Malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 (NF1): a rare case of primary lung location
We present a rare case of a patient operated due to a lung tumor, which was ultimately diagnosed as malignant peripherial nerve sheath tumor (MPNST). MPNSTs are rare tumors of soft tissue with mesenchymal origin. The World Health Organization has distinguished this group in order to unify terms in m...
| Main Authors: | , , , , , , |
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| Format: | Article |
| Language: | English |
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Kazimierz Wielki University
2018-01-01
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| Series: | Journal of Education, Health and Sport |
| Subjects: | |
| Online Access: | http://www.ojs.ukw.edu.pl/index.php/johs/article/view/5183 |
| _version_ | 1818536570532134912 |
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| author | Anna Grzywa-Celińska Katarzyna Szmygin-Milanowska Justyna Emeryk-Maksymiuk Maria Walczyna Michał Palonka Adam Krusiński Jan Siwiec |
| author_facet | Anna Grzywa-Celińska Katarzyna Szmygin-Milanowska Justyna Emeryk-Maksymiuk Maria Walczyna Michał Palonka Adam Krusiński Jan Siwiec |
| author_sort | Anna Grzywa-Celińska |
| collection | DOAJ |
| description | We present a rare case of a patient operated due to a lung tumor, which was ultimately diagnosed as malignant peripherial nerve sheath tumor (MPNST). MPNSTs are rare tumors of soft tissue with mesenchymal origin. The World Health Organization has distinguished this group in order to unify terms in mesenchymal heterogeneous malignant tumors, e.g. neurofibrosarcomas, malignant schwannomas and malignant neurilemmoma [1]. They can occur as a result of neoplastic expansion of peripheral nerves’ branches, peripheral nerve fibers’ sheaths or Schwann cells, although many researchers believe that these tumors can derive not only from one, but several cell lines. MPNSTs are very rare in thorax, where they show aggressive pattern of growth [2] and stem from pleural cells rather than lung tissue. |
| first_indexed | 2024-12-11T18:39:40Z |
| format | Article |
| id | doaj.art-47d749a097cf4121a9482f092bcece22 |
| institution | Directory Open Access Journal |
| issn | 2391-8306 |
| language | English |
| last_indexed | 2024-12-11T18:39:40Z |
| publishDate | 2018-01-01 |
| publisher | Kazimierz Wielki University |
| record_format | Article |
| series | Journal of Education, Health and Sport |
| spelling | doaj.art-47d749a097cf4121a9482f092bcece222022-12-22T00:54:39ZengKazimierz Wielki UniversityJournal of Education, Health and Sport2391-83062018-01-0181111710.5281/zenodo.11345254834Malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 (NF1): a rare case of primary lung locationAnna Grzywa-Celińska0Katarzyna Szmygin-Milanowska1Justyna Emeryk-Maksymiuk2Maria Walczyna3Michał Palonka4Adam Krusiński5Jan Siwiec6Chair and Department of Pneumonology, Oncology and Allergology, Medical University of LublinChair and Department of Pneumonology, Oncology and Allergology, Medical University of LublinChair of Internal Medicine and Department of Internal Medicine in Nursing, Medical University of LublinChair and Department of Clinical Pathomorphology, Medical University of LublinChair and Department of Pneumonology, Oncology and Allergology, Medical University of LublinChair and Department of Pneumonology, Oncology and Allergology, Medical University of LublinChair and Department of Pneumonology, Oncology and Allergology, Medical University of LublinWe present a rare case of a patient operated due to a lung tumor, which was ultimately diagnosed as malignant peripherial nerve sheath tumor (MPNST). MPNSTs are rare tumors of soft tissue with mesenchymal origin. The World Health Organization has distinguished this group in order to unify terms in mesenchymal heterogeneous malignant tumors, e.g. neurofibrosarcomas, malignant schwannomas and malignant neurilemmoma [1]. They can occur as a result of neoplastic expansion of peripheral nerves’ branches, peripheral nerve fibers’ sheaths or Schwann cells, although many researchers believe that these tumors can derive not only from one, but several cell lines. MPNSTs are very rare in thorax, where they show aggressive pattern of growth [2] and stem from pleural cells rather than lung tissue.http://www.ojs.ukw.edu.pl/index.php/johs/article/view/5183malignant peripheral nerve sheath tumor, lung, primary location |
| spellingShingle | Anna Grzywa-Celińska Katarzyna Szmygin-Milanowska Justyna Emeryk-Maksymiuk Maria Walczyna Michał Palonka Adam Krusiński Jan Siwiec Malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 (NF1): a rare case of primary lung location Journal of Education, Health and Sport malignant peripheral nerve sheath tumor, lung, primary location |
| title | Malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 (NF1): a rare case of primary lung location |
| title_full | Malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 (NF1): a rare case of primary lung location |
| title_fullStr | Malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 (NF1): a rare case of primary lung location |
| title_full_unstemmed | Malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 (NF1): a rare case of primary lung location |
| title_short | Malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 (NF1): a rare case of primary lung location |
| title_sort | malignant peripheral nerve sheath tumor in a patient without neurofibromatosis 1 nf1 a rare case of primary lung location |
| topic | malignant peripheral nerve sheath tumor, lung, primary location |
| url | http://www.ojs.ukw.edu.pl/index.php/johs/article/view/5183 |
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