Melkersson-Rosenthal syndrome: a classical case report
ABSTRACT The Melkersson-Rosenthal syndrome constitutes a rare manifestation characterized by a triad of signs and symptoms: recurrent orofacial edema, fissured tongue, and recurrent facial paralysis. The difficulty in diagnosing Melkersson-Rosenthal syndrome is that orofacial edema is common to vari...
| Main Authors: | , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Faculdade São Leopoldo Mandic
2023-06-01
|
| Series: | RGO: Revista Gaúcha de Odontologia |
| Subjects: | |
| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372023000100806&lng=en&tlng=en |
| _version_ | 1797792660858077184 |
|---|---|
| author | Carina DOMANESCHI Claudia Fabiana Joca de ARRUDA Vanessa Juliana Gomes CARVALHO Rennan Luiz Oliveira dos SANTOS Norberto Nobuo SUGAYA |
| author_facet | Carina DOMANESCHI Claudia Fabiana Joca de ARRUDA Vanessa Juliana Gomes CARVALHO Rennan Luiz Oliveira dos SANTOS Norberto Nobuo SUGAYA |
| author_sort | Carina DOMANESCHI |
| collection | DOAJ |
| description | ABSTRACT The Melkersson-Rosenthal syndrome constitutes a rare manifestation characterized by a triad of signs and symptoms: recurrent orofacial edema, fissured tongue, and recurrent facial paralysis. The difficulty in diagnosing Melkersson-Rosenthal syndrome is that orofacial edema is common to various diseases besides the lack of awareness of the syndrome by health professionals and the frequent metachronous manifestation of its symptomatology. The aim of this report is to present a classical case of Melkersson-Rosenthal syndrome and its clinical and therapeutic approach. A patient who sought for assistance at the Stomatology Clinic presented a synchronous manifestation of the triad: a left lip and cheek nonpitting edema accompanied by facial paralysis on the same side and fissured tongue. Melkersson-Rosenthal syndrome was diagnosed due to the presence of the triad of signs and symptoms after initially ruling out Crohn’s disease, Sarcoidosis, and tuberculosis due to a lack of intestinal or respiratory complaints and absence of other clinical evidence. The treatment administered was steroids, the most common treatment with a satisfied prognosis we found in the literature for Melkersson-Rosenthal syndrome patients. We recommend its implementation intralesional injections of betamethasone dipropionate as after four infiltrations the edema subsided by 80% with no further relapses within one-year follow-up. |
| first_indexed | 2024-03-13T02:37:13Z |
| format | Article |
| id | doaj.art-4785d8efa7b543b79b8bcb26d42bd000 |
| institution | Directory Open Access Journal |
| issn | 1981-8637 |
| language | English |
| last_indexed | 2024-03-13T02:37:13Z |
| publishDate | 2023-06-01 |
| publisher | Faculdade São Leopoldo Mandic |
| record_format | Article |
| series | RGO: Revista Gaúcha de Odontologia |
| spelling | doaj.art-4785d8efa7b543b79b8bcb26d42bd0002023-06-28T23:17:31ZengFaculdade São Leopoldo MandicRGO: Revista Gaúcha de Odontologia1981-86372023-06-017110.1590/1981-86372023001920200005Melkersson-Rosenthal syndrome: a classical case reportCarina DOMANESCHIhttps://orcid.org/0000-0001-8615-3283Claudia Fabiana Joca de ARRUDAhttps://orcid.org/0000-0002-4774-8070Vanessa Juliana Gomes CARVALHOhttps://orcid.org/0000-0003-4529-9301Rennan Luiz Oliveira dos SANTOShttps://orcid.org/0000-0001-9093-3805Norberto Nobuo SUGAYAhttps://orcid.org/0000-0003-4966-6295ABSTRACT The Melkersson-Rosenthal syndrome constitutes a rare manifestation characterized by a triad of signs and symptoms: recurrent orofacial edema, fissured tongue, and recurrent facial paralysis. The difficulty in diagnosing Melkersson-Rosenthal syndrome is that orofacial edema is common to various diseases besides the lack of awareness of the syndrome by health professionals and the frequent metachronous manifestation of its symptomatology. The aim of this report is to present a classical case of Melkersson-Rosenthal syndrome and its clinical and therapeutic approach. A patient who sought for assistance at the Stomatology Clinic presented a synchronous manifestation of the triad: a left lip and cheek nonpitting edema accompanied by facial paralysis on the same side and fissured tongue. Melkersson-Rosenthal syndrome was diagnosed due to the presence of the triad of signs and symptoms after initially ruling out Crohn’s disease, Sarcoidosis, and tuberculosis due to a lack of intestinal or respiratory complaints and absence of other clinical evidence. The treatment administered was steroids, the most common treatment with a satisfied prognosis we found in the literature for Melkersson-Rosenthal syndrome patients. We recommend its implementation intralesional injections of betamethasone dipropionate as after four infiltrations the edema subsided by 80% with no further relapses within one-year follow-up.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372023000100806&lng=en&tlng=enFacial paralysisFissured tongueMelkersson-Rosenthal syndrome |
| spellingShingle | Carina DOMANESCHI Claudia Fabiana Joca de ARRUDA Vanessa Juliana Gomes CARVALHO Rennan Luiz Oliveira dos SANTOS Norberto Nobuo SUGAYA Melkersson-Rosenthal syndrome: a classical case report RGO: Revista Gaúcha de Odontologia Facial paralysis Fissured tongue Melkersson-Rosenthal syndrome |
| title | Melkersson-Rosenthal syndrome: a classical case report |
| title_full | Melkersson-Rosenthal syndrome: a classical case report |
| title_fullStr | Melkersson-Rosenthal syndrome: a classical case report |
| title_full_unstemmed | Melkersson-Rosenthal syndrome: a classical case report |
| title_short | Melkersson-Rosenthal syndrome: a classical case report |
| title_sort | melkersson rosenthal syndrome a classical case report |
| topic | Facial paralysis Fissured tongue Melkersson-Rosenthal syndrome |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372023000100806&lng=en&tlng=en |
| work_keys_str_mv | AT carinadomaneschi melkerssonrosenthalsyndromeaclassicalcasereport AT claudiafabianajocadearruda melkerssonrosenthalsyndromeaclassicalcasereport AT vanessajulianagomescarvalho melkerssonrosenthalsyndromeaclassicalcasereport AT rennanluizoliveiradossantos melkerssonrosenthalsyndromeaclassicalcasereport AT norbertonobuosugaya melkerssonrosenthalsyndromeaclassicalcasereport |