Agenesis of Frontal Sinuses in Association with Kindler Syndrome: A Rare Case Report Running title: Agenesis of frontal sinuses in Kindler Syndrome
Kindler syndrome, as a rare subtype of Epidermolysis Bullosa, sets in motion a series of genetic conditions causing minor traumas and blisters on skin and making the skin susceptible to sunburn. The present study presented a case report of a 32-year-old female diagnosed with Kindler syndrome. Corona...
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| Format: | Article |
| Language: | English |
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Cumhuriyet University
2020-06-01
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| Series: | Cumhuriyet Dental Journal |
| Subjects: | |
| Online Access: | https://dergipark.org.tr/tr/download/article-file/1174531 |
| _version_ | 1797760132678942720 |
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| author | Ali Bagherpour Shahin Moeını |
| author_facet | Ali Bagherpour Shahin Moeını |
| author_sort | Ali Bagherpour |
| collection | DOAJ |
| description | Kindler syndrome, as a rare subtype of Epidermolysis Bullosa, sets
in motion a series of genetic conditions causing minor traumas and blisters on
skin and making the skin susceptible to sunburn. The present study presented a
case report of a 32-year-old female diagnosed with Kindler syndrome. Coronal
and axial cone-beam computed tomography (CBCT) images clearly exhibited the agenesis
of frontal sinuses. The condition was completely obvious in the images, which
is a rare occurrence and has not been previously reported. The underdevelopment
or aplasia of the paranasal sinuses is a rare phenomenon, which relates primarily
to the frontal sinuses (12%) and secondarily to the maxillary sinuses (5-6%). Similarly,
the agenesis of the sphenoid sinuses is an extremely rare condition. Therefore,
raising our awareness about the paranasal sinus anomalies associated with the Kindler
syndrome can lead to new discoveries about this syndrome. Further, with respect
to the other patients suffering from Kindler syndrome, obtaining the basis of such
knowledge together with evaluating CBCT or CT images in order to detect
abnormalities can facilitate the management of the problems arising from paranasal
sinus abnormalities. |
| first_indexed | 2024-03-12T18:54:21Z |
| format | Article |
| id | doaj.art-3b0de56fe351496e981517cdc0a74e60 |
| institution | Directory Open Access Journal |
| issn | 1302-5805 2146-2852 |
| language | English |
| last_indexed | 2024-03-12T18:54:21Z |
| publishDate | 2020-06-01 |
| publisher | Cumhuriyet University |
| record_format | Article |
| series | Cumhuriyet Dental Journal |
| spelling | doaj.art-3b0de56fe351496e981517cdc0a74e602023-08-02T06:59:11ZengCumhuriyet UniversityCumhuriyet Dental Journal1302-58052146-28522020-06-012321491522057Agenesis of Frontal Sinuses in Association with Kindler Syndrome: A Rare Case Report Running title: Agenesis of frontal sinuses in Kindler SyndromeAli Bagherpour0Shahin Moeını1Mashhad University of Medical SciencesMashhad University of Medical SciencesKindler syndrome, as a rare subtype of Epidermolysis Bullosa, sets in motion a series of genetic conditions causing minor traumas and blisters on skin and making the skin susceptible to sunburn. The present study presented a case report of a 32-year-old female diagnosed with Kindler syndrome. Coronal and axial cone-beam computed tomography (CBCT) images clearly exhibited the agenesis of frontal sinuses. The condition was completely obvious in the images, which is a rare occurrence and has not been previously reported. The underdevelopment or aplasia of the paranasal sinuses is a rare phenomenon, which relates primarily to the frontal sinuses (12%) and secondarily to the maxillary sinuses (5-6%). Similarly, the agenesis of the sphenoid sinuses is an extremely rare condition. Therefore, raising our awareness about the paranasal sinus anomalies associated with the Kindler syndrome can lead to new discoveries about this syndrome. Further, with respect to the other patients suffering from Kindler syndrome, obtaining the basis of such knowledge together with evaluating CBCT or CT images in order to detect abnormalities can facilitate the management of the problems arising from paranasal sinus abnormalities.https://dergipark.org.tr/tr/download/article-file/1174531frontal sinusepidermolysis bullosasyndrome |
| spellingShingle | Ali Bagherpour Shahin Moeını Agenesis of Frontal Sinuses in Association with Kindler Syndrome: A Rare Case Report Running title: Agenesis of frontal sinuses in Kindler Syndrome Cumhuriyet Dental Journal frontal sinus epidermolysis bullosa syndrome |
| title | Agenesis of Frontal Sinuses in Association with Kindler Syndrome: A Rare Case Report Running title: Agenesis of frontal sinuses in Kindler Syndrome |
| title_full | Agenesis of Frontal Sinuses in Association with Kindler Syndrome: A Rare Case Report Running title: Agenesis of frontal sinuses in Kindler Syndrome |
| title_fullStr | Agenesis of Frontal Sinuses in Association with Kindler Syndrome: A Rare Case Report Running title: Agenesis of frontal sinuses in Kindler Syndrome |
| title_full_unstemmed | Agenesis of Frontal Sinuses in Association with Kindler Syndrome: A Rare Case Report Running title: Agenesis of frontal sinuses in Kindler Syndrome |
| title_short | Agenesis of Frontal Sinuses in Association with Kindler Syndrome: A Rare Case Report Running title: Agenesis of frontal sinuses in Kindler Syndrome |
| title_sort | agenesis of frontal sinuses in association with kindler syndrome a rare case report running title agenesis of frontal sinuses in kindler syndrome |
| topic | frontal sinus epidermolysis bullosa syndrome |
| url | https://dergipark.org.tr/tr/download/article-file/1174531 |
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