Mucinous adenocarcinoma in a neonate with congenital pulmonary malformation

Congenital pulmonary airway malformation (CPAM) is a rare developmental abnormality of the lower respiratory tract, often diagnosed during routine prenatal ultrasonography.We report a full-term newborn female noted to have a large mass in the left hemithorax during prenatal ultrasound, at 35 weeks g...

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Bibliographic Details
Main Authors: Tycie Linneman, Ratul Bhattacharyya, Jamshed Zuberi
Format: Article
Language:English
Published: Elsevier 2021-12-01
Series:Journal of Pediatric Surgery Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213576621003006
Description
Summary:Congenital pulmonary airway malformation (CPAM) is a rare developmental abnormality of the lower respiratory tract, often diagnosed during routine prenatal ultrasonography.We report a full-term newborn female noted to have a large mass in the left hemithorax during prenatal ultrasound, at 35 weeks gestation. A multicystic lesion in the lower left chest was confirmed using a Chest Radiograph and Computed Tomography (CT) angiogram. Her hospital course was next followed by a left lower lobectomy, with resultant pathology of CPAM Type 1 and invasive mucinous adenocarcinoma. Though patients with asymptomatic CPAM are often managed by observation, our case of unexpected malignancy advocates early considerations towards Surgery.
ISSN:2213-5766