Morphological Adaptation after Bilateral Lung Transplantation in a Patient with Kartagener Syndrome: A Case Report
Kartagener syndrome (KS) is a rare disease with an incidence of 1 in 20,000 to 30,000 births. There is no cure for KS, and conservative medical treatments are used to relieve symptoms and prevent disease progression. Lung transplantation (LT) is the only treatment option for end-stage KS. Since p...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Korean Society for Thoracic & Cardiovascular Surgery
2022-02-01
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| Series: | Journal of Chest Surgery |
| Subjects: |
| Summary: | Kartagener syndrome (KS) is a rare disease with an incidence of 1 in 20,000 to 30,000 births.
There is no cure for KS, and conservative medical treatments are used to relieve symptoms
and prevent disease progression. Lung transplantation (LT) is the only treatment option
for end-stage KS. Since patients with KS have anatomical abnormalities such as situs inversus
totalis, which often require surgery to correct, most reports are related to surgical
techniques. Reports about morphological adaptations and changes in transplanted lung
structure after LT in patients with KS are rare. We performed LT in a patient with KS and
observed morphological adaptation of the lungs for 6 months on chest computed tomography
using a quantitative evaluation tool (Chest Image Platform; Harvard University
Disability Resources, Cambridge, MA, USA). |
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| ISSN: | 2765-1606 2765-1614 |