Update of dental and maxillofacial alterations in patients with pycnodysostosis
ABSTRACT Pycnodysostosis is a rare, autosomal recessive genetic condition, which causes a decrease in bone remodeling, resulting in different clinical and radiographic manifestations. This case series aims to describe two clinical cases diagnosed at the Department of Oral and Maxillofacial Surgery a...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Sociedade Brasileira de Patologia Clínica
2019-11-01
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| Series: | Jornal Brasileiro de Patologia e Medicina Laboratorial |
| Subjects: | |
| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1676-24442019000500506&tlng=pt |
| _version_ | 1798014335348375552 |
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| author | Luiz Carlos Moreira Jr. Glória Maria França Victor Diniz B. Santos Hébel C. Galvão Petrus P. Gomes Adriano R. Germano |
| author_facet | Luiz Carlos Moreira Jr. Glória Maria França Victor Diniz B. Santos Hébel C. Galvão Petrus P. Gomes Adriano R. Germano |
| author_sort | Luiz Carlos Moreira Jr. |
| collection | DOAJ |
| description | ABSTRACT Pycnodysostosis is a rare, autosomal recessive genetic condition, which causes a decrease in bone remodeling, resulting in different clinical and radiographic manifestations. This case series aims to describe two clinical cases diagnosed at the Department of Oral and Maxillofacial Surgery and Traumatology of a University on the Northeast of Brazil. There are two complex cases involving osteomyelitis and dental and bone alterations of the jaws. It is concluded that the knowledge of oral and maxillofacial characteristics of this syndrome are required to plan appropriate treatment for patient in order to avoid complications of dental treatments due to inadequate bone remodeling. |
| first_indexed | 2024-04-11T15:16:50Z |
| format | Article |
| id | doaj.art-3d989f25c89d4649a785b8faf2cd062b |
| institution | Directory Open Access Journal |
| issn | 1678-4774 |
| language | English |
| last_indexed | 2024-04-11T15:16:50Z |
| publishDate | 2019-11-01 |
| publisher | Sociedade Brasileira de Patologia Clínica |
| record_format | Article |
| series | Jornal Brasileiro de Patologia e Medicina Laboratorial |
| spelling | doaj.art-3d989f25c89d4649a785b8faf2cd062b2022-12-22T04:16:28ZengSociedade Brasileira de Patologia ClínicaJornal Brasileiro de Patologia e Medicina Laboratorial1678-47742019-11-0155550651510.5935/1676-2444.20190046Update of dental and maxillofacial alterations in patients with pycnodysostosisLuiz Carlos Moreira Jr.Glória Maria FrançaVictor Diniz B. SantosHébel C. GalvãoPetrus P. GomesAdriano R. Germanohttps://orcid.org/0000-0002-1661-8038ABSTRACT Pycnodysostosis is a rare, autosomal recessive genetic condition, which causes a decrease in bone remodeling, resulting in different clinical and radiographic manifestations. This case series aims to describe two clinical cases diagnosed at the Department of Oral and Maxillofacial Surgery and Traumatology of a University on the Northeast of Brazil. There are two complex cases involving osteomyelitis and dental and bone alterations of the jaws. It is concluded that the knowledge of oral and maxillofacial characteristics of this syndrome are required to plan appropriate treatment for patient in order to avoid complications of dental treatments due to inadequate bone remodeling.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1676-24442019000500506&tlng=ptpycnodysostosisdentistrybone disease |
| spellingShingle | Luiz Carlos Moreira Jr. Glória Maria França Victor Diniz B. Santos Hébel C. Galvão Petrus P. Gomes Adriano R. Germano Update of dental and maxillofacial alterations in patients with pycnodysostosis Jornal Brasileiro de Patologia e Medicina Laboratorial pycnodysostosis dentistry bone disease |
| title | Update of dental and maxillofacial alterations in patients with pycnodysostosis |
| title_full | Update of dental and maxillofacial alterations in patients with pycnodysostosis |
| title_fullStr | Update of dental and maxillofacial alterations in patients with pycnodysostosis |
| title_full_unstemmed | Update of dental and maxillofacial alterations in patients with pycnodysostosis |
| title_short | Update of dental and maxillofacial alterations in patients with pycnodysostosis |
| title_sort | update of dental and maxillofacial alterations in patients with pycnodysostosis |
| topic | pycnodysostosis dentistry bone disease |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1676-24442019000500506&tlng=pt |
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