Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients
Summary:. Cherubism is a rare, autosomal dominant condition characterized by the replacement of medullary bone by fibro-osseous lesions, predominantly in the bilateral maxillae and/or mandibles. The clinical presentation of cherubism can vary widely, from clinically undetectable to severe facial dis...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer
2022-01-01
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| Series: | Plastic and Reconstructive Surgery, Global Open |
| Online Access: | http://journals.lww.com/prsgo/fulltext/10.1097/GOX.0000000000004079 |
| _version_ | 1818476368633004032 |
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| author | Whitney Moss, MD Giovanna Pires, BA Rehan Zahid, MD Richard Tyrell, MD Irfan Rhemtulla, MD Barbu Gociman, MD, PhD |
| author_facet | Whitney Moss, MD Giovanna Pires, BA Rehan Zahid, MD Richard Tyrell, MD Irfan Rhemtulla, MD Barbu Gociman, MD, PhD |
| author_sort | Whitney Moss, MD |
| collection | DOAJ |
| description | Summary:. Cherubism is a rare, autosomal dominant condition characterized by the replacement of medullary bone by fibro-osseous lesions, predominantly in the bilateral maxillae and/or mandibles. The clinical presentation of cherubism can vary widely, from clinically undetectable to severe facial disfigurement. Although there are no established management guidelines for this condition, conservative management with observation is typically favored in most cases due to the possibility of spontaneous regression following puberty. In this article, we present three cases of moderate to severe cherubism managed with early surgical intervention utilizing curettage and osteotomy followed by bony repositioning. We aimed to show the feasibility and safety of this minimally invasive surgical technique in the management of moderate to severe cases of cherubism to provide improvement in patient quality of life, aesthetics, and function while also possibly mitigating the need for later reconstructive surgery. |
| first_indexed | 2024-12-10T09:24:43Z |
| format | Article |
| id | doaj.art-4d91c13d174543caa2ff9fd0c31369ee |
| institution | Directory Open Access Journal |
| issn | 2169-7574 |
| language | English |
| last_indexed | 2024-12-10T09:24:43Z |
| publishDate | 2022-01-01 |
| publisher | Wolters Kluwer |
| record_format | Article |
| series | Plastic and Reconstructive Surgery, Global Open |
| spelling | doaj.art-4d91c13d174543caa2ff9fd0c31369ee2022-12-22T01:54:34ZengWolters KluwerPlastic and Reconstructive Surgery, Global Open2169-75742022-01-01101e407910.1097/GOX.0000000000004079202201000-00063Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three PatientsWhitney Moss, MD0Giovanna Pires, BA1Rehan Zahid, MD2Richard Tyrell, MD3Irfan Rhemtulla, MD4Barbu Gociman, MD, PhD5From the * Division of Plastic and Reconstructive Surgery, Department of Surgery, University of Utah School of Medicine, Salt Lake City, UtahFrom the * Division of Plastic and Reconstructive Surgery, Department of Surgery, University of Utah School of Medicine, Salt Lake City, UtahFrom the * Division of Plastic and Reconstructive Surgery, Department of Surgery, University of Utah School of Medicine, Salt Lake City, Utah† Division of Plastic Surgery, Department of Surgery, Lewis Katz School of Medicine at Temple University, Philadelphia, Pa.From the * Division of Plastic and Reconstructive Surgery, Department of Surgery, University of Utah School of Medicine, Salt Lake City, UtahFrom the * Division of Plastic and Reconstructive Surgery, Department of Surgery, University of Utah School of Medicine, Salt Lake City, UtahSummary:. Cherubism is a rare, autosomal dominant condition characterized by the replacement of medullary bone by fibro-osseous lesions, predominantly in the bilateral maxillae and/or mandibles. The clinical presentation of cherubism can vary widely, from clinically undetectable to severe facial disfigurement. Although there are no established management guidelines for this condition, conservative management with observation is typically favored in most cases due to the possibility of spontaneous regression following puberty. In this article, we present three cases of moderate to severe cherubism managed with early surgical intervention utilizing curettage and osteotomy followed by bony repositioning. We aimed to show the feasibility and safety of this minimally invasive surgical technique in the management of moderate to severe cases of cherubism to provide improvement in patient quality of life, aesthetics, and function while also possibly mitigating the need for later reconstructive surgery.http://journals.lww.com/prsgo/fulltext/10.1097/GOX.0000000000004079 |
| spellingShingle | Whitney Moss, MD Giovanna Pires, BA Rehan Zahid, MD Richard Tyrell, MD Irfan Rhemtulla, MD Barbu Gociman, MD, PhD Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients Plastic and Reconstructive Surgery, Global Open |
| title | Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients |
| title_full | Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients |
| title_fullStr | Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients |
| title_full_unstemmed | Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients |
| title_short | Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients |
| title_sort | severe cherubism treated with curettage osteotomy and bony repositioning a case series of three patients |
| url | http://journals.lww.com/prsgo/fulltext/10.1097/GOX.0000000000004079 |
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