A rare case of congenital insensitivity to pain with anhydrosiss
Congenital insensitivity to pain syndrome with anhydrosis (CIPA) is a rare inherited disorder. It is characterized by loss of pain and temperature sensation, lack of sweating and mild mental retardation. This disorder belongs to hereditary sensory and autonomic neuropathy family (type IV). Because o...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2015-01-01
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| Series: | Indian Journal of Pain |
| Subjects: | |
| Online Access: | http://www.indianjpain.org/article.asp?issn=0970-5333;year=2015;volume=29;issue=2;spage=118;epage=120;aulast=Yanamadala |
| _version_ | 1818964829795254272 |
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| author | Govardhani Yanamadala Varaprasad Ussa Pavani Medisetty Bhavya Gatte |
| author_facet | Govardhani Yanamadala Varaprasad Ussa Pavani Medisetty Bhavya Gatte |
| author_sort | Govardhani Yanamadala |
| collection | DOAJ |
| description | Congenital insensitivity to pain syndrome with anhydrosis (CIPA) is a rare inherited disorder. It is characterized by loss of pain and temperature sensation, lack of sweating and mild mental retardation. This disorder belongs to hereditary sensory and autonomic neuropathy family (type IV). Because of these abnormalities, patients require special anesthetic care. They include titration of intraoperative opioids, an anesthetic to ensure co-operation and immobility and intra-operative temperature monitoring. Here we report a 7-year-old female child with CIPA posted for restoration and cementation for dental caries along with sural nerve and skin biopsy. |
| first_indexed | 2024-12-20T13:07:20Z |
| format | Article |
| id | doaj.art-3b34624f99ff49019b6fc78edd4d9710 |
| institution | Directory Open Access Journal |
| issn | 0970-5333 |
| language | English |
| last_indexed | 2024-12-20T13:07:20Z |
| publishDate | 2015-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Pain |
| spelling | doaj.art-3b34624f99ff49019b6fc78edd4d97102022-12-21T19:39:46ZengWolters Kluwer Medknow PublicationsIndian Journal of Pain0970-53332015-01-0129211812010.4103/0970-5333.153591A rare case of congenital insensitivity to pain with anhydrosissGovardhani YanamadalaVaraprasad UssaPavani MedisettyBhavya GatteCongenital insensitivity to pain syndrome with anhydrosis (CIPA) is a rare inherited disorder. It is characterized by loss of pain and temperature sensation, lack of sweating and mild mental retardation. This disorder belongs to hereditary sensory and autonomic neuropathy family (type IV). Because of these abnormalities, patients require special anesthetic care. They include titration of intraoperative opioids, an anesthetic to ensure co-operation and immobility and intra-operative temperature monitoring. Here we report a 7-year-old female child with CIPA posted for restoration and cementation for dental caries along with sural nerve and skin biopsy.http://www.indianjpain.org/article.asp?issn=0970-5333;year=2015;volume=29;issue=2;spage=118;epage=120;aulast=YanamadalaAnestheticsanhydrosiscongenital insensitivity to pain |
| spellingShingle | Govardhani Yanamadala Varaprasad Ussa Pavani Medisetty Bhavya Gatte A rare case of congenital insensitivity to pain with anhydrosiss Indian Journal of Pain Anesthetics anhydrosis congenital insensitivity to pain |
| title | A rare case of congenital insensitivity to pain with anhydrosiss |
| title_full | A rare case of congenital insensitivity to pain with anhydrosiss |
| title_fullStr | A rare case of congenital insensitivity to pain with anhydrosiss |
| title_full_unstemmed | A rare case of congenital insensitivity to pain with anhydrosiss |
| title_short | A rare case of congenital insensitivity to pain with anhydrosiss |
| title_sort | rare case of congenital insensitivity to pain with anhydrosiss |
| topic | Anesthetics anhydrosis congenital insensitivity to pain |
| url | http://www.indianjpain.org/article.asp?issn=0970-5333;year=2015;volume=29;issue=2;spage=118;epage=120;aulast=Yanamadala |
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