Giant right ventricular thrombus as the revealing form of Behçet's disease
Abstract Background Behçet's disease BD is a rare multisystemic disease, with rare cardiac involvement. This case illustrates a rare cardiac involvement as a giant intracavitary thrombus which was the revealing form of Behçet disease. Case presentation An 15-year-old male admitted to the emerge...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
SpringerOpen
2023-04-01
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| Series: | The Egyptian Heart Journal |
| Subjects: | |
| Online Access: | https://doi.org/10.1186/s43044-023-00354-5 |
| _version_ | 1797845866164256768 |
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| author | Anass A. Maaroufi Sara S. Abouradi Salah S. Hayar Abdenacer A. Drighil |
| author_facet | Anass A. Maaroufi Sara S. Abouradi Salah S. Hayar Abdenacer A. Drighil |
| author_sort | Anass A. Maaroufi |
| collection | DOAJ |
| description | Abstract Background Behçet's disease BD is a rare multisystemic disease, with rare cardiac involvement. This case illustrates a rare cardiac involvement as a giant intracavitary thrombus which was the revealing form of Behçet disease. Case presentation An 15-year-old male admitted to the emergency department for progressive dyspnoea, hemoptysis for which an echocardiogram displayed a large echogenic mass in the right ventricle and angio CT revealed associated bilateral pulmonary embolism. The patient was then proposed for surgery for removal and pathological study the later confirmed its fibrin thrombotic nature. Behçet disease was suspected based on past history of recurrent oral aphthosis and confirmed with a positive pathergy test. Further management by anticoagulants, immunosuppressants and corticosteroids seemed effective to avoid relapse. Conclusions Cardiac involvement during BD can be life-threatening as it is not always diagnosed in timely manner. However, intracardiac thrombus is uncommon with only few case reports. Echocardiography is the key tool for the diagnosis of intracardiac thrombus. |
| first_indexed | 2024-04-09T17:45:54Z |
| format | Article |
| id | doaj.art-46e1c3ecbda04274a77b2de450b1215d |
| institution | Directory Open Access Journal |
| issn | 2090-911X |
| language | English |
| last_indexed | 2024-04-09T17:45:54Z |
| publishDate | 2023-04-01 |
| publisher | SpringerOpen |
| record_format | Article |
| series | The Egyptian Heart Journal |
| spelling | doaj.art-46e1c3ecbda04274a77b2de450b1215d2023-04-16T11:17:44ZengSpringerOpenThe Egyptian Heart Journal2090-911X2023-04-017511410.1186/s43044-023-00354-5Giant right ventricular thrombus as the revealing form of Behçet's diseaseAnass A. Maaroufi0Sara S. Abouradi1Salah S. Hayar2Abdenacer A. Drighil3Cardiology Department, Ibn Rochd University HospitalCardiology Department, Ibn Rochd University HospitalCardiology Department, Ibn Rochd University HospitalCardiology Department, Ibn Rochd University HospitalAbstract Background Behçet's disease BD is a rare multisystemic disease, with rare cardiac involvement. This case illustrates a rare cardiac involvement as a giant intracavitary thrombus which was the revealing form of Behçet disease. Case presentation An 15-year-old male admitted to the emergency department for progressive dyspnoea, hemoptysis for which an echocardiogram displayed a large echogenic mass in the right ventricle and angio CT revealed associated bilateral pulmonary embolism. The patient was then proposed for surgery for removal and pathological study the later confirmed its fibrin thrombotic nature. Behçet disease was suspected based on past history of recurrent oral aphthosis and confirmed with a positive pathergy test. Further management by anticoagulants, immunosuppressants and corticosteroids seemed effective to avoid relapse. Conclusions Cardiac involvement during BD can be life-threatening as it is not always diagnosed in timely manner. However, intracardiac thrombus is uncommon with only few case reports. Echocardiography is the key tool for the diagnosis of intracardiac thrombus.https://doi.org/10.1186/s43044-023-00354-5Behçet diseaseIntra cardiac thrombusCardio-BehçetPulmonary embolism |
| spellingShingle | Anass A. Maaroufi Sara S. Abouradi Salah S. Hayar Abdenacer A. Drighil Giant right ventricular thrombus as the revealing form of Behçet's disease The Egyptian Heart Journal Behçet disease Intra cardiac thrombus Cardio-Behçet Pulmonary embolism |
| title | Giant right ventricular thrombus as the revealing form of Behçet's disease |
| title_full | Giant right ventricular thrombus as the revealing form of Behçet's disease |
| title_fullStr | Giant right ventricular thrombus as the revealing form of Behçet's disease |
| title_full_unstemmed | Giant right ventricular thrombus as the revealing form of Behçet's disease |
| title_short | Giant right ventricular thrombus as the revealing form of Behçet's disease |
| title_sort | giant right ventricular thrombus as the revealing form of behcet s disease |
| topic | Behçet disease Intra cardiac thrombus Cardio-Behçet Pulmonary embolism |
| url | https://doi.org/10.1186/s43044-023-00354-5 |
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