Trigeminal Trophic Syndrome – Case Report

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Main Authors: Boštjan Matos, Neža Prezelj
Format: Article
Language:English
Published: Slovenian Medical Association 2015-05-01
Series:Zdravniški Vestnik
Subjects:
Online Access:http://vestnik.szd.si/index.php/ZdravVest/article/view/1128
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author Boštjan Matos
Neža Prezelj
author_facet Boštjan Matos
Neža Prezelj
author_sort Boštjan Matos
collection DOAJ
description <!--[if gte mso 9]><xml> <o:OfficeDocumentSettings> <o:RelyOnVML/> <o:AllowPNG/> <o:TargetScreenSize>1024x768</o:TargetScreenSize> </o:OfficeDocumentSettings> </xml><![endif]--><p class="MsoNormal" style="margin-top: 0cm; margin-right: 12.6pt; margin-bottom: .0001pt; margin-left: 18.0pt; text-align: justify; line-height: 200%; mso-layout-grid-align: none; text-autospace: none;"><span style="font-size: 12.0pt; line-height: 200%; font-family: 'Times New Roman','serif';" lang="SL">Trigeminal trophic syndrome is a rare condition resulting from compulsive self-manipulation of the skin after a peripheral or central injury to the trigeminal system. The classic triad consists of trigeminal anesthesia, facial paresthesias, and crescentric lateral nasal alar erosion and ulceration.</span><span style="font-size: 12.0pt; line-height: 200%; font-family: 'Times New Roman','serif'; mso-fareast-font-family: 'Times New Roman'; mso-fareast-language: SL;" lang="SL"> Although the symptoms are visibly clear, the diagnosis is not easy to establish.</span><span style="font-size: 12.0pt; line-height: 200%; font-family: 'Times New Roman','serif';" lang="SL"> The appearance of the ulcers mimics many other disease entities such as neoplasm, infection, granulomatous disease, vasculitis and factitial dermatitis. Trigeminal trophic syndrome should be considered with a positive neurologic history and when laboratory and biopsy workup is inconclusive. Once diagnosis is confirmed, treatment is complicated and often multidisciplinary. We report a case of a woman who developed a strictly unilateral crescent ulcer of the ala nasi after resection of an statoacoustic neurinoma. A clinician who is faced with a patient with nasal ulceration should consider this diagnosis.</span></p><p class="MsoNormal" style="margin-top: 0cm; margin-right: 12.6pt; margin-bottom: .0001pt; margin-left: 18.0pt; text-align: justify; line-height: 200%; mso-layout-grid-align: none; text-autospace: none;"><span style="font-size: 12.0pt; line-height: 200%; font-family: 'Times New Roman','serif'; mso-fareast-font-family: 'Times New Roman'; mso-fareast-language: SL;" lang="SL"> </span></p><p class="MsoNormal" style="margin-top: 0cm; margin-right: 12.6pt; margin-bottom: .0001pt; margin-left: 18.0pt; text-align: justify; line-height: 200%; mso-layout-grid-align: none; text-autospace: none;"><span style="font-size: 10.5pt; line-height: 200%; font-family: 'Times New Roman','serif';" lang="SL"> </span></p><p class="MsoNormal" style="margin-top: 0cm; margin-right: 12.6pt; margin-bottom: .0001pt; margin-left: 18.0pt; text-align: justify; line-height: 200%;"><span style="font-size: 12.0pt; 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spelling doaj.art-42cd3dd182e14f9ba94d254fd313916f2022-12-22T02:46:38ZengSlovenian Medical AssociationZdravniški Vestnik1318-03471581-02242015-05-018441004Trigeminal Trophic Syndrome – Case ReportBoštjan Matos0Neža Prezelj1University clinical center LjubljanaMedical faculty Ljubljana<!--[if gte mso 9]><xml> <o:OfficeDocumentSettings> <o:RelyOnVML/> <o:AllowPNG/> <o:TargetScreenSize>1024x768</o:TargetScreenSize> </o:OfficeDocumentSettings> </xml><![endif]--><p class="MsoNormal" style="margin-top: 0cm; margin-right: 12.6pt; margin-bottom: .0001pt; margin-left: 18.0pt; text-align: justify; line-height: 200%; mso-layout-grid-align: none; text-autospace: none;"><span style="font-size: 12.0pt; line-height: 200%; font-family: 'Times New Roman','serif';" lang="SL">Trigeminal trophic syndrome is a rare condition resulting from compulsive self-manipulation of the skin after a peripheral or central injury to the trigeminal system. The classic triad consists of trigeminal anesthesia, facial paresthesias, and crescentric lateral nasal alar erosion and ulceration.