Skin symptoms as diagnostic clue for autoinflammatory diseases
ABSTRACT Autoinflammatory disorders are immune-mediated diseases with increased production of inflammatory cytokines and absence of detectable autoantibodies. They course with recurrent episodes of systemic inflammation and fever is the most common symptom. Cutaneous manifestations are prevalent and...
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Format: | Article |
Language: | English |
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Sociedade Brasileira de Dermatologia
2017-02-01
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Series: | Anais Brasileiros de Dermatologia |
Subjects: | |
Online Access: | http://www.scielo.br/pdf/abd/v92n1/0365-0596-abd-92-01-0072.pdf |
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author | Alvaro Moreira Barbara Torres Juliano Peruzzo Alberto Mota Kilian Eyerich Johannes Ring |
author_facet | Alvaro Moreira Barbara Torres Juliano Peruzzo Alberto Mota Kilian Eyerich Johannes Ring |
author_sort | Alvaro Moreira |
collection | DOAJ |
description | ABSTRACT Autoinflammatory disorders are immune-mediated diseases with increased production of inflammatory cytokines and absence of detectable autoantibodies. They course with recurrent episodes of systemic inflammation and fever is the most common symptom. Cutaneous manifestations are prevalent and important to diagnosis and early treatment of the syndromes. The purpose of this review is to emphasize to dermatologists the skin symptoms present in these syndromes in order to provide their early diagnosis. |
first_indexed | 2024-12-18T02:30:17Z |
format | Article |
id | doaj.art-33bed5a9c4f94e9a892b35883ec6bdb1 |
institution | Directory Open Access Journal |
issn | 0365-0596 |
language | English |
last_indexed | 2024-12-18T02:30:17Z |
publishDate | 2017-02-01 |
publisher | Sociedade Brasileira de Dermatologia |
record_format | Article |
series | Anais Brasileiros de Dermatologia |
spelling | doaj.art-33bed5a9c4f94e9a892b35883ec6bdb12022-12-21T21:23:55ZengSociedade Brasileira de DermatologiaAnais Brasileiros de Dermatologia0365-05962017-02-01921728010.1590/abd1806-4841.20175208Skin symptoms as diagnostic clue for autoinflammatory diseasesAlvaro MoreiraBarbara TorresJuliano PeruzzoAlberto MotaKilian EyerichJohannes RingABSTRACT Autoinflammatory disorders are immune-mediated diseases with increased production of inflammatory cytokines and absence of detectable autoantibodies. They course with recurrent episodes of systemic inflammation and fever is the most common symptom. Cutaneous manifestations are prevalent and important to diagnosis and early treatment of the syndromes. The purpose of this review is to emphasize to dermatologists the skin symptoms present in these syndromes in order to provide their early diagnosis.http://www.scielo.br/pdf/abd/v92n1/0365-0596-abd-92-01-0072.pdfAcquired hyperostosis syndromeBehçet syndromeCryopyrin-associated periodic syndromesFamilial mediterranean feverMevalonate kinase deficiencyStill's disease, adult-onsetSchnitzler syndromeSweet syndromeHereditary autoinflammatory diseasesTumor necrosis factor receptor-associated peptides and proteins |
spellingShingle | Alvaro Moreira Barbara Torres Juliano Peruzzo Alberto Mota Kilian Eyerich Johannes Ring Skin symptoms as diagnostic clue for autoinflammatory diseases Anais Brasileiros de Dermatologia Acquired hyperostosis syndrome Behçet syndrome Cryopyrin-associated periodic syndromes Familial mediterranean fever Mevalonate kinase deficiency Still's disease, adult-onset Schnitzler syndrome Sweet syndrome Hereditary autoinflammatory diseases Tumor necrosis factor receptor-associated peptides and proteins |
title | Skin symptoms as diagnostic clue for autoinflammatory diseases |
title_full | Skin symptoms as diagnostic clue for autoinflammatory diseases |
title_fullStr | Skin symptoms as diagnostic clue for autoinflammatory diseases |
title_full_unstemmed | Skin symptoms as diagnostic clue for autoinflammatory diseases |
title_short | Skin symptoms as diagnostic clue for autoinflammatory diseases |
title_sort | skin symptoms as diagnostic clue for autoinflammatory diseases |
topic | Acquired hyperostosis syndrome Behçet syndrome Cryopyrin-associated periodic syndromes Familial mediterranean fever Mevalonate kinase deficiency Still's disease, adult-onset Schnitzler syndrome Sweet syndrome Hereditary autoinflammatory diseases Tumor necrosis factor receptor-associated peptides and proteins |
url | http://www.scielo.br/pdf/abd/v92n1/0365-0596-abd-92-01-0072.pdf |
work_keys_str_mv | AT alvaromoreira skinsymptomsasdiagnosticclueforautoinflammatorydiseases AT barbaratorres skinsymptomsasdiagnosticclueforautoinflammatorydiseases AT julianoperuzzo skinsymptomsasdiagnosticclueforautoinflammatorydiseases AT albertomota skinsymptomsasdiagnosticclueforautoinflammatorydiseases AT kilianeyerich skinsymptomsasdiagnosticclueforautoinflammatorydiseases AT johannesring skinsymptomsasdiagnosticclueforautoinflammatorydiseases |