Anesthetic management of a patient with Osler-Weber-Rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement: a case report
Abstract Background Osler-Weber-Rendu syndrome is characterized by mucocutaneous telangiectasia and arteriovenous malformations in organs. Anesthesia for patients with Osler-Weber-Rendu syndrome is challenging due to complications and physiological changes. Case presentation The case was a 49-year-o...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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SpringerOpen
2023-02-01
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| Series: | JA Clinical Reports |
| Subjects: | |
| Online Access: | https://doi.org/10.1186/s40981-023-00600-4 |
| _version_ | 1811165994105700352 |
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| author | Toshiharu Hiyoshi Kazuyoshi Shimizu Satoshi Kimura Toshiki Naritani Hiroshi Morimatsu |
| author_facet | Toshiharu Hiyoshi Kazuyoshi Shimizu Satoshi Kimura Toshiki Naritani Hiroshi Morimatsu |
| author_sort | Toshiharu Hiyoshi |
| collection | DOAJ |
| description | Abstract Background Osler-Weber-Rendu syndrome is characterized by mucocutaneous telangiectasia and arteriovenous malformations in organs. Anesthesia for patients with Osler-Weber-Rendu syndrome is challenging due to complications and physiological changes. Case presentation The case was a 49-year-old female with Osler-Weber-Rendu syndrome, multiple pulmonary arteriovenous malformations and pheochromocytoma who presented for femoral bone head fracture with metastatic adenocarcinoma. The patient was scheduled to undergo bone tumor resection and artificial bone replacement, being positioned laterally with a planned operation duration of 5 h. Anesthesia was managed with spinal and epidural anesthesia, combined with sedation by sevoflurane using a supraglottic airway (SGA) device under spontaneous breathing. Her intraoperative and postoperative courses were uneventful. Conclusion Neuraxial anesthesia combined with general anesthesia using an SGA device to maintain spontaneous ventilation in order to minimize the risk of rupture of pulmonary arteriovenous malformations could be an option. |
| first_indexed | 2024-04-10T15:46:16Z |
| format | Article |
| id | doaj.art-4d6d698be1e4461f803cf1d03bc2595d |
| institution | Directory Open Access Journal |
| issn | 2363-9024 |
| language | English |
| last_indexed | 2024-04-10T15:46:16Z |
| publishDate | 2023-02-01 |
| publisher | SpringerOpen |
| record_format | Article |
| series | JA Clinical Reports |
| spelling | doaj.art-4d6d698be1e4461f803cf1d03bc2595d2023-02-12T12:06:27ZengSpringerOpenJA Clinical Reports2363-90242023-02-01911510.1186/s40981-023-00600-4Anesthetic management of a patient with Osler-Weber-Rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement: a case reportToshiharu Hiyoshi0Kazuyoshi Shimizu1Satoshi Kimura2Toshiki Naritani3Hiroshi Morimatsu4Department of Anesthesiology and Resuscitology, Okayama University HospitalDepartment of Anesthesiology and Resuscitology, Okayama University HospitalDepartment of Anesthesiology and Resuscitology, Okayama University HospitalDepartment of Anesthesiology and Resuscitology, Okayama University HospitalDepartment of Anesthesiology and Resuscitology, Okayama University HospitalAbstract Background Osler-Weber-Rendu syndrome is characterized by mucocutaneous telangiectasia and arteriovenous malformations in organs. Anesthesia for patients with Osler-Weber-Rendu syndrome is challenging due to complications and physiological changes. Case presentation The case was a 49-year-old female with Osler-Weber-Rendu syndrome, multiple pulmonary arteriovenous malformations and pheochromocytoma who presented for femoral bone head fracture with metastatic adenocarcinoma. The patient was scheduled to undergo bone tumor resection and artificial bone replacement, being positioned laterally with a planned operation duration of 5 h. Anesthesia was managed with spinal and epidural anesthesia, combined with sedation by sevoflurane using a supraglottic airway (SGA) device under spontaneous breathing. Her intraoperative and postoperative courses were uneventful. Conclusion Neuraxial anesthesia combined with general anesthesia using an SGA device to maintain spontaneous ventilation in order to minimize the risk of rupture of pulmonary arteriovenous malformations could be an option.https://doi.org/10.1186/s40981-023-00600-4Osler-Weber-Rendu syndromeArteriovenous malformationsGeneral anesthesiaNeuraxial anesthesia |
| spellingShingle | Toshiharu Hiyoshi Kazuyoshi Shimizu Satoshi Kimura Toshiki Naritani Hiroshi Morimatsu Anesthetic management of a patient with Osler-Weber-Rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement: a case report JA Clinical Reports Osler-Weber-Rendu syndrome Arteriovenous malformations General anesthesia Neuraxial anesthesia |
| title | Anesthetic management of a patient with Osler-Weber-Rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement: a case report |
| title_full | Anesthetic management of a patient with Osler-Weber-Rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement: a case report |
| title_fullStr | Anesthetic management of a patient with Osler-Weber-Rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement: a case report |
| title_full_unstemmed | Anesthetic management of a patient with Osler-Weber-Rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement: a case report |
| title_short | Anesthetic management of a patient with Osler-Weber-Rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement: a case report |
| title_sort | anesthetic management of a patient with osler weber rendu syndrome with multiple pulmonary arteriovenous malformations and pheochromocytoma for femoral artificial bone replacement a case report |
| topic | Osler-Weber-Rendu syndrome Arteriovenous malformations General anesthesia Neuraxial anesthesia |
| url | https://doi.org/10.1186/s40981-023-00600-4 |
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