Late diagnosed congenital agenesis of the left lung in 15-year-old boy

Pulmonary agenesis is a rare congenital lung defect involving the complete absence of the primary bronchus as well as pulmonary parenchyma and vessels. Unilateral agenesis occurs at the rate of 1/10,000–20,000 pregnancies. The cause of this defect is still unknown. This abnormality does not cause...

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Main Authors: Majka Jaszczura, Magdalena Kleszyk, Karolina Bień, Edyta Machura
Format: Article
Language:English
Published: Medical Communications Sp. z o.o. 2017-03-01
Series:Pediatria i Medycyna Rodzinna
Subjects:
Online Access:http://www.pimr.pl/index.php/issues/2017-vol-13-no-1/late-diagnosed-congenital-agenesis-of-the-left-lung-in-15-year-old-boy?aid=1042
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author Majka Jaszczura
Magdalena Kleszyk
Karolina Bień
Edyta Machura
author_facet Majka Jaszczura
Magdalena Kleszyk
Karolina Bień
Edyta Machura
author_sort Majka Jaszczura
collection DOAJ
description Pulmonary agenesis is a rare congenital lung defect involving the complete absence of the primary bronchus as well as pulmonary parenchyma and vessels. Unilateral agenesis occurs at the rate of 1/10,000–20,000 pregnancies. The cause of this defect is still unknown. This abnormality does not cause any specific symptoms; it may lead to respiratory failure, but an asymptomatic course lasting many years is also possible. This defect can often be suspected based on a chest radiograph performed for other reasons. We present the case of a 15-year-old boy with an accidental diagnosis of left pulmonary agenesis. Upon diagnosis the patient did not report any complaints. During a routine visit at an allergy clinic decreased vesicular sounds were present on the left side. A subsequent chest radiograph was reported as showing left lung inferior lobe atelectasis, which was an indication for a more comprehensive diagnostic investigation. A computed tomography scan revealed the complete absence of the left lung.
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spelling doaj.art-3b8da1f1ae6f40fab4adf31be49ad4472022-12-22T03:17:25ZengMedical Communications Sp. z o.o.Pediatria i Medycyna Rodzinna1734-15312451-07422017-03-0113112613210.15557/PiMR.2017.0013Late diagnosed congenital agenesis of the left lung in 15-year-old boyMajka Jaszczura0Magdalena Kleszyk1Karolina Bień2Edyta Machura3Department of Paediatrics of the School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Zabrze, PolandDepartment of Paediatrics of the School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Zabrze, PolandDepartment of Medical Radiology and Radiodiagnostics of the School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Zabrze, PolandDepartment of Paediatrics of the School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Zabrze, PolandPulmonary agenesis is a rare congenital lung defect involving the complete absence of the primary bronchus as well as pulmonary parenchyma and vessels. Unilateral agenesis occurs at the rate of 1/10,000–20,000 pregnancies. The cause of this defect is still unknown. This abnormality does not cause any specific symptoms; it may lead to respiratory failure, but an asymptomatic course lasting many years is also possible. This defect can often be suspected based on a chest radiograph performed for other reasons. We present the case of a 15-year-old boy with an accidental diagnosis of left pulmonary agenesis. Upon diagnosis the patient did not report any complaints. During a routine visit at an allergy clinic decreased vesicular sounds were present on the left side. A subsequent chest radiograph was reported as showing left lung inferior lobe atelectasis, which was an indication for a more comprehensive diagnostic investigation. A computed tomography scan revealed the complete absence of the left lung.http://www.pimr.pl/index.php/issues/2017-vol-13-no-1/late-diagnosed-congenital-agenesis-of-the-left-lung-in-15-year-old-boy?aid=1042pulmonary agenesiscongenital defectlungs
spellingShingle Majka Jaszczura
Magdalena Kleszyk
Karolina Bień
Edyta Machura
Late diagnosed congenital agenesis of the left lung in 15-year-old boy
Pediatria i Medycyna Rodzinna
pulmonary agenesis
congenital defect
lungs
title Late diagnosed congenital agenesis of the left lung in 15-year-old boy
title_full Late diagnosed congenital agenesis of the left lung in 15-year-old boy
title_fullStr Late diagnosed congenital agenesis of the left lung in 15-year-old boy
title_full_unstemmed Late diagnosed congenital agenesis of the left lung in 15-year-old boy
title_short Late diagnosed congenital agenesis of the left lung in 15-year-old boy
title_sort late diagnosed congenital agenesis of the left lung in 15 year old boy
topic pulmonary agenesis
congenital defect
lungs
url http://www.pimr.pl/index.php/issues/2017-vol-13-no-1/late-diagnosed-congenital-agenesis-of-the-left-lung-in-15-year-old-boy?aid=1042
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