Staged Percutaneous Management of Pulmonary Atresia and Intact Interventricular Septum: Stretching the Limits

Aims. Pulmonary atresia with intact ventricular septum (PA/IVS) can be treated by catheter-based interventions and complemented by various surgical procedures. We aim to determine a long-term treatment strategy to enable patients to be surgery free, depending solely on percutaneous interventions. Me...

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Main Authors: Sonia A. El-Saiedi, Wael A. Attia, Baher M. Hanna, Mahmoud O. Aboudeif, Rania Zakaria, Mohamad Abd ElMeguid, Ashraf Abd El Reheem, Reda Abuelatta
Format: Article
Language:English
Published: Hindawi-Wiley 2023-01-01
Series:Journal of Interventional Cardiology
Online Access:http://dx.doi.org/10.1155/2023/9709227
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author Sonia A. El-Saiedi
Wael A. Attia
Baher M. Hanna
Mahmoud O. Aboudeif
Rania Zakaria
Mohamad Abd ElMeguid
Ashraf Abd El Reheem
Reda Abuelatta
author_facet Sonia A. El-Saiedi
Wael A. Attia
Baher M. Hanna
Mahmoud O. Aboudeif
Rania Zakaria
Mohamad Abd ElMeguid
Ashraf Abd El Reheem
Reda Abuelatta
author_sort Sonia A. El-Saiedi
collection DOAJ
description Aims. Pulmonary atresia with intact ventricular septum (PA/IVS) can be treated by catheter-based interventions and complemented by various surgical procedures. We aim to determine a long-term treatment strategy to enable patients to be surgery free, depending solely on percutaneous interventions. Methods and Results. We selected five patients from among a cohort of patients with PA/IVS treated at birth with radiofrequency perforation and dilatation of the pulmonary valve. Patients had reached a pulmonary valve annulus of 20 mm or larger on their biannual echocardiographic follow-up, with right ventricular dilatation. The findings, together with the right ventricular outflow tract and pulmonary arterial tree, were confirmed by multislice computerised tomography. Based on the angiographic size of the pulmonary valve annulus, all patients were successfully implanted with either Melody® or Edwards® pulmonary valves percutaneously, regardless of their small weights and ages. No complications were encountered. Conclusion. We managed to stretch the age and weight limitations for performing percutaneous pulmonary valve implantation (PPVI): interventions were attempted whenever a pulmonary annulus size of >20 mm was reached, which was rationalised by the prevention of progressive right ventricular outflow tract dilatation and accommodating valves between 24 and 26 mm, which is enough to sustain a normal pulmonary flow in adulthood.
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spelling doaj.art-48d77b8abfeb4d44baabe6eea2f3c3212023-02-13T01:08:15ZengHindawi-WileyJournal of Interventional Cardiology1540-81832023-01-01202310.1155/2023/9709227Staged Percutaneous Management of Pulmonary Atresia and Intact Interventricular Septum: Stretching the LimitsSonia A. El-Saiedi0Wael A. Attia1Baher M. Hanna2Mahmoud O. Aboudeif3Rania Zakaria4Mohamad Abd ElMeguid5Ashraf Abd El Reheem6Reda Abuelatta7Pediatric DepartmentPediatric DepartmentPediatric DepartmentPediatric DepartmentRadiodiagnostics DepartmentCardiology DepartmentAnaesthesia DepartmentSenior Cardiology ConsultantAims. Pulmonary atresia with intact ventricular septum (PA/IVS) can be treated by catheter-based interventions and complemented by various surgical procedures. We aim to determine a long-term treatment strategy to enable patients to be surgery free, depending solely on percutaneous interventions. Methods and Results. We selected five patients from among a cohort of patients with PA/IVS treated at birth with radiofrequency perforation and dilatation of the pulmonary valve. Patients had reached a pulmonary valve annulus of 20 mm or larger on their biannual echocardiographic follow-up, with right ventricular dilatation. The findings, together with the right ventricular outflow tract and pulmonary arterial tree, were confirmed by multislice computerised tomography. Based on the angiographic size of the pulmonary valve annulus, all patients were successfully implanted with either Melody® or Edwards® pulmonary valves percutaneously, regardless of their small weights and ages. No complications were encountered. Conclusion. We managed to stretch the age and weight limitations for performing percutaneous pulmonary valve implantation (PPVI): interventions were attempted whenever a pulmonary annulus size of >20 mm was reached, which was rationalised by the prevention of progressive right ventricular outflow tract dilatation and accommodating valves between 24 and 26 mm, which is enough to sustain a normal pulmonary flow in adulthood.http://dx.doi.org/10.1155/2023/9709227
spellingShingle Sonia A. El-Saiedi
Wael A. Attia
Baher M. Hanna
Mahmoud O. Aboudeif
Rania Zakaria
Mohamad Abd ElMeguid
Ashraf Abd El Reheem
Reda Abuelatta
Staged Percutaneous Management of Pulmonary Atresia and Intact Interventricular Septum: Stretching the Limits
Journal of Interventional Cardiology
title Staged Percutaneous Management of Pulmonary Atresia and Intact Interventricular Septum: Stretching the Limits
title_full Staged Percutaneous Management of Pulmonary Atresia and Intact Interventricular Septum: Stretching the Limits
title_fullStr Staged Percutaneous Management of Pulmonary Atresia and Intact Interventricular Septum: Stretching the Limits
title_full_unstemmed Staged Percutaneous Management of Pulmonary Atresia and Intact Interventricular Septum: Stretching the Limits
title_short Staged Percutaneous Management of Pulmonary Atresia and Intact Interventricular Septum: Stretching the Limits
title_sort staged percutaneous management of pulmonary atresia and intact interventricular septum stretching the limits
url http://dx.doi.org/10.1155/2023/9709227
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