A rare case of postoperative pain in congenital analgesia: case report
Objective: we describe a case of a patient with familial dysautonomia and postoperative pain. Methodology: clinical follow-up for 10 years in a tertiary pediatric hospital. Results: it is a 12 years old teenager, diagnosed with Riley-Day Syndrome, after undergoing various orthopedic surgical procedu...
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Format: | Article |
Language: | English |
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Universidade Federal do Ceará
2023-07-01
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Series: | Revista de Medicina da UFC |
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Online Access: | http://periodicos.ufc.br/revistademedicinadaufc/article/view/71305 |
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author | André Lavor Alves Flávio Lobo Maia Washington Aspilicueta Pinto Filho Pinto Filho João Lucas Ferreira da Silva Joaquim Trajano de Lima Filho |
author_facet | André Lavor Alves Flávio Lobo Maia Washington Aspilicueta Pinto Filho Pinto Filho João Lucas Ferreira da Silva Joaquim Trajano de Lima Filho |
author_sort | André Lavor Alves |
collection | DOAJ |
description | Objective: we describe a case of a patient with familial dysautonomia and postoperative pain. Methodology: clinical follow-up for 10 years in a tertiary pediatric hospital. Results: it is a 12 years old teenager, diagnosed with Riley-Day Syndrome, after undergoing various orthopedic surgical procedures, evolves with changes in pain perception, in systematic assessments. Conclusion: Family Disautonomy is one of the most common Hereditary Sensory and Autonomic Neuropathies (HSAN). Children gradually evolve with sensory changes, leading to a progressive decrease in pain perception. In addition, spinal deformities and recurrent orthopedic trauma can occur. The reported patient presents, contradictorily, an increase in the perception of pain and allodynia after undergoing repetitive orthopedic procedures. |
first_indexed | 2024-03-12T14:57:20Z |
format | Article |
id | doaj.art-35b0d676721244a591495ea52133df20 |
institution | Directory Open Access Journal |
issn | 0100-1302 2447-6595 |
language | English |
last_indexed | 2024-03-12T14:57:20Z |
publishDate | 2023-07-01 |
publisher | Universidade Federal do Ceará |
record_format | Article |
series | Revista de Medicina da UFC |
spelling | doaj.art-35b0d676721244a591495ea52133df202023-08-14T11:48:47ZengUniversidade Federal do CearáRevista de Medicina da UFC0100-13022447-65952023-07-016311310.20513/2447-6595.2023v63n1e71305p1-371305A rare case of postoperative pain in congenital analgesia: case reportAndré Lavor Alves0Flávio Lobo Maia1Washington Aspilicueta Pinto Filho Pinto Filho2João Lucas Ferreira da Silva3Joaquim Trajano de Lima Filho4Hospital Universitário Walter Cantídio (HUWC)Hospital Universitário Walter Cantídio (HUWC)Hospital Infantil Albert Sabin (HIAS)Hospital Universitário Walter Cantídio (HUWC)Hospital Universitário Walter Cantídio (HUWC)Objective: we describe a case of a patient with familial dysautonomia and postoperative pain. Methodology: clinical follow-up for 10 years in a tertiary pediatric hospital. Results: it is a 12 years old teenager, diagnosed with Riley-Day Syndrome, after undergoing various orthopedic surgical procedures, evolves with changes in pain perception, in systematic assessments. Conclusion: Family Disautonomy is one of the most common Hereditary Sensory and Autonomic Neuropathies (HSAN). Children gradually evolve with sensory changes, leading to a progressive decrease in pain perception. In addition, spinal deformities and recurrent orthopedic trauma can occur. The reported patient presents, contradictorily, an increase in the perception of pain and allodynia after undergoing repetitive orthopedic procedures.http://periodicos.ufc.br/revistademedicinadaufc/article/view/71305dysautonomia, familialhereditary sensory and autonomic neuropathiespediatricspain, postoperative |
spellingShingle | André Lavor Alves Flávio Lobo Maia Washington Aspilicueta Pinto Filho Pinto Filho João Lucas Ferreira da Silva Joaquim Trajano de Lima Filho A rare case of postoperative pain in congenital analgesia: case report Revista de Medicina da UFC dysautonomia, familial hereditary sensory and autonomic neuropathies pediatrics pain, postoperative |
title | A rare case of postoperative pain in congenital analgesia: case report |
title_full | A rare case of postoperative pain in congenital analgesia: case report |
title_fullStr | A rare case of postoperative pain in congenital analgesia: case report |
title_full_unstemmed | A rare case of postoperative pain in congenital analgesia: case report |
title_short | A rare case of postoperative pain in congenital analgesia: case report |
title_sort | rare case of postoperative pain in congenital analgesia case report |
topic | dysautonomia, familial hereditary sensory and autonomic neuropathies pediatrics pain, postoperative |
url | http://periodicos.ufc.br/revistademedicinadaufc/article/view/71305 |
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