infertility after marriage. Imaging is the cornerstone for diagnosis of the condition. Radiologists should screen for Müllerian duct anomaly if unilateral renal agenesis is detected and vice versa. Early diagnosis and surgical intervention help in prevention of complications like endometriosis, adhesions in lesser pelvis, infertility, pyosalpinx, abscess, and hematoma of cervix and vagina. We present a case of HWW syndrome in an adolescent female visiting the emergency department with complaint of dysmenorrhea. We diagnosed the case in ultrasonography (US) and confirmed in MRI. |
| first_indexed | 2024-03-09T15:40:39Z |
| format | Article |
| id | doaj.art-32fb7828eb4045cca2f131dda3f16be2 |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-03-09T15:40:39Z |
| publishDate | 2024-01-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-32fb7828eb4045cca2f131dda3f16be22023-11-25T04:47:16ZengElsevierRadiology Case Reports1930-04332024-01-011918288Herlyn-Werner-Wunderlich syndrome in a young female presenting with dysmenorrhea: A case reportPrajwal Dahal, MD0Ongden Yonjen Tamang, MD1Rudra Prasad Upadhyaya, MD2Kapil Dawadi, MD3Prajina Pradhan, MD4Sabina Parajuli, MBBS5Department of Radiology and Imaging, Grande International Hospital, Kathmandu, Nepal; Corresponding author.Department of Radiology and Imaging, Grande International Hospital, Kathmandu, NepalDepartment of Radiology and Imaging, Grande International Hospital, Kathmandu, NepalDepartment of Radiology and Imaging, Grande International Hospital, Kathmandu, NepalDepartment of Radiology and Imaging, Grande International Hospital, Kathmandu, NepalDepartment of Pathology, Bir Hospital, Kathmandu, NepalHerlyn-Werner-Wunderlich (HWW) syndrome, popularly known by acronym of obstructed hemivagina with ipsilateral renal agenesis (OHVIRA) is a rare Müllerian and Wolffian duct anomaly. The syndrome is classically described as triad of uterine didelphy, obstructed hemivagina, and ipsilateral renal agenesis. The symptoms are seen after menarche. Clinically, the patients present with dysmenorrhea, palpable paravaginal mass, increased frequency of micturition heaviness in pelvis and sometimes with infertility after marriage. Imaging is the cornerstone for diagnosis of the condition. Radiologists should screen for Müllerian duct anomaly if unilateral renal agenesis is detected and vice versa. Early diagnosis and surgical intervention help in prevention of complications like endometriosis, adhesions in lesser pelvis, infertility, pyosalpinx, abscess, and hematoma of cervix and vagina. We present a case of HWW syndrome in an adolescent female visiting the emergency department with complaint of dysmenorrhea. We diagnosed the case in ultrasonography (US) and confirmed in MRI.http://www.sciencedirect.com/science/article/pii/S1930043323006672Herlyn-Werner-Wunderlich (HWW)Müllerian ductObstructed hemivagina with ipsilateral renal agenesis (OHVIRA)Pyosalpinx |
| spellingShingle | Prajwal Dahal, MD Ongden Yonjen Tamang, MD Rudra Prasad Upadhyaya, MD Kapil Dawadi, MD Prajina Pradhan, MD Sabina Parajuli, MBBS Herlyn-Werner-Wunderlich syndrome in a young female presenting with dysmenorrhea: A case report Radiology Case Reports Herlyn-Werner-Wunderlich (HWW) Müllerian duct Obstructed hemivagina with ipsilateral renal agenesis (OHVIRA) Pyosalpinx |
| title | Herlyn-Werner-Wunderlich syndrome in a young female presenting with dysmenorrhea: A case report |
| title_full | Herlyn-Werner-Wunderlich syndrome in a young female presenting with dysmenorrhea: A case report |
| title_fullStr | Herlyn-Werner-Wunderlich syndrome in a young female presenting with dysmenorrhea: A case report |
| title_full_unstemmed | Herlyn-Werner-Wunderlich syndrome in a young female presenting with dysmenorrhea: A case report |
| title_short | Herlyn-Werner-Wunderlich syndrome in a young female presenting with dysmenorrhea: A case report |
| title_sort | herlyn werner wunderlich syndrome in a young female presenting with dysmenorrhea a case report |
| topic | Herlyn-Werner-Wunderlich (HWW) Müllerian duct Obstructed hemivagina with ipsilateral renal agenesis (OHVIRA) Pyosalpinx |
| url | http://www.sciencedirect.com/science/article/pii/S1930043323006672 |
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