Crowned Dens Syndrome: A Rare Cause of Sudden Onset Neck Pain

Objective: To report a case of Crowned Dens Syndrome (CDS), which is a rare disorder caused by crystal deposition by calcium pyrophosphate dihydrate in the peridontoid soft tissues surrounding the C1 and C2 vertebrae that presents in elderly with sudden onset neck pain, neck stiffness, fever, and el...

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Main Authors: Nauman Ismat Butt, Muhammad Bilal Rasheed, Fahmina Ashfaq, Aniqa Anser
Format: Article
Language:English
Published: Universitas Padjadjaran 2023-09-01
Series:International Journal of Integrated Health Sciences
Subjects:
Online Access:https://journal.fk.unpad.ac.id/index.php/ijihs/article/view/3083
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author Nauman Ismat Butt
Muhammad Bilal Rasheed
Fahmina Ashfaq
Aniqa Anser
author_facet Nauman Ismat Butt
Muhammad Bilal Rasheed
Fahmina Ashfaq
Aniqa Anser
author_sort Nauman Ismat Butt
collection DOAJ
description Objective: To report a case of Crowned Dens Syndrome (CDS), which is a rare disorder caused by crystal deposition by calcium pyrophosphate dihydrate in the peridontoid soft tissues surrounding the C1 and C2 vertebrae that presents in elderly with sudden onset neck pain, neck stiffness, fever, and elevated inflammatory markers, with periodontal calcification in a halo or crown configuration on radiography considered diagnostic. Methods: A 64-year-old diabetic and hypertensive female patient presented with a 6-day history of sudden onset posterior neck pain and stiffness. Movements of the cervical spine were equally limited in all directions, causing marked aggravation of pain. There was no focal neurologic loss. Her inflammatory markers were markedly raised. Results: Based on radiography, she was diagnosed with Crowned Dens syndrome and started on oral prednisolone, paracetamol, and tizanidine along with topical diclofenac. Oral NSAIDs were contraindicated due to her renal insufficiency. Conclusion: Crowned Dens Syndrome (CDS) is a rare cause of neck pain. Clinicians should consider this syndrome in their differential diagnosis. Timely diagnosis and treatment of CDS will lead to avoidance of unnecessary investigations and medications in such patients, along with a reduction in the length of stay.
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spelling doaj.art-3b70b32245e04987b3c05eeebceaa4f62023-11-28T09:18:09ZengUniversitas PadjadjaranInternational Journal of Integrated Health Sciences2302-13812338-45062023-09-0111212012410.15850/ijihs.v11n2.30831638Crowned Dens Syndrome: A Rare Cause of Sudden Onset Neck PainNauman Ismat Butt0Muhammad Bilal Rasheed1Fahmina Ashfaq2Aniqa Anser3Department of Medicine & Allied Azra Naheed Medical College, Superior University LahoreDepartment of Medicine & Allied Azra Naheed Medical College, Superior University LahoreDepartment of Medicine, Jinnah Hospital, Allama Iqbal Medical College LahoreDepartment of Medicine & Allied Azra Naheed Medical College, Superior University LahoreObjective: To report a case of Crowned Dens Syndrome (CDS), which is a rare disorder caused by crystal deposition by calcium pyrophosphate dihydrate in the peridontoid soft tissues surrounding the C1 and C2 vertebrae that presents in elderly with sudden onset neck pain, neck stiffness, fever, and elevated inflammatory markers, with periodontal calcification in a halo or crown configuration on radiography considered diagnostic. Methods: A 64-year-old diabetic and hypertensive female patient presented with a 6-day history of sudden onset posterior neck pain and stiffness. Movements of the cervical spine were equally limited in all directions, causing marked aggravation of pain. There was no focal neurologic loss. Her inflammatory markers were markedly raised. Results: Based on radiography, she was diagnosed with Crowned Dens syndrome and started on oral prednisolone, paracetamol, and tizanidine along with topical diclofenac. Oral NSAIDs were contraindicated due to her renal insufficiency. Conclusion: Crowned Dens Syndrome (CDS) is a rare cause of neck pain. Clinicians should consider this syndrome in their differential diagnosis. Timely diagnosis and treatment of CDS will lead to avoidance of unnecessary investigations and medications in such patients, along with a reduction in the length of stay.https://journal.fk.unpad.ac.id/index.php/ijihs/article/view/3083calcium pyrophosphate deposition, crowned dens syndrome, neck pain, neck stiffness
spellingShingle Nauman Ismat Butt
Muhammad Bilal Rasheed
Fahmina Ashfaq
Aniqa Anser
Crowned Dens Syndrome: A Rare Cause of Sudden Onset Neck Pain
International Journal of Integrated Health Sciences
calcium pyrophosphate deposition, crowned dens syndrome, neck pain, neck stiffness
title Crowned Dens Syndrome: A Rare Cause of Sudden Onset Neck Pain
title_full Crowned Dens Syndrome: A Rare Cause of Sudden Onset Neck Pain
title_fullStr Crowned Dens Syndrome: A Rare Cause of Sudden Onset Neck Pain
title_full_unstemmed Crowned Dens Syndrome: A Rare Cause of Sudden Onset Neck Pain
title_short Crowned Dens Syndrome: A Rare Cause of Sudden Onset Neck Pain
title_sort crowned dens syndrome a rare cause of sudden onset neck pain
topic calcium pyrophosphate deposition, crowned dens syndrome, neck pain, neck stiffness
url https://journal.fk.unpad.ac.id/index.php/ijihs/article/view/3083
work_keys_str_mv AT naumanismatbutt crowneddenssyndromeararecauseofsuddenonsetneckpain
AT muhammadbilalrasheed crowneddenssyndromeararecauseofsuddenonsetneckpain
AT fahminaashfaq crowneddenssyndromeararecauseofsuddenonsetneckpain
AT aniqaanser crowneddenssyndromeararecauseofsuddenonsetneckpain