Rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations. How would I approach it?
HOW WOULD I APPROACH IT? Authors present an interesting case of a 10-year-old with a familial history of Rendu-Osler-Weber disease. The patient shows signs of cyanosis, polyglobulia, and baseline oxygen saturation levels of 85% due to a large and complex pulmonary arteriovenous malformati...
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| Format: | Article |
| Language: | English |
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Permanyer
2022-05-01
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| Series: | REC: Interventional Cardiology (English Ed.) |
| Online Access: | https://recintervcardiol.org/en/index.php?option=com_content&view=article&id=826 |
| _version_ | 1811307426660483072 |
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| author | Roberto Blanco Mata |
| author_facet | Roberto Blanco Mata |
| author_sort | Roberto Blanco Mata |
| collection | DOAJ |
| description | HOW WOULD I APPROACH IT? Authors present an interesting case of a 10-year-old with a familial history of Rendu-Osler-Weber disease. The patient shows signs of cyanosis, polyglobulia, and baseline oxygen saturation levels of 85% due to a large and complex pulmonary arteriovenous malformation (PAVM) that is causing systemic desaturation due to the existence of a significant right-to-left shunt. PAVMs are direct connections between arterial branches—often the pulmonary artery—and pulmonary veins without a normal capillary bed connected through an aneurysmal sac that can be partially septated in the inside. PAVMs can be categorized into simple, when they receive blood from a single afferent arterial vessel, and complex, when afference is multiple. Most of them are congenital and in over 70% of the cases they are associated with Rendu-Osler-Weber disease or hereditary hemorrhagic telangiectasia. Although it is a dominant autosomal disease that can be diagnosed through a genetic study the so-called Curaçao diagnostic criteria1 are often used to achieve diagnosis: Recurrent epistaxis. Multiple telangiectasias in typical locations: lips, oral cavity, fingers, and nose. Visceral vascular malformations: gastrointestinal, pulmonary, hepatic, cerebral or spinal. First-degree relative who is a disease carrier. With 3 or more criteria, the diagnosis becomes conclusive. With just 2 the diagnosis is possible. Most of the times this disease... |
| first_indexed | 2024-04-13T09:04:10Z |
| format | Article |
| id | doaj.art-46065fe6a10b415fb6a57456cb1661ab |
| institution | Directory Open Access Journal |
| issn | 2604-7322 |
| language | English |
| last_indexed | 2024-04-13T09:04:10Z |
| publishDate | 2022-05-01 |
| publisher | Permanyer |
| record_format | Article |
| series | REC: Interventional Cardiology (English Ed.) |
| spelling | doaj.art-46065fe6a10b415fb6a57456cb1661ab2022-12-22T02:53:01ZengPermanyerREC: Interventional Cardiology (English Ed.)2604-73222022-05-014215415610.24875/RECICE.M21000266Rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations. How would I approach it?Roberto Blanco Mata0Servicio de Cardiología, Hospital Universitario Cruces, Barakaldo, Bizkaia, SpainHOW WOULD I APPROACH IT? Authors present an interesting case of a 10-year-old with a familial history of Rendu-Osler-Weber disease. The patient shows signs of cyanosis, polyglobulia, and baseline oxygen saturation levels of 85% due to a large and complex pulmonary arteriovenous malformation (PAVM) that is causing systemic desaturation due to the existence of a significant right-to-left shunt. PAVMs are direct connections between arterial branches—often the pulmonary artery—and pulmonary veins without a normal capillary bed connected through an aneurysmal sac that can be partially septated in the inside. PAVMs can be categorized into simple, when they receive blood from a single afferent arterial vessel, and complex, when afference is multiple. Most of them are congenital and in over 70% of the cases they are associated with Rendu-Osler-Weber disease or hereditary hemorrhagic telangiectasia. Although it is a dominant autosomal disease that can be diagnosed through a genetic study the so-called Curaçao diagnostic criteria1 are often used to achieve diagnosis: Recurrent epistaxis. Multiple telangiectasias in typical locations: lips, oral cavity, fingers, and nose. Visceral vascular malformations: gastrointestinal, pulmonary, hepatic, cerebral or spinal. First-degree relative who is a disease carrier. With 3 or more criteria, the diagnosis becomes conclusive. With just 2 the diagnosis is possible. Most of the times this disease...https://recintervcardiol.org/en/index.php?option=com_content&view=article&id=826 |
| spellingShingle | Roberto Blanco Mata Rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations. How would I approach it? REC: Interventional Cardiology (English Ed.) |
| title | Rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations. How would I approach it? |
| title_full | Rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations. How would I approach it? |
| title_fullStr | Rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations. How would I approach it? |
| title_full_unstemmed | Rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations. How would I approach it? |
| title_short | Rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations. How would I approach it? |
| title_sort | rotational angiography and the contribution of roadmapping to the occlusion of arteriovenous malformations how would i approach it |
| url | https://recintervcardiol.org/en/index.php?option=com_content&view=article&id=826 |
| work_keys_str_mv | AT robertoblancomata rotationalangiographyandthecontributionofroadmappingtotheocclusionofarteriovenousmalformationshowwouldiapproachit |