Congenital High Airway Obstructive Syndrome (CHAOS) Survival of a Newborn with Laryngeal Atresia
Congenital high airway obstructive syndrome (CHAOS) is a rare congenital anomaly, frequently caused by laryngeal or tracheal atresia, tracheal stenosis, and obstructing laryngeal cysts. This is a congenital malformation, often fatal, with an unknown prevalence. Laryngeal atresia is the most frequent...
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MDPI AG
2023-12-01
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| Series: | Diagnostics |
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| Online Access: | https://www.mdpi.com/2075-4418/13/24/3658 |
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| author | Carmen Heriseanu Mihaela Bizubac Loredana Draghia Veronica Marcu Dan Gheorghe Catalin Cirstoveanu |
| author_facet | Carmen Heriseanu Mihaela Bizubac Loredana Draghia Veronica Marcu Dan Gheorghe Catalin Cirstoveanu |
| author_sort | Carmen Heriseanu |
| collection | DOAJ |
| description | Congenital high airway obstructive syndrome (CHAOS) is a rare congenital anomaly, frequently caused by laryngeal or tracheal atresia, tracheal stenosis, and obstructing laryngeal cysts. This is a congenital malformation, often fatal, with an unknown prevalence. Laryngeal atresia is the most frequent cause. We report a case of an intrauterine diagnosis of CHAOS and ascites in a 17-week fetus delivered at 38 weeks of gestation without other associated malformations. A fetoscopic procedure was performed at 22 weeks of gestation. An attempt was made to perforate the affected area to ensure pulmonary fluid circulation and the ascites’ resolution. After birth, a tracheostomy was performed. The patient was mechanically ventilated until 11 months of age, when she was discharged with no cerebral or other complications of immediate postnatal anoxia or episodes of respiratory arrest. A laryngotracheoplasty was performed at 2 years old, but decannulation was not possible due to certain complications. At 5 years old, a new surgical intervention was performed, which allowed decannulation 6 months later. |
| first_indexed | 2024-03-08T20:51:34Z |
| format | Article |
| id | doaj.art-3464313725444341b70523afbdcfe817 |
| institution | Directory Open Access Journal |
| issn | 2075-4418 |
| language | English |
| last_indexed | 2024-03-08T20:51:34Z |
| publishDate | 2023-12-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Diagnostics |
| spelling | doaj.art-3464313725444341b70523afbdcfe8172023-12-22T14:03:14ZengMDPI AGDiagnostics2075-44182023-12-011324365810.3390/diagnostics13243658Congenital High Airway Obstructive Syndrome (CHAOS) Survival of a Newborn with Laryngeal AtresiaCarmen Heriseanu0Mihaela Bizubac1Loredana Draghia2Veronica Marcu3Dan Gheorghe4Catalin Cirstoveanu5Neonatal Intensive Care Unit, “M.S. Curie” Children’s Hospital, Constantin Brâncoveanu Boulevard, No. 20, 4th District, 041451 Bucharest, RomaniaNeonatal Intensive Care Unit, “M.S. Curie” Children’s Hospital, Constantin Brâncoveanu Boulevard, No. 20, 4th District, 041451 Bucharest, RomaniaNeonatal Intensive Care Unit, “M.S. Curie” Children’s Hospital, Constantin Brâncoveanu Boulevard, No. 20, 4th District, 041451 Bucharest, RomaniaDepartment of Radiology, “M.S. Curie” Children’s Hospital, Constantin Brâncoveanu Boulevard, No. 20, 4th District, 041451 Bucharest, RomaniaDepartment of ENT, “Carol Davila” University of Medicine and Pharmacy, 020021 Bucharest, RomaniaNeonatal Intensive Care Unit, “M.S. Curie” Children’s Hospital, Constantin Brâncoveanu Boulevard, No. 20, 4th District, 041451 Bucharest, RomaniaCongenital high airway obstructive syndrome (CHAOS) is a rare congenital anomaly, frequently caused by laryngeal or tracheal atresia, tracheal stenosis, and obstructing laryngeal cysts. This is a congenital malformation, often fatal, with an unknown prevalence. Laryngeal atresia is the most frequent cause. We report a case of an intrauterine diagnosis of CHAOS and ascites in a 17-week fetus delivered at 38 weeks of gestation without other associated malformations. A fetoscopic procedure was performed at 22 weeks of gestation. An attempt was made to perforate the affected area to ensure pulmonary fluid circulation and the ascites’ resolution. After birth, a tracheostomy was performed. The patient was mechanically ventilated until 11 months of age, when she was discharged with no cerebral or other complications of immediate postnatal anoxia or episodes of respiratory arrest. A laryngotracheoplasty was performed at 2 years old, but decannulation was not possible due to certain complications. At 5 years old, a new surgical intervention was performed, which allowed decannulation 6 months later.https://www.mdpi.com/2075-4418/13/24/3658CHAOSlaryngeal atresiafetoscopytracheostomylaryngotracheoplasty |
| spellingShingle | Carmen Heriseanu Mihaela Bizubac Loredana Draghia Veronica Marcu Dan Gheorghe Catalin Cirstoveanu Congenital High Airway Obstructive Syndrome (CHAOS) Survival of a Newborn with Laryngeal Atresia Diagnostics CHAOS laryngeal atresia fetoscopy tracheostomy laryngotracheoplasty |
| title | Congenital High Airway Obstructive Syndrome (CHAOS) Survival of a Newborn with Laryngeal Atresia |
| title_full | Congenital High Airway Obstructive Syndrome (CHAOS) Survival of a Newborn with Laryngeal Atresia |
| title_fullStr | Congenital High Airway Obstructive Syndrome (CHAOS) Survival of a Newborn with Laryngeal Atresia |
| title_full_unstemmed | Congenital High Airway Obstructive Syndrome (CHAOS) Survival of a Newborn with Laryngeal Atresia |
| title_short | Congenital High Airway Obstructive Syndrome (CHAOS) Survival of a Newborn with Laryngeal Atresia |
| title_sort | congenital high airway obstructive syndrome chaos survival of a newborn with laryngeal atresia |
| topic | CHAOS laryngeal atresia fetoscopy tracheostomy laryngotracheoplasty |
| url | https://www.mdpi.com/2075-4418/13/24/3658 |
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