NUTRITIONAL KNOWLEDGE IN PHENYLKETONURIA (PKU)

NUTRITIONAL KNOWLEDGE IN PHENYLKETONURIA (PKU)

<p align="justify">ABSTRACT: A review of phenylketonuria (PKU) an autosomal recessive genetic desorder discovered and described in 1934 is presented and discussed. Excess phenylalanine is transamined and its presence or metabolites may cause brain damage. Hydroxylation is the...

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Bibliographic Details
Main Authors:	Beatriz D. O. MIRANDA DA CRUZ, Horst SEIDER, Kurt WIDHALM
Format:	Article
Language:	English
Published:	Universidade Estadual Paulista 2009-07-01
Series:	Alimentos e Nutrição
Subjects:	Phenylketonuria children phenylalanine, nutrition PKU.
Online Access:	http://serv-bib.fcfar.unesp.br/seer/index.php/alimentos/article/view/730

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