Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis
The systemic vasculitides are multifocal diseases characterized by the presence of blood vessel inflammation in multiple organ systems. Their clinical presentation is variable extending from self-limited illness to critical complications including diffuse alveolar hemorrhage and glomerulonephritis....
Main Authors: | , , , , , , , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
MDPI AG
2014-07-01
|
Series: | Clinics and Practice |
Subjects: | |
Online Access: | https://www.clinicsandpractice.org/index.php/cp/article/view/653 |
_version_ | 1828138525672865792 |
---|---|
author | Evdokia Sourla Vasilis Bagalas Helias Tsioulis Asimina Paspala Sofia Akritidou Athanasia Pataka Katalin Fekete Ioannis Kioumis Ioannis Stanopoulos Georgia Pitsiou |
author_facet | Evdokia Sourla Vasilis Bagalas Helias Tsioulis Asimina Paspala Sofia Akritidou Athanasia Pataka Katalin Fekete Ioannis Kioumis Ioannis Stanopoulos Georgia Pitsiou |
author_sort | Evdokia Sourla |
collection | DOAJ |
description | The systemic vasculitides are multifocal diseases characterized by the presence of blood vessel inflammation in multiple organ systems. Their clinical presentation is variable extending from self-limited illness to critical complications including diffuse alveolar hemorrhage and glomerulonephritis. Alveolar hemorrhage is a lifethreatening manifestation of pulmonary vasculitis that can rapidly progress into acute respiratory failure requiring ventilatory support. We present the case of a 74-year-old patient admitted to the Intensive Care Unit with severe hypoxic respiratory failure and diffuse alveolar infiltrates in chest imaging that was later diagnosed as antineutrophil cytoplasmic antibodies-associated vasculitis. The report highlights the importance of differentiate between alveolar hemorrhage and acute respiratory distress syndrome of other etiology because alveolar hemorrhage is reversible with prompt initiation of treatment. |
first_indexed | 2024-04-11T18:37:24Z |
format | Article |
id | doaj.art-411d90703ace4e28b9b78a936b7f3660 |
institution | Directory Open Access Journal |
issn | 2039-7275 2039-7283 |
language | English |
last_indexed | 2024-04-11T18:37:24Z |
publishDate | 2014-07-01 |
publisher | MDPI AG |
record_format | Article |
series | Clinics and Practice |
spelling | doaj.art-411d90703ace4e28b9b78a936b7f36602022-12-22T04:09:09ZengMDPI AGClinics and Practice2039-72752039-72832014-07-014210.4081/cp.2014.653270Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitisEvdokia Sourla0Vasilis Bagalas1Helias Tsioulis2Asimina Paspala3Sofia Akritidou4Athanasia Pataka5Katalin Fekete6Ioannis Kioumis7Ioannis Stanopoulos8Georgia Pitsiou9Respiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiDepartment of Pneumonology, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, Thessaloniki,Respiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiThe systemic vasculitides are multifocal diseases characterized by the presence of blood vessel inflammation in multiple organ systems. Their clinical presentation is variable extending from self-limited illness to critical complications including diffuse alveolar hemorrhage and glomerulonephritis. Alveolar hemorrhage is a lifethreatening manifestation of pulmonary vasculitis that can rapidly progress into acute respiratory failure requiring ventilatory support. We present the case of a 74-year-old patient admitted to the Intensive Care Unit with severe hypoxic respiratory failure and diffuse alveolar infiltrates in chest imaging that was later diagnosed as antineutrophil cytoplasmic antibodies-associated vasculitis. The report highlights the importance of differentiate between alveolar hemorrhage and acute respiratory distress syndrome of other etiology because alveolar hemorrhage is reversible with prompt initiation of treatment.https://www.clinicsandpractice.org/index.php/cp/article/view/653respiratory failurevasculitisantineutrophil cytoplasmic antibodiesalveolar infiltrates. |
spellingShingle | Evdokia Sourla Vasilis Bagalas Helias Tsioulis Asimina Paspala Sofia Akritidou Athanasia Pataka Katalin Fekete Ioannis Kioumis Ioannis Stanopoulos Georgia Pitsiou Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis Clinics and Practice respiratory failure vasculitis antineutrophil cytoplasmic antibodies alveolar infiltrates. |
title | Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis |
title_full | Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis |
title_fullStr | Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis |
title_full_unstemmed | Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis |
title_short | Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis |
title_sort | acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies associated vasculitis |
topic | respiratory failure vasculitis antineutrophil cytoplasmic antibodies alveolar infiltrates. |
url | https://www.clinicsandpractice.org/index.php/cp/article/view/653 |
work_keys_str_mv | AT evdokiasourla acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT vasilisbagalas acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT heliastsioulis acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT asiminapaspala acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT sofiaakritidou acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT athanasiapataka acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT katalinfekete acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT ioanniskioumis acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT ioannisstanopoulos acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis AT georgiapitsiou acuterespiratoryfailureasprimarymanifestationofantineutrophilcytoplasmicantibodiesassociatedvasculitis |