Restrictive Cardiomyopathy in a Child
Restrictive cardiomyopathy in young children is rare and carries a poor prognosis. We report an 18-month-old girl with poor feeding and abdominal distension. Except for hepatomegaly, no other gastrointestinal abnormalities were found. She had normalsized ventricles but biatrial enlargement. Echocard...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2008-04-01
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| Series: | Pediatrics and Neonatology |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1875957208600121 |
| _version_ | 1811269494382788608 |
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| author | Shan-Miao Lin Haw-Kwei Hwang Ming-Ren Chen |
| author_facet | Shan-Miao Lin Haw-Kwei Hwang Ming-Ren Chen |
| author_sort | Shan-Miao Lin |
| collection | DOAJ |
| description | Restrictive cardiomyopathy in young children is rare and carries a poor prognosis. We report an 18-month-old girl with poor feeding and abdominal distension. Except for hepatomegaly, no other gastrointestinal abnormalities were found. She had normalsized ventricles but biatrial enlargement. Echocardiography demonstrated normal systolic but impaired diastolic function. Cardiac catheterization revealed a characteristic dip-and-plateau configuration of the right ventricular pressure tracing. The diagnosis turned out to be typical restrictive cardiomyopathy. The patient was maintained on aspirin while awaiting cardiac transplant. |
| first_indexed | 2024-04-12T21:43:02Z |
| format | Article |
| id | doaj.art-38f59bec23124a6783412798641ffb58 |
| institution | Directory Open Access Journal |
| issn | 1875-9572 |
| language | English |
| last_indexed | 2024-04-12T21:43:02Z |
| publishDate | 2008-04-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Pediatrics and Neonatology |
| spelling | doaj.art-38f59bec23124a6783412798641ffb582022-12-22T03:15:42ZengElsevierPediatrics and Neonatology1875-95722008-04-01492485110.1016/S1875-9572(08)60012-1Restrictive Cardiomyopathy in a ChildShan-Miao Lin0Haw-Kwei Hwang1Ming-Ren Chen2Department of Pediatrics, Mackay Memorial Hospital, Taipei, TaiwanDepartment of Pediatrics, Mackay Memorial Hospital, Taipei, TaiwanDepartment of Pediatrics, Mackay Memorial Hospital, Taipei, TaiwanRestrictive cardiomyopathy in young children is rare and carries a poor prognosis. We report an 18-month-old girl with poor feeding and abdominal distension. Except for hepatomegaly, no other gastrointestinal abnormalities were found. She had normalsized ventricles but biatrial enlargement. Echocardiography demonstrated normal systolic but impaired diastolic function. Cardiac catheterization revealed a characteristic dip-and-plateau configuration of the right ventricular pressure tracing. The diagnosis turned out to be typical restrictive cardiomyopathy. The patient was maintained on aspirin while awaiting cardiac transplant.http://www.sciencedirect.com/science/article/pii/S1875957208600121cardiac catheterizationchildrestrictive cardiomyopathy |
| spellingShingle | Shan-Miao Lin Haw-Kwei Hwang Ming-Ren Chen Restrictive Cardiomyopathy in a Child Pediatrics and Neonatology cardiac catheterization child restrictive cardiomyopathy |
| title | Restrictive Cardiomyopathy in a Child |
| title_full | Restrictive Cardiomyopathy in a Child |
| title_fullStr | Restrictive Cardiomyopathy in a Child |
| title_full_unstemmed | Restrictive Cardiomyopathy in a Child |
| title_short | Restrictive Cardiomyopathy in a Child |
| title_sort | restrictive cardiomyopathy in a child |
| topic | cardiac catheterization child restrictive cardiomyopathy |
| url | http://www.sciencedirect.com/science/article/pii/S1875957208600121 |
| work_keys_str_mv | AT shanmiaolin restrictivecardiomyopathyinachild AT hawkweihwang restrictivecardiomyopathyinachild AT mingrenchen restrictivecardiomyopathyinachild |