Effective Initial Treatment of Diffuse Pulmonary Lymphangiomatosis with Sirolimus and Propranolol: A Case Report

Diffuse pulmonary lymphangiomatosis (DPL), an exceptionally rare disease, mainly occurs in children and young adults of both sexes. Even though DPL is considered to be a benign disease, its prognosis is relatively poor. Because of its rarity, little guidance on diagnosis and treatment is available,...

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Main Authors: Ieva Dimiene, Kristina Bieksiene, Jurgita Zaveckiene, Mindaugas Andrulis, Daiva-Elzbieta Optazaite, Neringa Vaguliene, Marius Zemaitis, Skaidrius Miliauskas
Format: Article
Language:English
Published: MDPI AG 2021-11-01
Series:Medicina
Subjects:
Online Access:https://www.mdpi.com/1648-9144/57/12/1308
Description
Summary:Diffuse pulmonary lymphangiomatosis (DPL), an exceptionally rare disease, mainly occurs in children and young adults of both sexes. Even though DPL is considered to be a benign disease, its prognosis is relatively poor. Because of its rarity, little guidance on diagnosis and treatment is available, which makes working with patients with DPL challenging for clinicians. We present here a case of a young man with DPL in whom treatment with sirolimus and propranolol rapidly achieved positive radiological and clinical effects.
ISSN:1010-660X
1648-9144