MAJEWSKI OSTEODYSPLASTIC PRIMORDIAL DWARFISM TYPE II: CLINICAL FINDINGS AND DENTAL MANAGEMENT OF A CHILD PATIENT
Majewski osteodysplastic primordial dwarfism type II (MOPD II) is an unusual autosomal recessive inherited form of primordial dwarfism, which is characterized by a small head diameter at birth, but which also progresses to severe microcephaly, progressive bony dysplasia, and characteristic facies an...
| Main Authors: | , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Istanbul University
2015-01-01
|
| Series: | Journal of Istanbul University Faculty of Dentistry |
| Subjects: | |
| Online Access: | http://www.journals.istanbul.edu.tr/iudis/article/view/1023021632/5000101124 |
| _version_ | 1828026060764086272 |
|---|---|
| author | Arslan Terlemez Mustafa Altunsoy Hakkı Çelebi |
| author_facet | Arslan Terlemez Mustafa Altunsoy Hakkı Çelebi |
| author_sort | Arslan Terlemez |
| collection | DOAJ |
| description | Majewski osteodysplastic primordial dwarfism type II (MOPD II) is an unusual autosomal recessive inherited form of primordial dwarfism, which is characterized by a small head diameter at birth, but which also progresses to severe microcephaly, progressive bony dysplasia, and characteristic facies and personality. This report presents a case of a five-year-old girl with MOPD II syndrome. The patient was referred to our clinic with the complaint of severe tooth pain at the left mandibular primary molar teeth. Clinical examination revealed that most of the primary teeth had been decayed and all primary teeth were hypoplastic. Patient’s history revealed delayed development in the primary dentition and radiographic examination showed rootless primary molar teeth and short-rooted incisors. The treatment was not possible due to the lack of root of the left mandibular primary molars; so the teeth were extracted. Thorough and timely dental evaluation is crucial for the prevention of dental problems and the maintenance of oral health in patients with MOPD II syndrome is of utmost importance. |
| first_indexed | 2024-04-10T13:13:33Z |
| format | Article |
| id | doaj.art-37a3c14239e8409da8c5bf43bc8d4b11 |
| institution | Directory Open Access Journal |
| issn | 2149-2352 2149-4592 |
| language | English |
| last_indexed | 2024-04-10T13:13:33Z |
| publishDate | 2015-01-01 |
| publisher | Istanbul University |
| record_format | Article |
| series | Journal of Istanbul University Faculty of Dentistry |
| spelling | doaj.art-37a3c14239e8409da8c5bf43bc8d4b112023-02-15T16:12:30ZengIstanbul UniversityJournal of Istanbul University Faculty of Dentistry2149-23522149-45922015-01-01491414610.17096/jiufd.73283MAJEWSKI OSTEODYSPLASTIC PRIMORDIAL DWARFISM TYPE II: CLINICAL FINDINGS AND DENTAL MANAGEMENT OF A CHILD PATIENTArslan Terlemez0Mustafa Altunsoy1Hakkı Çelebi2Department of Endodontics Faculty of Dentistry Necmettin Erbakan UniversityDepartment of Pediatric Dentistry Faculty of Dentistry Sifa UniversityDepartment of Prosthodontics Faculty of Dentistry Necmettin Erbakan UniversityMajewski osteodysplastic primordial dwarfism type II (MOPD II) is an unusual autosomal recessive inherited form of primordial dwarfism, which is characterized by a small head diameter at birth, but which also progresses to severe microcephaly, progressive bony dysplasia, and characteristic facies and personality. This report presents a case of a five-year-old girl with MOPD II syndrome. The patient was referred to our clinic with the complaint of severe tooth pain at the left mandibular primary molar teeth. Clinical examination revealed that most of the primary teeth had been decayed and all primary teeth were hypoplastic. Patient’s history revealed delayed development in the primary dentition and radiographic examination showed rootless primary molar teeth and short-rooted incisors. The treatment was not possible due to the lack of root of the left mandibular primary molars; so the teeth were extracted. Thorough and timely dental evaluation is crucial for the prevention of dental problems and the maintenance of oral health in patients with MOPD II syndrome is of utmost importance.http://www.journals.istanbul.edu.tr/iudis/article/view/1023021632/5000101124MajewskiOsteodysplasticPrimordial Dwarfism Type II |
| spellingShingle | Arslan Terlemez Mustafa Altunsoy Hakkı Çelebi MAJEWSKI OSTEODYSPLASTIC PRIMORDIAL DWARFISM TYPE II: CLINICAL FINDINGS AND DENTAL MANAGEMENT OF A CHILD PATIENT Journal of Istanbul University Faculty of Dentistry Majewski Osteodysplastic Primordial Dwarfism Type II |
| title | MAJEWSKI OSTEODYSPLASTIC PRIMORDIAL DWARFISM TYPE II: CLINICAL FINDINGS AND DENTAL MANAGEMENT OF A CHILD PATIENT |
| title_full | MAJEWSKI OSTEODYSPLASTIC PRIMORDIAL DWARFISM TYPE II: CLINICAL FINDINGS AND DENTAL MANAGEMENT OF A CHILD PATIENT |
| title_fullStr | MAJEWSKI OSTEODYSPLASTIC PRIMORDIAL DWARFISM TYPE II: CLINICAL FINDINGS AND DENTAL MANAGEMENT OF A CHILD PATIENT |
| title_full_unstemmed | MAJEWSKI OSTEODYSPLASTIC PRIMORDIAL DWARFISM TYPE II: CLINICAL FINDINGS AND DENTAL MANAGEMENT OF A CHILD PATIENT |
| title_short | MAJEWSKI OSTEODYSPLASTIC PRIMORDIAL DWARFISM TYPE II: CLINICAL FINDINGS AND DENTAL MANAGEMENT OF A CHILD PATIENT |
| title_sort | majewski osteodysplastic primordial dwarfism type ii clinical findings and dental management of a child patient |
| topic | Majewski Osteodysplastic Primordial Dwarfism Type II |
| url | http://www.journals.istanbul.edu.tr/iudis/article/view/1023021632/5000101124 |
| work_keys_str_mv | AT arslanterlemez majewskiosteodysplasticprimordialdwarfismtypeiiclinicalfindingsanddentalmanagementofachildpatient AT mustafaaltunsoy majewskiosteodysplasticprimordialdwarfismtypeiiclinicalfindingsanddentalmanagementofachildpatient AT hakkıcelebi majewskiosteodysplasticprimordialdwarfismtypeiiclinicalfindingsanddentalmanagementofachildpatient |