Gingival fibromatosis with hypertrichosis syndrome: Case series of rare syndrome
Gingival fibromatosis with hypertrichosis syndrome is an extremely rare genetic condition characterized by profound overgrowth of hair and gums, as well as other variable features. Gingival fibromatosis is characterized by a large increase in the gingival dimension which extends above the dental cro...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2017-01-01
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| Series: | Indian Journal of Dental Research |
| Subjects: | |
| Online Access: | http://www.ijdr.in/article.asp?issn=0970-9290;year=2017;volume=28;issue=4;spage=457;epage=460;aulast=Balaji |
| _version_ | 1818484964536090624 |
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| author | Preetha Balaji S M Balaji |
| author_facet | Preetha Balaji S M Balaji |
| author_sort | Preetha Balaji |
| collection | DOAJ |
| description | Gingival fibromatosis with hypertrichosis syndrome is an extremely rare genetic condition characterized by profound overgrowth of hair and gums, as well as other variable features. Gingival fibromatosis is characterized by a large increase in the gingival dimension which extends above the dental crowns, covering them partially or completely. They were found to have a genetic origin, may also occur in isolation or be part of a syndrome, or acquired origin, due to specific drugs administered systemically. Congenital generalized hypertrichosis is a heterogeneous group of diseases with continuing excessive growth of terminal hair without androgenic stimulation. It has informally been called werewolf syndrome because the appearance is similar to that of a werewolf. Various syndromes have been associated with these features such as epilepsy, mental retardation, cardiomegaly, or osteochondrodysplasia. As so far very few cases have been reported in literature, we are reporting a series of three cases with management of the same. The excess gingival tissues, in these cases, were removed by conventional gingivectomy under general anesthesia. The postoperative result was uneventful and the patient's appearance improved significantly. Good esthetic result was achieved to allow patient to practice oral hygiene measures. Though this is not a serious condition clinically, psychosocial trauma cannot be neglected owing to the cosmetic disfigurement it produces. |
| first_indexed | 2024-12-10T16:01:48Z |
| format | Article |
| id | doaj.art-46c1322988e440a5a70ff8a821d41f7f |
| institution | Directory Open Access Journal |
| issn | 0970-9290 1998-3603 |
| language | English |
| last_indexed | 2024-12-10T16:01:48Z |
| publishDate | 2017-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Dental Research |
| spelling | doaj.art-46c1322988e440a5a70ff8a821d41f7f2022-12-22T01:42:24ZengWolters Kluwer Medknow PublicationsIndian Journal of Dental Research0970-92901998-36032017-01-0128445746010.4103/ijdr.IJDR_367_17Gingival fibromatosis with hypertrichosis syndrome: Case series of rare syndromePreetha BalajiS M BalajiGingival fibromatosis with hypertrichosis syndrome is an extremely rare genetic condition characterized by profound overgrowth of hair and gums, as well as other variable features. Gingival fibromatosis is characterized by a large increase in the gingival dimension which extends above the dental crowns, covering them partially or completely. They were found to have a genetic origin, may also occur in isolation or be part of a syndrome, or acquired origin, due to specific drugs administered systemically. Congenital generalized hypertrichosis is a heterogeneous group of diseases with continuing excessive growth of terminal hair without androgenic stimulation. It has informally been called werewolf syndrome because the appearance is similar to that of a werewolf. Various syndromes have been associated with these features such as epilepsy, mental retardation, cardiomegaly, or osteochondrodysplasia. As so far very few cases have been reported in literature, we are reporting a series of three cases with management of the same. The excess gingival tissues, in these cases, were removed by conventional gingivectomy under general anesthesia. The postoperative result was uneventful and the patient's appearance improved significantly. Good esthetic result was achieved to allow patient to practice oral hygiene measures. Though this is not a serious condition clinically, psychosocial trauma cannot be neglected owing to the cosmetic disfigurement it produces.http://www.ijdr.in/article.asp?issn=0970-9290;year=2017;volume=28;issue=4;spage=457;epage=460;aulast=BalajiGingival fibromatosishypertrichosiswerewolf syndrome |
| spellingShingle | Preetha Balaji S M Balaji Gingival fibromatosis with hypertrichosis syndrome: Case series of rare syndrome Indian Journal of Dental Research Gingival fibromatosis hypertrichosis werewolf syndrome |
| title | Gingival fibromatosis with hypertrichosis syndrome: Case series of rare syndrome |
| title_full | Gingival fibromatosis with hypertrichosis syndrome: Case series of rare syndrome |
| title_fullStr | Gingival fibromatosis with hypertrichosis syndrome: Case series of rare syndrome |
| title_full_unstemmed | Gingival fibromatosis with hypertrichosis syndrome: Case series of rare syndrome |
| title_short | Gingival fibromatosis with hypertrichosis syndrome: Case series of rare syndrome |
| title_sort | gingival fibromatosis with hypertrichosis syndrome case series of rare syndrome |
| topic | Gingival fibromatosis hypertrichosis werewolf syndrome |
| url | http://www.ijdr.in/article.asp?issn=0970-9290;year=2017;volume=28;issue=4;spage=457;epage=460;aulast=Balaji |
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