Papular elastorrhexis: clinical perspectives
Engin Sezer, Emel Öztürk Durmaz, Sedef Şahin Department of Dermatology, Acibadem University School of Medicine, Istanbul, Turkey Abstract: First described by Bordas in 1987, papular elastorrhexis (PE) is a rare elastic fiber disorder of the skin characterized by multiple, discrete,...
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| Format: | Article |
| Language: | English |
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Dove Medical Press
2018-10-01
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| Series: | Clinical, Cosmetic and Investigational Dermatology |
| Subjects: | |
| Online Access: | https://www.dovepress.com/papular-elastorrhexis-clinical-perspectives-peer-reviewed-article-CCID |
| _version_ | 1818258340841521152 |
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| author | Sezer E Durmaz EÖ Şahin S |
| author_facet | Sezer E Durmaz EÖ Şahin S |
| author_sort | Sezer E |
| collection | DOAJ |
| description | Engin Sezer, Emel Öztürk Durmaz, Sedef Şahin Department of Dermatology, Acibadem University School of Medicine, Istanbul, Turkey Abstract: First described by Bordas in 1987, papular elastorrhexis (PE) is a rare elastic fiber disorder of the skin characterized by multiple, discrete, asymptomatic, firm, nonfollicular, monomorphous, 1–5 mm, circumscribed, hypopigmented, oval to round papules, symmetrically distributed on the chest, abdomen, back, shoulders, arms, and thighs. The onset of the condition is usually in the first or second decade of life. PE appears to be an exceedingly rare entity, with 33 cases reported in the literature until now. However, the disorder might be underestimated probably because of its subtlety, asymptomatic course, and benign nature of clinical alterations, which can easily be confused with other dermatoses such as acne scars. Clinical and histopathological differential diagnosis of PE is broad and includes papular acne scars, eruptive collagenoma, disseminated lenticular dermatofibrosis (as a component of Buschke–Ollendorff syndrome), white fibrous papulosis of the neck, pseudoxanthoma elasticum, pseudoxanthoma elasticum-like papillary dermal elastolysis, middermal elastolysis, and perifollicular elastolysis. Treatment of PE is a matter of debate and no reliable curative option exists. Keywords: papular elastorrhexis, elastic fibers, connective tissue |
| first_indexed | 2024-12-12T17:58:00Z |
| format | Article |
| id | doaj.art-3fe92d7e0c16439cb9482b19ba7a2b1a |
| institution | Directory Open Access Journal |
| issn | 1178-7015 |
| language | English |
| last_indexed | 2024-12-12T17:58:00Z |
| publishDate | 2018-10-01 |
| publisher | Dove Medical Press |
| record_format | Article |
| series | Clinical, Cosmetic and Investigational Dermatology |
| spelling | doaj.art-3fe92d7e0c16439cb9482b19ba7a2b1a2022-12-22T00:16:40ZengDove Medical PressClinical, Cosmetic and Investigational Dermatology1178-70152018-10-01Volume 1154154441803Papular elastorrhexis: clinical perspectivesSezer EDurmaz EÖŞahin SEngin Sezer, Emel Öztürk Durmaz, Sedef Şahin Department of Dermatology, Acibadem University School of Medicine, Istanbul, Turkey Abstract: First described by Bordas in 1987, papular elastorrhexis (PE) is a rare elastic fiber disorder of the skin characterized by multiple, discrete, asymptomatic, firm, nonfollicular, monomorphous, 1–5 mm, circumscribed, hypopigmented, oval to round papules, symmetrically distributed on the chest, abdomen, back, shoulders, arms, and thighs. The onset of the condition is usually in the first or second decade of life. PE appears to be an exceedingly rare entity, with 33 cases reported in the literature until now. However, the disorder might be underestimated probably because of its subtlety, asymptomatic course, and benign nature of clinical alterations, which can easily be confused with other dermatoses such as acne scars. Clinical and histopathological differential diagnosis of PE is broad and includes papular acne scars, eruptive collagenoma, disseminated lenticular dermatofibrosis (as a component of Buschke–Ollendorff syndrome), white fibrous papulosis of the neck, pseudoxanthoma elasticum, pseudoxanthoma elasticum-like papillary dermal elastolysis, middermal elastolysis, and perifollicular elastolysis. Treatment of PE is a matter of debate and no reliable curative option exists. Keywords: papular elastorrhexis, elastic fibers, connective tissuehttps://www.dovepress.com/papular-elastorrhexis-clinical-perspectives-peer-reviewed-article-CCIDPapular elastorrhexiselastic fibersconnective tissue |
| spellingShingle | Sezer E Durmaz EÖ Şahin S Papular elastorrhexis: clinical perspectives Clinical, Cosmetic and Investigational Dermatology Papular elastorrhexis elastic fibers connective tissue |
| title | Papular elastorrhexis: clinical perspectives |
| title_full | Papular elastorrhexis: clinical perspectives |
| title_fullStr | Papular elastorrhexis: clinical perspectives |
| title_full_unstemmed | Papular elastorrhexis: clinical perspectives |
| title_short | Papular elastorrhexis: clinical perspectives |
| title_sort | papular elastorrhexis clinical perspectives |
| topic | Papular elastorrhexis elastic fibers connective tissue |
| url | https://www.dovepress.com/papular-elastorrhexis-clinical-perspectives-peer-reviewed-article-CCID |
| work_keys_str_mv | AT sezere papularelastorrhexisclinicalperspectives AT durmazeo papularelastorrhexisclinicalperspectives AT sahins papularelastorrhexisclinicalperspectives |