Ichthyosis hystrix disease or verrucous epidermal nevus (a retrospective analysis of 20-year observation)
We present a clinical case of ichthyosis hystrix, a rare genetic ichthyosiform dermatosis. Specifics of the disease are related to the complexity of differential diagnosis and verification of the diagnosis, because clinical manifestation of ichthyosis hystrix is similar with that of verrucous epide...
| Main Authors: | , , , , |
|---|---|
| Format: | Article |
| Language: | Russian |
| Published: |
MONIKI
2017-02-01
|
| Series: | Alʹmanah Kliničeskoj Mediciny |
| Subjects: | |
| Online Access: | https://www.almclinmed.ru/jour/article/view/476 |
| _version_ | 1819127923345457152 |
|---|---|
| author | V. D. El'kin T. G. Sedova E. V. Plotnikova I. D. Kuznetsov M. Yu. Novoselova |
| author_facet | V. D. El'kin T. G. Sedova E. V. Plotnikova I. D. Kuznetsov M. Yu. Novoselova |
| author_sort | V. D. El'kin |
| collection | DOAJ |
| description | We present a clinical case of ichthyosis hystrix, a rare genetic ichthyosiform dermatosis. Specifics of the disease are related to the complexity of differential diagnosis and verification of the diagnosis, because clinical manifestation of ichthyosis hystrix is similar with that of verrucous epidermal nevus. Clinical particulars of both nosologies are characterized by bizarre and widespread skin lesions of spicular hyperkeratotic growth, located along Blaschko lines. The exclusive feature of the clinical case described is a long-term (20 years) clinical and laboratory monitoring of the patient. The literature review provides brief information on etiology, pathogenesis, clinical features, differential diagnosis, and pathomorphology of ichthyosis hystrix and verrucous epidermal nevus. |
| first_indexed | 2024-12-22T08:19:38Z |
| format | Article |
| id | doaj.art-3ff0e84b5e494e65ba7cfc1fe287b6aa |
| institution | Directory Open Access Journal |
| issn | 2072-0505 2587-9294 |
| language | Russian |
| last_indexed | 2024-12-22T08:19:38Z |
| publishDate | 2017-02-01 |
| publisher | MONIKI |
| record_format | Article |
| series | Alʹmanah Kliničeskoj Mediciny |
| spelling | doaj.art-3ff0e84b5e494e65ba7cfc1fe287b6aa2022-12-21T18:32:48ZrusMONIKIAlʹmanah Kliničeskoj Mediciny2072-05052587-92942017-02-01451626710.18786/2072-0505-2017-45-1-62-67424Ichthyosis hystrix disease or verrucous epidermal nevus (a retrospective analysis of 20-year observation)V. D. El'kin0T. G. Sedova1E. V. Plotnikova2I. D. Kuznetsov3M. Yu. Novoselova4Perm State Medical University named after academician E.A. VagnerPerm State Medical University named after academician E.A. VagnerPerm State Medical University named after academician E.A. VagnerPerm State Medical University named after academician E.A. VagnerPerm State Medical University named after academician E.A. VagnerWe present a clinical case of ichthyosis hystrix, a rare genetic ichthyosiform dermatosis. Specifics of the disease are related to the complexity of differential diagnosis and verification of the diagnosis, because clinical manifestation of ichthyosis hystrix is similar with that of verrucous epidermal nevus. Clinical particulars of both nosologies are characterized by bizarre and widespread skin lesions of spicular hyperkeratotic growth, located along Blaschko lines. The exclusive feature of the clinical case described is a long-term (20 years) clinical and laboratory monitoring of the patient. The literature review provides brief information on etiology, pathogenesis, clinical features, differential diagnosis, and pathomorphology of ichthyosis hystrix and verrucous epidermal nevus.https://www.almclinmed.ru/jour/article/view/476ichthyosis hystrix diseaseverrucous epidermal nevusclinicdifferential diagnosis |
| spellingShingle | V. D. El'kin T. G. Sedova E. V. Plotnikova I. D. Kuznetsov M. Yu. Novoselova Ichthyosis hystrix disease or verrucous epidermal nevus (a retrospective analysis of 20-year observation) Alʹmanah Kliničeskoj Mediciny ichthyosis hystrix disease verrucous epidermal nevus clinic differential diagnosis |
| title | Ichthyosis hystrix disease or verrucous epidermal nevus (a retrospective analysis of 20-year observation) |
| title_full | Ichthyosis hystrix disease or verrucous epidermal nevus (a retrospective analysis of 20-year observation) |
| title_fullStr | Ichthyosis hystrix disease or verrucous epidermal nevus (a retrospective analysis of 20-year observation) |
| title_full_unstemmed | Ichthyosis hystrix disease or verrucous epidermal nevus (a retrospective analysis of 20-year observation) |
| title_short | Ichthyosis hystrix disease or verrucous epidermal nevus (a retrospective analysis of 20-year observation) |
| title_sort | ichthyosis hystrix disease or verrucous epidermal nevus a retrospective analysis of 20 year observation |
| topic | ichthyosis hystrix disease verrucous epidermal nevus clinic differential diagnosis |
| url | https://www.almclinmed.ru/jour/article/view/476 |
| work_keys_str_mv | AT vdelkin ichthyosishystrixdiseaseorverrucousepidermalnevusaretrospectiveanalysisof20yearobservation AT tgsedova ichthyosishystrixdiseaseorverrucousepidermalnevusaretrospectiveanalysisof20yearobservation AT evplotnikova ichthyosishystrixdiseaseorverrucousepidermalnevusaretrospectiveanalysisof20yearobservation AT idkuznetsov ichthyosishystrixdiseaseorverrucousepidermalnevusaretrospectiveanalysisof20yearobservation AT myunovoselova ichthyosishystrixdiseaseorverrucousepidermalnevusaretrospectiveanalysisof20yearobservation |