Challenges in Surgical Intervention for a Rare Case of Anterior Segment Dysgenesis: A Case Report
Amirah Aldawood,1 Sultan Bakri,1 Batool Alotaibi2 1Ophthalmology Department, Dhahran Eye Specialist Hospital, Dhahran, Saudi Arabia; 2Ophthalmology Department, Imam Abdulrahman Bin Faisal University, Dammam, Saudi ArabiaCorrespondence: Sultan Bakri, Ophthalmology Department, Dhahran Eye Specialist H...
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| Format: | Article |
| Language: | English |
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Dove Medical Press
2023-09-01
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| Series: | International Medical Case Reports Journal |
| Subjects: | |
| Online Access: | https://www.dovepress.com/challenges-in-surgical-intervention-for-a-rare-case-of-anterior-segmen-peer-reviewed-fulltext-article-IMCRJ |
| _version_ | 1797678082575826944 |
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| author | Aldawood A Bakri S Alotaibi B |
| author_facet | Aldawood A Bakri S Alotaibi B |
| author_sort | Aldawood A |
| collection | DOAJ |
| description | Amirah Aldawood,1 Sultan Bakri,1 Batool Alotaibi2 1Ophthalmology Department, Dhahran Eye Specialist Hospital, Dhahran, Saudi Arabia; 2Ophthalmology Department, Imam Abdulrahman Bin Faisal University, Dammam, Saudi ArabiaCorrespondence: Sultan Bakri, Ophthalmology Department, Dhahran Eye Specialist Hospital, Dhahran, Saudi Arabia, Tel +966 553324350, Email soltan.bakri@hotmail.comAbstract: Anterior Segment Dysgenesis (ASD) represents a spectrum of rare, congenital disorders that pose significant challenges to ophthalmological management due to their complex and heterogeneous nature. The management of ASD becomes particularly complex when associated with other serious ocular conditions. This report discusses the case of a 4-year-old girl diagnosed with ASD exhibiting a combination of sclerocornea, aphakia, aniridia, and secondary glaucoma. Owing to the complexity of such condition, a multi-disciplinary approach is required. Despite successful initial surgical interventions on the left eye, eye was lost due to subsequent endophthalmitis and retinal detachment, resulting in a decision to adopt a conservative, non-surgical approach for the right eye. Although a series of therapeutic interventions have been performed, the final visual outcome was poor, demonstrating the complexity and seriousness of such cases. This case serves as a reminder of the need for regular follow-up, prompt recognition, and management of potential complications. Further research is necessary to optimize the outcomes in patients with similar presentations.Keywords: congenital aniridia, aphakia, secondary glaucoma, sclerocornea, case report |
| first_indexed | 2024-03-11T22:54:30Z |
| format | Article |
| id | doaj.art-45706ac3cd5f4063a102716f90e58ec5 |
| institution | Directory Open Access Journal |
| issn | 1179-142X |
| language | English |
| last_indexed | 2024-03-11T22:54:30Z |
| publishDate | 2023-09-01 |
| publisher | Dove Medical Press |
| record_format | Article |
| series | International Medical Case Reports Journal |
| spelling | doaj.art-45706ac3cd5f4063a102716f90e58ec52023-09-21T19:09:00ZengDove Medical PressInternational Medical Case Reports Journal1179-142X2023-09-01Volume 1657958486861Challenges in Surgical Intervention for a Rare Case of Anterior Segment Dysgenesis: A Case ReportAldawood ABakri SAlotaibi BAmirah Aldawood,1 Sultan Bakri,1 Batool Alotaibi2 1Ophthalmology Department, Dhahran Eye Specialist Hospital, Dhahran, Saudi Arabia; 2Ophthalmology Department, Imam Abdulrahman Bin Faisal University, Dammam, Saudi ArabiaCorrespondence: Sultan Bakri, Ophthalmology Department, Dhahran Eye Specialist Hospital, Dhahran, Saudi Arabia, Tel +966 553324350, Email soltan.bakri@hotmail.comAbstract: Anterior Segment Dysgenesis (ASD) represents a spectrum of rare, congenital disorders that pose significant challenges to ophthalmological management due to their complex and heterogeneous nature. The management of ASD becomes particularly complex when associated with other serious ocular conditions. This report discusses the case of a 4-year-old girl diagnosed with ASD exhibiting a combination of sclerocornea, aphakia, aniridia, and secondary glaucoma. Owing to the complexity of such condition, a multi-disciplinary approach is required. Despite successful initial surgical interventions on the left eye, eye was lost due to subsequent endophthalmitis and retinal detachment, resulting in a decision to adopt a conservative, non-surgical approach for the right eye. Although a series of therapeutic interventions have been performed, the final visual outcome was poor, demonstrating the complexity and seriousness of such cases. This case serves as a reminder of the need for regular follow-up, prompt recognition, and management of potential complications. Further research is necessary to optimize the outcomes in patients with similar presentations.Keywords: congenital aniridia, aphakia, secondary glaucoma, sclerocornea, case reporthttps://www.dovepress.com/challenges-in-surgical-intervention-for-a-rare-case-of-anterior-segmen-peer-reviewed-fulltext-article-IMCRJcongenital aniridiaaphakiasecondary glaucomasclerocorneacase report |
| spellingShingle | Aldawood A Bakri S Alotaibi B Challenges in Surgical Intervention for a Rare Case of Anterior Segment Dysgenesis: A Case Report International Medical Case Reports Journal congenital aniridia aphakia secondary glaucoma sclerocornea case report |
| title | Challenges in Surgical Intervention for a Rare Case of Anterior Segment Dysgenesis: A Case Report |
| title_full | Challenges in Surgical Intervention for a Rare Case of Anterior Segment Dysgenesis: A Case Report |
| title_fullStr | Challenges in Surgical Intervention for a Rare Case of Anterior Segment Dysgenesis: A Case Report |
| title_full_unstemmed | Challenges in Surgical Intervention for a Rare Case of Anterior Segment Dysgenesis: A Case Report |
| title_short | Challenges in Surgical Intervention for a Rare Case of Anterior Segment Dysgenesis: A Case Report |
| title_sort | challenges in surgical intervention for a rare case of anterior segment dysgenesis a case report |
| topic | congenital aniridia aphakia secondary glaucoma sclerocornea case report |
| url | https://www.dovepress.com/challenges-in-surgical-intervention-for-a-rare-case-of-anterior-segmen-peer-reviewed-fulltext-article-IMCRJ |
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