Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis

The systemic vasculitides are multifocal diseases characterized by the presence of blood vessel inflammation in multiple organ systems. Their clinical presentation is variable extending from self-limited illness to critical complications including diffuse alveolar hemorrhage and glomerulonephritis....

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Main Authors: Evdokia Sourla, Vasilis Bagalas, Helias Tsioulis, Asimina Paspala, Sofia Akritidou, Athanasia Pataka, Katalin Fekete, Ioannis Kioumis, Ioannis Stanopoulos, Georgia Pitsiou
Format: Article
Language:English
Published: MDPI AG 2014-07-01
Series:Clinics and Practice
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Online Access:https://www.clinicsandpractice.org/index.php/cp/article/view/653
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author Evdokia Sourla
Vasilis Bagalas
Helias Tsioulis
Asimina Paspala
Sofia Akritidou
Athanasia Pataka
Katalin Fekete
Ioannis Kioumis
Ioannis Stanopoulos
Georgia Pitsiou
author_facet Evdokia Sourla
Vasilis Bagalas
Helias Tsioulis
Asimina Paspala
Sofia Akritidou
Athanasia Pataka
Katalin Fekete
Ioannis Kioumis
Ioannis Stanopoulos
Georgia Pitsiou
author_sort Evdokia Sourla
collection DOAJ
description The systemic vasculitides are multifocal diseases characterized by the presence of blood vessel inflammation in multiple organ systems. Their clinical presentation is variable extending from self-limited illness to critical complications including diffuse alveolar hemorrhage and glomerulonephritis. Alveolar hemorrhage is a lifethreatening manifestation of pulmonary vasculitis that can rapidly progress into acute respiratory failure requiring ventilatory support. We present the case of a 74-year-old patient admitted to the Intensive Care Unit with severe hypoxic respiratory failure and diffuse alveolar infiltrates in chest imaging that was later diagnosed as antineutrophil cytoplasmic antibodies-associated vasculitis. The report highlights the importance of differentiate between alveolar hemorrhage and acute respiratory distress syndrome of other etiology because alveolar hemorrhage is reversible with prompt initiation of treatment.
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spelling doaj.art-411d90703ace4e28b9b78a936b7f36602022-12-22T04:09:09ZengMDPI AGClinics and Practice2039-72752039-72832014-07-014210.4081/cp.2014.653270Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitisEvdokia Sourla0Vasilis Bagalas1Helias Tsioulis2Asimina Paspala3Sofia Akritidou4Athanasia Pataka5Katalin Fekete6Ioannis Kioumis7Ioannis Stanopoulos8Georgia Pitsiou9Respiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiDepartment of Pneumonology, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, Thessaloniki,Respiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiRespiratory Intensive Care Unit, Aristotle University of Thessaloniki, G.H. “G. Papanikolaou”, ThessalonikiThe systemic vasculitides are multifocal diseases characterized by the presence of blood vessel inflammation in multiple organ systems. Their clinical presentation is variable extending from self-limited illness to critical complications including diffuse alveolar hemorrhage and glomerulonephritis. Alveolar hemorrhage is a lifethreatening manifestation of pulmonary vasculitis that can rapidly progress into acute respiratory failure requiring ventilatory support. We present the case of a 74-year-old patient admitted to the Intensive Care Unit with severe hypoxic respiratory failure and diffuse alveolar infiltrates in chest imaging that was later diagnosed as antineutrophil cytoplasmic antibodies-associated vasculitis. The report highlights the importance of differentiate between alveolar hemorrhage and acute respiratory distress syndrome of other etiology because alveolar hemorrhage is reversible with prompt initiation of treatment.https://www.clinicsandpractice.org/index.php/cp/article/view/653respiratory failurevasculitisantineutrophil cytoplasmic antibodiesalveolar infiltrates.
spellingShingle Evdokia Sourla
Vasilis Bagalas
Helias Tsioulis
Asimina Paspala
Sofia Akritidou
Athanasia Pataka
Katalin Fekete
Ioannis Kioumis
Ioannis Stanopoulos
Georgia Pitsiou
Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis
Clinics and Practice
respiratory failure
vasculitis
antineutrophil cytoplasmic antibodies
alveolar infiltrates.
title Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis
title_full Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis
title_fullStr Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis
title_full_unstemmed Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis
title_short Acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies-associated vasculitis
title_sort acute respiratory failure as primary manifestation of antineutrophil cytoplasmic antibodies associated vasculitis
topic respiratory failure
vasculitis
antineutrophil cytoplasmic antibodies
alveolar infiltrates.
url https://www.clinicsandpractice.org/index.php/cp/article/view/653
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