The Short and Intensive Rehabilitation (SHAiR) Program Improves Dropped Head Syndrome Caused by Amyotrophic Lateral Sclerosis: A Case Report
<i>Background and Objectives:</i> Dropped head syndrome (DHS) is a syndrome that presents with correctable cervical kyphotic deformity as a result of weakening cervical paraspinal muscles. DHS with amyotrophic lateral sclerosis (ALS) is a relatively rare condition, and there is no establ...
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| Format: | Article |
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MDPI AG
2022-03-01
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| Series: | Medicina |
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| Online Access: | https://www.mdpi.com/1648-9144/58/3/452 |
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| author | Ryunosuke Urata Tatsuya Igawa Akifumi Suzuki Yutaka Sasao Norihiro Isogai Haruki Funao Ken Ishii |
| author_facet | Ryunosuke Urata Tatsuya Igawa Akifumi Suzuki Yutaka Sasao Norihiro Isogai Haruki Funao Ken Ishii |
| author_sort | Ryunosuke Urata |
| collection | DOAJ |
| description | <i>Background and Objectives:</i> Dropped head syndrome (DHS) is a syndrome that presents with correctable cervical kyphotic deformity as a result of weakening cervical paraspinal muscles. DHS with amyotrophic lateral sclerosis (ALS) is a relatively rare condition, and there is no established treatment. This is the first case report describing the improvement of both dropped head (DH) and cervical pain after the short and intensive rehabilitation (SHAiR) program in an ALS patient with DHS. <i>Case Report:</i> After being diagnosed with ALS in June 2020, a 75-year-old man visited our hospital in October 2020 to receive treatment for DHS. At the initial visit, the patient’s DH was prominent during standing and walking. The pain intensity of the neck was 9 out of 10 on the numerical rating scale (NRS), which was indicative of severe pain. The patient was hospitalized for 2 weeks and admitted into the SHAiR program. DH began to decrease one week after undergoing the SHAiR program and improved two weeks later. Neck pain decreased from 9 to 6 on the NRS. <i>Results:</i> The SHAiR program is a rehabilitation program aimed at improving DH in patients with idiopathic DHS. The program was designed to improve neck extensor and flexor function and global spinal alignment, and the program may have contributed to the improvement of DH and neck pain. Currently, reports of conservative therapies for this disease are limited to the use of cervical orthosis. Although further research is needed on the safety and indications of treatment, the SHAiR program may be a viable treatment option. |
| first_indexed | 2024-03-09T13:23:10Z |
| format | Article |
| id | doaj.art-3cf09c90815047c291e163b38a4a9719 |
| institution | Directory Open Access Journal |
| issn | 1010-660X 1648-9144 |
| language | English |
| last_indexed | 2024-03-09T13:23:10Z |
| publishDate | 2022-03-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Medicina |
| spelling | doaj.art-3cf09c90815047c291e163b38a4a97192023-11-30T21:27:14ZengMDPI AGMedicina1010-660X1648-91442022-03-0158345210.3390/medicina58030452The Short and Intensive Rehabilitation (SHAiR) Program Improves Dropped Head Syndrome Caused by Amyotrophic Lateral Sclerosis: A Case ReportRyunosuke Urata0Tatsuya Igawa1Akifumi Suzuki2Yutaka Sasao3Norihiro Isogai4Haruki Funao5Ken Ishii6Department of Orthopaedic Surgery, School of Medicine, International University of Health and Welfare, Chiba 286-8520, JapanDepartment of Orthopaedic Surgery, School of Medicine, International University of Health and Welfare, Chiba 286-8520, JapanDepartment of Orthopaedic Surgery, School of Medicine, International University of Health and Welfare, Chiba 286-8520, JapanDepartment of Orthopaedic Surgery, School of Medicine, International University of Health and Welfare, Chiba 286-8520, JapanDepartment of Orthopaedic Surgery, School of Medicine, International University of Health and Welfare, Chiba 286-8520, JapanDepartment of Orthopaedic Surgery, School of Medicine, International University of Health and Welfare, Chiba 286-8520, JapanDepartment of Orthopaedic Surgery, School of Medicine, International University of Health and Welfare, Chiba 286-8520, Japan<i>Background and Objectives:</i> Dropped head syndrome (DHS) is a syndrome that presents with correctable cervical kyphotic deformity as a result of weakening cervical paraspinal muscles. DHS with amyotrophic lateral sclerosis (ALS) is a relatively rare condition, and there is no established treatment. This is the first case report describing the improvement of both dropped head (DH) and cervical pain after the short and intensive rehabilitation (SHAiR) program in an ALS patient with DHS. <i>Case Report:</i> After being diagnosed with ALS in June 2020, a 75-year-old man visited our hospital in October 2020 to receive treatment for DHS. At the initial visit, the patient’s DH was prominent during standing and walking. The pain intensity of the neck was 9 out of 10 on the numerical rating scale (NRS), which was indicative of severe pain. The patient was hospitalized for 2 weeks and admitted into the SHAiR program. DH began to decrease one week after undergoing the SHAiR program and improved two weeks later. Neck pain decreased from 9 to 6 on the NRS. <i>Results:</i> The SHAiR program is a rehabilitation program aimed at improving DH in patients with idiopathic DHS. The program was designed to improve neck extensor and flexor function and global spinal alignment, and the program may have contributed to the improvement of DH and neck pain. Currently, reports of conservative therapies for this disease are limited to the use of cervical orthosis. Although further research is needed on the safety and indications of treatment, the SHAiR program may be a viable treatment option.https://www.mdpi.com/1648-9144/58/3/452dropped head syndrome (DHS)amyotrophic lateral sclerosis (ALS)rehabilitationshort and intensive rehabilitation (SHAiR) program |
| spellingShingle | Ryunosuke Urata Tatsuya Igawa Akifumi Suzuki Yutaka Sasao Norihiro Isogai Haruki Funao Ken Ishii The Short and Intensive Rehabilitation (SHAiR) Program Improves Dropped Head Syndrome Caused by Amyotrophic Lateral Sclerosis: A Case Report Medicina dropped head syndrome (DHS) amyotrophic lateral sclerosis (ALS) rehabilitation short and intensive rehabilitation (SHAiR) program |
| title | The Short and Intensive Rehabilitation (SHAiR) Program Improves Dropped Head Syndrome Caused by Amyotrophic Lateral Sclerosis: A Case Report |
| title_full | The Short and Intensive Rehabilitation (SHAiR) Program Improves Dropped Head Syndrome Caused by Amyotrophic Lateral Sclerosis: A Case Report |
| title_fullStr | The Short and Intensive Rehabilitation (SHAiR) Program Improves Dropped Head Syndrome Caused by Amyotrophic Lateral Sclerosis: A Case Report |
| title_full_unstemmed | The Short and Intensive Rehabilitation (SHAiR) Program Improves Dropped Head Syndrome Caused by Amyotrophic Lateral Sclerosis: A Case Report |
| title_short | The Short and Intensive Rehabilitation (SHAiR) Program Improves Dropped Head Syndrome Caused by Amyotrophic Lateral Sclerosis: A Case Report |
| title_sort | short and intensive rehabilitation shair program improves dropped head syndrome caused by amyotrophic lateral sclerosis a case report |
| topic | dropped head syndrome (DHS) amyotrophic lateral sclerosis (ALS) rehabilitation short and intensive rehabilitation (SHAiR) program |
| url | https://www.mdpi.com/1648-9144/58/3/452 |
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