The subaortic tendon as a mimic of hypertrophic cardiomyopathy
<p>Abstract</p> <p>Originally described by Brock and Teare, today hypertrophic cardiomyopathy is clinically defined as left (or right) ventricular hypertrophy without a known cardiac or systemic cause, such as systemic hypertension, Fabry's disease or aortic stenosis.</p>...
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| Format: | Article |
| Language: | English |
| Published: |
BMC
2009-07-01
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| Series: | Cardiovascular Ultrasound |
| Online Access: | http://www.cardiovascularultrasound.com/content/7/1/31 |
| _version_ | 1818484479990169600 |
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| author | Ker James |
| author_facet | Ker James |
| author_sort | Ker James |
| collection | DOAJ |
| description | <p>Abstract</p> <p>Originally described by Brock and Teare, today hypertrophic cardiomyopathy is clinically defined as left (or right) ventricular hypertrophy without a known cardiac or systemic cause, such as systemic hypertension, Fabry's disease or aortic stenosis.</p> <p>Also appreciated today is the enormous genotypic and phenotypic heterogeneity of this disease with more than 300 mutations over more than 24 genes, encoding various sarcomeric, mitochondrial and calcium-handling proteins, all as genetic causes for hypertrophic cardiomyopathy.</p> <p>Phenotypically, the disease can vary from negligible to extreme hypertrophy, affecting either the left and/or right ventricle in an apical, midventricular or subaortic location.</p> <p>Left ventricular false tendons are thin, fibrous or fibromuscular structures that traverse the left ventricular cavity. Recently, a case report was presented where it was shown that such a false tendon, originating from a subaortic location, was responsible for striking ST-segment elevation on the surface electrocardiogram.</p> <p>In this case report, a case is presented where such a subaortic tendon led to the classic echocardiographic appearance of hypertrophic cardiomyopathy, thus in the assessment of hypertrophic cardiomyopathy, this entity needs to be excluded in order to prevent a false positive diagnosis of hypertrophic cardiomyopathy.</p> |
| first_indexed | 2024-12-10T15:56:07Z |
| format | Article |
| id | doaj.art-45e66e3d050c4f3ba4b2e72a41abd90f |
| institution | Directory Open Access Journal |
| issn | 1476-7120 |
| language | English |
| last_indexed | 2024-12-10T15:56:07Z |
| publishDate | 2009-07-01 |
| publisher | BMC |
| record_format | Article |
| series | Cardiovascular Ultrasound |
| spelling | doaj.art-45e66e3d050c4f3ba4b2e72a41abd90f2022-12-22T01:42:38ZengBMCCardiovascular Ultrasound1476-71202009-07-01713110.1186/1476-7120-7-31The subaortic tendon as a mimic of hypertrophic cardiomyopathyKer James<p>Abstract</p> <p>Originally described by Brock and Teare, today hypertrophic cardiomyopathy is clinically defined as left (or right) ventricular hypertrophy without a known cardiac or systemic cause, such as systemic hypertension, Fabry's disease or aortic stenosis.</p> <p>Also appreciated today is the enormous genotypic and phenotypic heterogeneity of this disease with more than 300 mutations over more than 24 genes, encoding various sarcomeric, mitochondrial and calcium-handling proteins, all as genetic causes for hypertrophic cardiomyopathy.</p> <p>Phenotypically, the disease can vary from negligible to extreme hypertrophy, affecting either the left and/or right ventricle in an apical, midventricular or subaortic location.</p> <p>Left ventricular false tendons are thin, fibrous or fibromuscular structures that traverse the left ventricular cavity. Recently, a case report was presented where it was shown that such a false tendon, originating from a subaortic location, was responsible for striking ST-segment elevation on the surface electrocardiogram.</p> <p>In this case report, a case is presented where such a subaortic tendon led to the classic echocardiographic appearance of hypertrophic cardiomyopathy, thus in the assessment of hypertrophic cardiomyopathy, this entity needs to be excluded in order to prevent a false positive diagnosis of hypertrophic cardiomyopathy.</p>http://www.cardiovascularultrasound.com/content/7/1/31 |
| spellingShingle | Ker James The subaortic tendon as a mimic of hypertrophic cardiomyopathy Cardiovascular Ultrasound |
| title | The subaortic tendon as a mimic of hypertrophic cardiomyopathy |
| title_full | The subaortic tendon as a mimic of hypertrophic cardiomyopathy |
| title_fullStr | The subaortic tendon as a mimic of hypertrophic cardiomyopathy |
| title_full_unstemmed | The subaortic tendon as a mimic of hypertrophic cardiomyopathy |
| title_short | The subaortic tendon as a mimic of hypertrophic cardiomyopathy |
| title_sort | subaortic tendon as a mimic of hypertrophic cardiomyopathy |
| url | http://www.cardiovascularultrasound.com/content/7/1/31 |
| work_keys_str_mv | AT kerjames thesubaortictendonasamimicofhypertrophiccardiomyopathy AT kerjames subaortictendonasamimicofhypertrophiccardiomyopathy |