A rare case of postoperative pain in congenital analgesia: case report

Objective: we describe a case of a patient with familial dysautonomia and postoperative pain. Methodology: clinical follow-up for 10 years in a tertiary pediatric hospital. Results: it is a 12 years old teenager, diagnosed with Riley-Day Syndrome, after undergoing various orthopedic surgical procedu...

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Main Authors: André Lavor Alves, Flávio Lobo Maia, Washington Aspilicueta Pinto Filho Pinto Filho, João Lucas Ferreira da Silva, Joaquim Trajano de Lima Filho
Format: Article
Language:English
Published: Universidade Federal do Ceará 2023-07-01
Series:Revista de Medicina da UFC
Subjects:
Online Access:http://periodicos.ufc.br/revistademedicinadaufc/article/view/71305
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author André Lavor Alves
Flávio Lobo Maia
Washington Aspilicueta Pinto Filho Pinto Filho
João Lucas Ferreira da Silva
Joaquim Trajano de Lima Filho
author_facet André Lavor Alves
Flávio Lobo Maia
Washington Aspilicueta Pinto Filho Pinto Filho
João Lucas Ferreira da Silva
Joaquim Trajano de Lima Filho
author_sort André Lavor Alves
collection DOAJ
description Objective: we describe a case of a patient with familial dysautonomia and postoperative pain. Methodology: clinical follow-up for 10 years in a tertiary pediatric hospital. Results: it is a 12 years old teenager, diagnosed with Riley-Day Syndrome, after undergoing various orthopedic surgical procedures, evolves with changes in pain perception, in systematic assessments. Conclusion: Family Disautonomy is one of the most common Hereditary Sensory and Autonomic Neuropathies (HSAN). Children gradually evolve with sensory changes, leading to a progressive decrease in pain perception. In addition, spinal deformities and recurrent orthopedic trauma can occur. The reported patient presents, contradictorily, an increase in the perception of pain and allodynia after undergoing repetitive orthopedic procedures.
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spelling doaj.art-35b0d676721244a591495ea52133df202023-08-14T11:48:47ZengUniversidade Federal do CearáRevista de Medicina da UFC0100-13022447-65952023-07-016311310.20513/2447-6595.2023v63n1e71305p1-371305A rare case of postoperative pain in congenital analgesia: case reportAndré Lavor Alves0Flávio Lobo Maia1Washington Aspilicueta Pinto Filho Pinto Filho2João Lucas Ferreira da Silva3Joaquim Trajano de Lima Filho4Hospital Universitário Walter Cantídio (HUWC)Hospital Universitário Walter Cantídio (HUWC)Hospital Infantil Albert Sabin (HIAS)Hospital Universitário Walter Cantídio (HUWC)Hospital Universitário Walter Cantídio (HUWC)Objective: we describe a case of a patient with familial dysautonomia and postoperative pain. Methodology: clinical follow-up for 10 years in a tertiary pediatric hospital. Results: it is a 12 years old teenager, diagnosed with Riley-Day Syndrome, after undergoing various orthopedic surgical procedures, evolves with changes in pain perception, in systematic assessments. Conclusion: Family Disautonomy is one of the most common Hereditary Sensory and Autonomic Neuropathies (HSAN). Children gradually evolve with sensory changes, leading to a progressive decrease in pain perception. In addition, spinal deformities and recurrent orthopedic trauma can occur. The reported patient presents, contradictorily, an increase in the perception of pain and allodynia after undergoing repetitive orthopedic procedures.http://periodicos.ufc.br/revistademedicinadaufc/article/view/71305dysautonomia, familialhereditary sensory and autonomic neuropathiespediatricspain, postoperative
spellingShingle André Lavor Alves
Flávio Lobo Maia
Washington Aspilicueta Pinto Filho Pinto Filho
João Lucas Ferreira da Silva
Joaquim Trajano de Lima Filho
A rare case of postoperative pain in congenital analgesia: case report
Revista de Medicina da UFC
dysautonomia, familial
hereditary sensory and autonomic neuropathies
pediatrics
pain, postoperative
title A rare case of postoperative pain in congenital analgesia: case report
title_full A rare case of postoperative pain in congenital analgesia: case report
title_fullStr A rare case of postoperative pain in congenital analgesia: case report
title_full_unstemmed A rare case of postoperative pain in congenital analgesia: case report
title_short A rare case of postoperative pain in congenital analgesia: case report
title_sort rare case of postoperative pain in congenital analgesia case report
topic dysautonomia, familial
hereditary sensory and autonomic neuropathies
pediatrics
pain, postoperative
url http://periodicos.ufc.br/revistademedicinadaufc/article/view/71305
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