A case of Herlyn-Werner-Wunderlich syndrome: a rare, congenital genitourinary anomaly in a 12-year-old girl
Herlyn-Werner-Wunderlich (HWW) syndrome is a rare, congenital genitourinary anomaly involving the Müllerian and Wolffian structures, and is characterized by the triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents in adolescent girls in whom hematome...
| Main Authors: | , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Korean Society of Pediatric Emergency Medicine
2016-06-01
|
| Series: | Pediatric Emergency Medicine Journal |
| Subjects: | |
| Online Access: | http://pemj.org/upload/pdf/pemj-3-1-32.pdf |
| _version_ | 1797852241141432320 |
|---|---|
| author | Joong Wan Park Jae Yun Jung |
| author_facet | Joong Wan Park Jae Yun Jung |
| author_sort | Joong Wan Park |
| collection | DOAJ |
| description | Herlyn-Werner-Wunderlich (HWW) syndrome is a rare, congenital genitourinary anomaly involving the Müllerian and Wolffian structures, and is characterized by the triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents in adolescent girls in whom hematometrocolpos produces a pronounced mass effect and pain on the side of the obstructed hemivagina. Accurate diagnosis and surgical treatment can be delayed for several months or even years. Here, we report a case of a 12-year-old girl who presented to the emergency department with lower abdominal pain and mass that had lasted for 2 weeks. After the confirmation of HWW syndrome with magnetic resonance imaging, hysteroscopic septostomy was carried out as a definitive treatment. When we evaluate adolescent girls with lower abdominal pain and mass, we should consider the possibility of HWW syndrome. |
| first_indexed | 2024-04-09T19:30:52Z |
| format | Article |
| id | doaj.art-4de455a649b0436c83f865af4a20317a |
| institution | Directory Open Access Journal |
| issn | 2383-4897 |
| language | English |
| last_indexed | 2024-04-09T19:30:52Z |
| publishDate | 2016-06-01 |
| publisher | Korean Society of Pediatric Emergency Medicine |
| record_format | Article |
| series | Pediatric Emergency Medicine Journal |
| spelling | doaj.art-4de455a649b0436c83f865af4a20317a2023-04-04T23:43:47ZengKorean Society of Pediatric Emergency MedicinePediatric Emergency Medicine Journal2383-48972016-06-0131323510.22470/pemj.2016.3.1.322A case of Herlyn-Werner-Wunderlich syndrome: a rare, congenital genitourinary anomaly in a 12-year-old girlJoong Wan Park0Jae Yun Jung1Department of Emergency Medicine, Seoul National University Bundang Hospital, Seongnam, KoreaDepartment of Emergency Medicine, Seoul National University College of Medicine, Seoul, KoreaHerlyn-Werner-Wunderlich (HWW) syndrome is a rare, congenital genitourinary anomaly involving the Müllerian and Wolffian structures, and is characterized by the triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents in adolescent girls in whom hematometrocolpos produces a pronounced mass effect and pain on the side of the obstructed hemivagina. Accurate diagnosis and surgical treatment can be delayed for several months or even years. Here, we report a case of a 12-year-old girl who presented to the emergency department with lower abdominal pain and mass that had lasted for 2 weeks. After the confirmation of HWW syndrome with magnetic resonance imaging, hysteroscopic septostomy was carried out as a definitive treatment. When we evaluate adolescent girls with lower abdominal pain and mass, we should consider the possibility of HWW syndrome.http://pemj.org/upload/pdf/pemj-3-1-32.pdfhematocolposhereditary renal agenesismullerian ductsuterine anomalieswolffian ducts |
| spellingShingle | Joong Wan Park Jae Yun Jung A case of Herlyn-Werner-Wunderlich syndrome: a rare, congenital genitourinary anomaly in a 12-year-old girl Pediatric Emergency Medicine Journal hematocolpos hereditary renal agenesis mullerian ducts uterine anomalies wolffian ducts |
| title | A case of Herlyn-Werner-Wunderlich syndrome: a rare, congenital genitourinary anomaly in a 12-year-old girl |
| title_full | A case of Herlyn-Werner-Wunderlich syndrome: a rare, congenital genitourinary anomaly in a 12-year-old girl |
| title_fullStr | A case of Herlyn-Werner-Wunderlich syndrome: a rare, congenital genitourinary anomaly in a 12-year-old girl |
| title_full_unstemmed | A case of Herlyn-Werner-Wunderlich syndrome: a rare, congenital genitourinary anomaly in a 12-year-old girl |
| title_short | A case of Herlyn-Werner-Wunderlich syndrome: a rare, congenital genitourinary anomaly in a 12-year-old girl |
| title_sort | case of herlyn werner wunderlich syndrome a rare congenital genitourinary anomaly in a 12 year old girl |
| topic | hematocolpos hereditary renal agenesis mullerian ducts uterine anomalies wolffian ducts |
| url | http://pemj.org/upload/pdf/pemj-3-1-32.pdf |
| work_keys_str_mv | AT joongwanpark acaseofherlynwernerwunderlichsyndromeararecongenitalgenitourinaryanomalyina12yearoldgirl AT jaeyunjung acaseofherlynwernerwunderlichsyndromeararecongenitalgenitourinaryanomalyina12yearoldgirl AT joongwanpark caseofherlynwernerwunderlichsyndromeararecongenitalgenitourinaryanomalyina12yearoldgirl AT jaeyunjung caseofherlynwernerwunderlichsyndromeararecongenitalgenitourinaryanomalyina12yearoldgirl |