Vaso-vagal Syncope (VVS) after Mydriatic Eyedrops in Cutaneous and Intracranial Vascular Deformations (Pascual-Castroviejo Syndrome Type II)

Purpose: To present a case of vaso-vagal syncope (VVS) after mydriatic eye drops in a patient with cutaneous hemangioma and intracerebral vascular abnormalities. Case report: A 41-year old woman presented to an ophthalmology clinic complaining of near vision disturbance. On examination...

Full description

Bibliographic Details
Main Authors: Sarah A Alowedi, Abdullah Qahtani, Reinaldo A Garcia, J Fernando Arevalo
Format: Article
Language:English
Published: Pan-American Association of Ophthalmology 2017-04-01
Series:Vision Pan-America
Subjects:
Online Access:http://journals.sfu.ca/paao/index.php/journal/article/view/405
_version_ 1819238955073142784
author Sarah A Alowedi
Abdullah Qahtani
Reinaldo A Garcia
J Fernando Arevalo
author_facet Sarah A Alowedi
Abdullah Qahtani
Reinaldo A Garcia
J Fernando Arevalo
author_sort Sarah A Alowedi
collection DOAJ
description Purpose: To present a case of vaso-vagal syncope (VVS) after mydriatic eye drops in a patient with cutaneous hemangioma and intracerebral vascular abnormalities. Case report: A 41-year old woman presented to an ophthalmology clinic complaining of near vision disturbance. On examination, there was dilatation and telangiectasis of the conjunctival vessels on the temporal side of the right eye associated with right hemicranial and neck cutaneous involuted hemangioma ipsilateral to the conjunctival lesion. The patient experienced vaso-vagal syncope for approximately 15 minutes after mydriatic eye drops, 2 months prior to presentation. A magnetic resonance angiogram (MRA) showed right hypoplasia of the lateral and sigmoideus venous sinus ipsilateral to the external right hemangioma with predominantly compensatory drainage at the contralateral left system. At the neck vessels, the MRA showed dominant drainage through the lateral and jugular left sinus by the hypoplasia of the contralateral right system. Conclusion: This case shows the association of telangiectasis of the conjunctiva, and cutaneous hemangiomas of the head and neck with anomalies involving the central nervous system (CNS) as described by Pascual-Castroviejo in 1978, which they called cutaneous hemangioma– vascular complex syndrome. The diagnosis was made after the patient experienced VVS after mydriatic eyedrops instillation.
first_indexed 2024-12-23T13:44:26Z
format Article
id doaj.art-34871ef50d51479086140917fbd5ce5b
institution Directory Open Access Journal
issn 2219-4665
2219-4673
language English
last_indexed 2024-12-23T13:44:26Z
publishDate 2017-04-01
publisher Pan-American Association of Ophthalmology
record_format Article
series Vision Pan-America
spelling doaj.art-34871ef50d51479086140917fbd5ce5b2022-12-21T17:44:46ZengPan-American Association of OphthalmologyVision Pan-America2219-46652219-46732017-04-01161283010.15234/vpa.v1i1.405275Vaso-vagal Syncope (VVS) after Mydriatic Eyedrops in Cutaneous and Intracranial Vascular Deformations (Pascual-Castroviejo Syndrome Type II)Sarah A Alowedi0Abdullah Qahtani1Reinaldo A Garcia2J Fernando Arevalo3Retina Division at King Khaled Eye Specialist Hospital, Riyadh, Kingdom of Saudi Arabia. King Abdulaziz University, Jeddah, Saudi ArabiaRetina Division at King Khaled Eye Specialist Hospital, Riyadh, Kingdom of Saudi Arabia.Retina and Vitreous Service, Clinica Oftalmológica Centro Caracas, Caracas, Venezuela. Arevalo-Coutinho Foundation for Research in Ophthalmology, Caracas, Venezuela.Retina Division, Wilmer Eye