Early abdomino-perineal pull-through vaginoplasty
Vaginal agenesis is known as one of the Mόllerian anomalies. Mόllerian anomalies occur during gonadal development and differentiation, and may lead to complex outcomes. McKusick-Kaufman syndrome (MKS) is an autosomal recessive multiple malformation syndrome characterized by Mόllerian anomalies with...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2013-01-01
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| Series: | African Journal of Paediatric Surgery |
| Subjects: | |
| Online Access: | http://www.afrjpaedsurg.org/article.asp?issn=0189-6725;year=2013;volume=10;issue=2;spage=188;epage=191;aulast=Ciftci |
| _version_ | 1811242692886134784 |
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| author | Ilhan Ciftci Ayhan Tastekin Ali Annagur Mustafa Koplay |
| author_facet | Ilhan Ciftci Ayhan Tastekin Ali Annagur Mustafa Koplay |
| author_sort | Ilhan Ciftci |
| collection | DOAJ |
| description | Vaginal agenesis is known as one of the Mόllerian anomalies. Mόllerian anomalies occur during gonadal development and differentiation, and may lead to complex outcomes. McKusick-Kaufman syndrome (MKS) is an autosomal recessive multiple malformation syndrome characterized by Mόllerian anomalies with hydrometrocolpos (HMC) and postaxial polydactyly (PAP). We report a case of a female newborn that developed hydronephrosis and respiratory distress due to compression of the cystic mass and underwent surgery on postpartum day 3. Pull-through vaginoplasty was performed with an abdomino-perineal approach. We report the unique treatment approach in this case. |
| first_indexed | 2024-04-12T13:55:42Z |
| format | Article |
| id | doaj.art-391efcaa7ee64c5190f2209c7de883b6 |
| institution | Directory Open Access Journal |
| issn | 0189-6725 0974-5998 |
| language | English |
| last_indexed | 2024-04-12T13:55:42Z |
| publishDate | 2013-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | African Journal of Paediatric Surgery |
| spelling | doaj.art-391efcaa7ee64c5190f2209c7de883b62022-12-22T03:30:23ZengWolters Kluwer Medknow PublicationsAfrican Journal of Paediatric Surgery0189-67250974-59982013-01-0110218819110.4103/0189-6725.115053Early abdomino-perineal pull-through vaginoplastyIlhan CiftciAyhan TastekinAli AnnagurMustafa KoplayVaginal agenesis is known as one of the Mόllerian anomalies. Mόllerian anomalies occur during gonadal development and differentiation, and may lead to complex outcomes. McKusick-Kaufman syndrome (MKS) is an autosomal recessive multiple malformation syndrome characterized by Mόllerian anomalies with hydrometrocolpos (HMC) and postaxial polydactyly (PAP). We report a case of a female newborn that developed hydronephrosis and respiratory distress due to compression of the cystic mass and underwent surgery on postpartum day 3. Pull-through vaginoplasty was performed with an abdomino-perineal approach. We report the unique treatment approach in this case.http://www.afrjpaedsurg.org/article.asp?issn=0189-6725;year=2013;volume=10;issue=2;spage=188;epage=191;aulast=CiftciCongenitalhydrometrocolposMcKusick-Kaufman syndromeneonatepolydactylypull-throughvaginoplasty |
| spellingShingle | Ilhan Ciftci Ayhan Tastekin Ali Annagur Mustafa Koplay Early abdomino-perineal pull-through vaginoplasty African Journal of Paediatric Surgery Congenital hydrometrocolpos McKusick-Kaufman syndrome neonate polydactyly pull-through vaginoplasty |
| title | Early abdomino-perineal pull-through vaginoplasty |
| title_full | Early abdomino-perineal pull-through vaginoplasty |
| title_fullStr | Early abdomino-perineal pull-through vaginoplasty |
| title_full_unstemmed | Early abdomino-perineal pull-through vaginoplasty |
| title_short | Early abdomino-perineal pull-through vaginoplasty |
| title_sort | early abdomino perineal pull through vaginoplasty |
| topic | Congenital hydrometrocolpos McKusick-Kaufman syndrome neonate polydactyly pull-through vaginoplasty |
| url | http://www.afrjpaedsurg.org/article.asp?issn=0189-6725;year=2013;volume=10;issue=2;spage=188;epage=191;aulast=Ciftci |
| work_keys_str_mv | AT ilhanciftci earlyabdominoperinealpullthroughvaginoplasty AT ayhantastekin earlyabdominoperinealpullthroughvaginoplasty AT aliannagur earlyabdominoperinealpullthroughvaginoplasty AT mustafakoplay earlyabdominoperinealpullthroughvaginoplasty |