A Rare Case Report of Inguinal Hernia with Persistent Mullerian Duct and Klinefelter Syndrome
Inguinal hernia in male is a common problem but having female reproductive organs in hernial sac is rare. It occur because of failure of mullerian duct to regress in a male fetus during embryonic development, result in a syndrome known as Persistent Mullerian Duct Syndrome (PMDS), which is a rare...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
JCDR Research and Publications Private Limited
2016-06-01
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| Series: | Journal of Clinical and Diagnostic Research |
| Subjects: | |
| Online Access: | https://jcdr.net/articles/PDF/8050/18361_CE(RA1)_F(T)_PF1(SWAK)_PFA(AK)_PF2(PAG).pdf |
| Summary: | Inguinal hernia in male is a common problem but having female reproductive organs in hernial sac is rare. It occur because of failure
of mullerian duct to regress in a male fetus during embryonic development, result in a syndrome known as Persistent Mullerian Duct
Syndrome (PMDS), which is a rare entity of male pseudohermaphroditism. We hereby present a case of 21-year-old male patient
reported with complains of cryptorchidism and inguinal hernia. Generally diagnosis of PMDS was established during investigation like
ultrasonography, MRI for localization of undescended testis and during surgical exploration for inguinal hernia or cryptorchidism. Our
patient was operated by bilateral inguinal incision; hernial sac contained adult size uterus fallopian tube and upper 2/3rd of vagina. On
karyotyping it was found that he was a case of klinefelter syndrome also. Association of PMDS with klinefelter syndrome is very rare. |
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| ISSN: | 2249-782X 0973-709X |