Institute, Johns Hopkins University School of Medicine, Baltimore, MD, USA.Purpose: To present a case of vaso-vagal syncope (VVS) after mydriatic eye drops in a patient with cutaneous hemangioma and intracerebral vascular abnormalities. Case report: A 41-year old woman presented to an ophthalmology clinic complaining of near vision disturbance. On examination, there was dilatation and telangiectasis of the conjunctival vessels on the temporal side of the right eye associated with right hemicranial and neck cutaneous involuted hemangioma ipsilateral to the conjunctival lesion. The patient experienced vaso-vagal syncope for approximately 15 minutes after mydriatic eye drops, 2 months prior to presentation. A magnetic resonance angiogram (MRA) showed right hypoplasia of the lateral and sigmoideus venous sinus ipsilateral to the external right hemangioma with predominantly compensatory drainage at the contralateral left system. At the neck vessels, the MRA showed dominant drainage through the lateral and jugular left sinus by the hypoplasia of the contralateral right system. Conclusion: This case shows the association of telangiectasis of the conjunctiva, and cutaneous hemangiomas of the head and neck with anomalies involving the central nervous system (CNS) as described by Pascual-Castroviejo in 1978, which they called cutaneous hemangioma– vascular complex syndrome. The diagnosis was made after the patient experienced VVS after mydriatic eyedrops instillation.http://journals.sfu.ca/paao/index.php/journal/article/view/405Vaso-vagal syncopecutaneous hemangioma-vascular complex syndromemydriasis.
spellingShingle Sarah A Alowedi
Abdullah Qahtani
Reinaldo A Garcia
J Fernando Arevalo
Vaso-vagal Syncope (VVS) after Mydriatic Eyedrops in Cutaneous and Intracranial Vascular Deformations (Pascual-Castroviejo Syndrome Type II)
Vision Pan-America
Vaso-vagal syncope
cutaneous hemangioma-vascular complex syndrome
mydriasis.
title Vaso-vagal Syncope (VVS) after Mydriatic Eyedrops in Cutaneous and Intracranial Vascular Deformations (Pascual-Castroviejo Syndrome Type II)
title_full Vaso-vagal Syncope (VVS) after Mydriatic Eyedrops in Cutaneous and Intracranial Vascular Deformations (Pascual-Castroviejo Syndrome Type II)
title_fullStr Vaso-vagal Syncope (VVS) after Mydriatic Eyedrops in Cutaneous and Intracranial Vascular Deformations (Pascual-Castroviejo Syndrome Type II)
title_full_unstemmed Vaso-vagal Syncope (VVS) after Mydriatic Eyedrops in Cutaneous and Intracranial Vascular Deformations (Pascual-Castroviejo Syndrome Type II)
title_short Vaso-vagal Syncope (VVS) after Mydriatic Eyedrops in Cutaneous and Intracranial Vascular Deformations (Pascual-Castroviejo Syndrome Type II)
title_sort vaso vagal syncope vvs after mydriatic eyedrops in cutaneous and intracranial vascular deformations pascual castroviejo syndrome type ii
topic Vaso-vagal syncope
cutaneous hemangioma-vascular complex syndrome
mydriasis.
url http://journals.sfu.ca/paao/index.php/journal/article/view/405
work_keys_str_mv AT sarahaalowedi vasovagalsyncopevvsaftermydriaticeyedropsincutaneousandintracranialvasculardeformationspascualcastroviejosyndrometypeii
AT abdullahqahtani vasovagalsyncopevvsaftermydriaticeyedropsincutaneousandintracranialvasculardeformationspascualcastroviejosyndrometypeii
AT reinaldoagarcia vasovagalsyncopevvsaftermydriaticeyedropsincutaneousandintracranialvasculardeformationspascualcastroviejosyndrometypeii
AT jfernandoarevalo vasovagalsyncopevvsaftermydriaticeyedropsincutaneousandintracranialvasculardeformationspascualcastroviejosyndrometypeii