</span><span style="font-size: 12.0pt; line-height: 200%; font-family: 'Times New Roman','serif'; mso-fareast-font-family: 'Times New Roman'; mso-fareast-language: SL;" lang="SL"> Although the symptoms are visibly clear, the diagnosis is not easy to establish.</span><span style="font-size: 12.0pt; line-height: 200%; font-family: 'Times New Roman','serif';" lang="SL"> The appearance of the ulcers mimics many other disease entities such as neoplasm, infection, granulomatous disease, vasculitis and factitial dermatitis. Trigeminal trophic syndrome should be considered with a positive neurologic history and when laboratory and biopsy workup is inconclusive. Once diagnosis is confirmed, treatment is complicated and often multidisciplinary. We report a case of a woman who developed a strictly unilateral crescent ulcer of the ala nasi after resection of an statoacoustic neurinoma. A clinician who is faced with a patient with nasal ulceration should consider this diagnosis.</span></p><p class="MsoNormal" style="margin-top: 0cm; margin-right: 12.6pt; margin-bottom: .0001pt; margin-left: 18.0pt; text-align: justify; line-height: 200%; mso-layout-grid-align: none; text-autospace: none;"><span style="font-size: 12.0pt; line-height: 200%; font-family: 'Times New Roman','serif'; mso-fareast-font-family: 'Times New Roman'; mso-fareast-language: SL;" lang="SL"> </span></p><p class="MsoNormal" style="margin-top: 0cm; margin-right: 12.6pt; margin-bottom: .0001pt; margin-left: 18.0pt; text-align: justify; line-height: 200%; mso-layout-grid-align: none; text-autospace: none;"><span style="font-size: 10.5pt; line-height: 200%; font-family: 'Times New Roman','serif';" lang="SL"> </span></p><p class="MsoNormal" style="margin-top: 0cm; margin-right: 12.6pt; margin-bottom: .0001pt; margin-left: 18.0pt; text-align: justify; line-height: 200%;"><span style="font-size: 12.0pt; 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table.MsoNormalTable {mso-style-name:"Table Normal"; mso-tstyle-rowband-size:0; mso-tstyle-colband-size:0; mso-style-noshow:yes; mso-style-priority:99; mso-style-qformat:yes; mso-style-parent:""; mso-padding-alt:0cm 5.4pt 0cm 5.4pt; mso-para-margin:0cm; mso-para-margin-bottom:.0001pt; mso-pagination:widow-orphan; font-size:11.0pt; font-family:"Calibri","sans-serif"; mso-ascii-font-family:Calibri; mso-ascii-theme-font:minor-latin; mso-fareast-font-family:"Times New Roman"; mso-fareast-theme-font:minor-fareast; mso-hansi-font-family:Calibri; mso-hansi-theme-font:minor-latin; mso-bidi-font-family:"Times New Roman"; mso-bidi-theme-font:minor-bidi;} </style> <![endif]-->http://vestnik.szd.si/index.php/ZdravVest/article/view/1128trigeminal trophic syndrome, statoacoustic neuroma, facial ulceration, wound healing, facial flap surgery
spellingShingle Boštjan Matos
Neža Prezelj
Trigeminal Trophic Syndrome – Case Report
Zdravniški Vestnik
trigeminal trophic syndrome, statoacoustic neuroma, facial ulceration, wound healing, facial flap surgery
title Trigeminal Trophic Syndrome – Case Report
title_full Trigeminal Trophic Syndrome – Case Report
title_fullStr Trigeminal Trophic Syndrome – Case Report
title_full_unstemmed Trigeminal Trophic Syndrome – Case Report
title_short Trigeminal Trophic Syndrome – Case Report
title_sort trigeminal trophic syndrome case report
topic trigeminal trophic syndrome, statoacoustic neuroma, facial ulceration, wound healing, facial flap surgery
url http://vestnik.szd.si/index.php/ZdravVest/article/view/1128
work_keys_str_mv AT bostjanmatos trigeminaltrophicsyndromecasereport
AT nezaprezelj trigeminaltrophicsyndromecasereport