Perioperative considerations of pyruvate dehydrogenase complex deficiency: a case report of two consecutive anesthesia
Background Pyruvate dehydrogenase complex (PDHC) deficiency is a rare mitochondrial disorder caused by a genetic mutation affecting the activity of the PDHC enzyme, which plays a major role in the tricarboxylic cycle. Few cases of surgery or anesthesia have been reported. Moreover, there is no recom...
Main Authors: | Won Yong Lim, Hyeon-Jeong Lee, Eun Ji Park, Soeun Jeon, Wangseok Do, Hyae Jin Kim, Dowon Lee, Jeong-Min Hong |
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Format: | Article |
Language: | English |
Published: |
Korean Society of Anesthesiologists
2023-07-01
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Series: | Anesthesia and Pain Medicine |
Subjects: | |
Online Access: | http://www.anesth-pain-med.org/upload/pdf/apm-23034.pdf |
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