Biliary atresia associated with pancreaticobiliary maljunction
We report here two cases of Kasai type IIIa biliary atresia (BA), associated with pancreaticobiliary maljunction (PBM). Both cases were referred to our hospital because of hyperbilirubinemia and diagnosed with BA preoperatively by abdominal ultrasonography and biliary scintigraphy. They underwent Ka...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2018-12-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S221357661830263X |
| _version_ | 1818314060589957120 |
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| author | Tatsuma Sakaguchi Yoshinori Hamada Takeshi Shirai Hiroshi Hamada Takashi Doi |
| author_facet | Tatsuma Sakaguchi Yoshinori Hamada Takeshi Shirai Hiroshi Hamada Takashi Doi |
| author_sort | Tatsuma Sakaguchi |
| collection | DOAJ |
| description | We report here two cases of Kasai type IIIa biliary atresia (BA), associated with pancreaticobiliary maljunction (PBM). Both cases were referred to our hospital because of hyperbilirubinemia and diagnosed with BA preoperatively by abdominal ultrasonography and biliary scintigraphy. They underwent Kasai portojejunostomy at 49 and 37 days old, respectively. Intraoperative cholangiographies performed from their gallbladders clarified Kasai type IIIa BA with PBM. Laboratory test of colorless fluid from the gallbladder of one patient showed high level of lipase (460 U/L). Reported cases of BA associated with PBM are rare and this is a second report showed elevated level of a pancreatic enzyme in bile. The findings in our cases indicate the pathogenesis of biliary anomaly in association with PBM. Keywords: Kasai type IIIa biliary atresia, Pancreaticobiliary maljunction, Infantile obstructive cholangiopathy |
| first_indexed | 2024-12-13T08:43:38Z |
| format | Article |
| id | doaj.art-4aab11c200294a7baf4d0d2a8d2bd942 |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-12-13T08:43:38Z |
| publishDate | 2018-12-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-4aab11c200294a7baf4d0d2a8d2bd9422022-12-21T23:53:29ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662018-12-01394852Biliary atresia associated with pancreaticobiliary maljunctionTatsuma Sakaguchi0Yoshinori Hamada1Takeshi Shirai2Hiroshi Hamada3Takashi Doi4Corresponding author. 2-5-1 Shinmachi, Hirakata, Osaka, 573-1191, Japan.; Division of Pediatric Surgery, Department of Surgery, Kansai Medical University, Hirakata, Osaka, JapanDivision of Pediatric Surgery, Department of Surgery, Kansai Medical University, Hirakata, Osaka, JapanDivision of Pediatric Surgery, Department of Surgery, Kansai Medical University, Hirakata, Osaka, JapanDivision of Pediatric Surgery, Department of Surgery, Kansai Medical University, Hirakata, Osaka, JapanDivision of Pediatric Surgery, Department of Surgery, Kansai Medical University, Hirakata, Osaka, JapanWe report here two cases of Kasai type IIIa biliary atresia (BA), associated with pancreaticobiliary maljunction (PBM). Both cases were referred to our hospital because of hyperbilirubinemia and diagnosed with BA preoperatively by abdominal ultrasonography and biliary scintigraphy. They underwent Kasai portojejunostomy at 49 and 37 days old, respectively. Intraoperative cholangiographies performed from their gallbladders clarified Kasai type IIIa BA with PBM. Laboratory test of colorless fluid from the gallbladder of one patient showed high level of lipase (460 U/L). Reported cases of BA associated with PBM are rare and this is a second report showed elevated level of a pancreatic enzyme in bile. The findings in our cases indicate the pathogenesis of biliary anomaly in association with PBM. Keywords: Kasai type IIIa biliary atresia, Pancreaticobiliary maljunction, Infantile obstructive cholangiopathyhttp://www.sciencedirect.com/science/article/pii/S221357661830263X |
| spellingShingle | Tatsuma Sakaguchi Yoshinori Hamada Takeshi Shirai Hiroshi Hamada Takashi Doi Biliary atresia associated with pancreaticobiliary maljunction Journal of Pediatric Surgery Case Reports |
| title | Biliary atresia associated with pancreaticobiliary maljunction |
| title_full | Biliary atresia associated with pancreaticobiliary maljunction |
| title_fullStr | Biliary atresia associated with pancreaticobiliary maljunction |
| title_full_unstemmed | Biliary atresia associated with pancreaticobiliary maljunction |
| title_short | Biliary atresia associated with pancreaticobiliary maljunction |
| title_sort | biliary atresia associated with pancreaticobiliary maljunction |
| url | http://www.sciencedirect.com/science/article/pii/S221357661830263X |
| work_keys_str_mv | AT tatsumasakaguchi biliaryatresiaassociatedwithpancreaticobiliarymaljunction AT yoshinorihamada biliaryatresiaassociatedwithpancreaticobiliarymaljunction AT takeshishirai biliaryatresiaassociatedwithpancreaticobiliarymaljunction AT hiroshihamada biliaryatresiaassociatedwithpancreaticobiliarymaljunction AT takashidoi biliaryatresiaassociatedwithpancreaticobiliarymaljunction |