Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case report
Background Congenital central hypoventilation syndrome (CCHS) is a rare disorder characterized by alveolar hypoventilation and autonomic dysregulation. Patients with CCHS have adequate ventilation while awake but exhibit hypoventilation while asleep. More severely affected patients exhibit hypoventi...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Korean Society of Anesthesiologists
2019-08-01
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| Series: | Korean Journal of Anesthesiology |
| Subjects: | |
| Online Access: | http://ekja.org/upload/pdf/kja-d-18-00118.pdf |
| _version_ | 1819265308647489536 |
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| author | Yongjoon Choi Sunam Lee Jiyeon Lee Seongwon Woo |
| author_facet | Yongjoon Choi Sunam Lee Jiyeon Lee Seongwon Woo |
| author_sort | Yongjoon Choi |
| collection | DOAJ |
| description | Background Congenital central hypoventilation syndrome (CCHS) is a rare disorder characterized by alveolar hypoventilation and autonomic dysregulation. Patients with CCHS have adequate ventilation while awake but exhibit hypoventilation while asleep. More severely affected patients exhibit hypoventilation both when awake and when asleep. Case Here, we report a case of successful spinal anesthesia and postoperative epidural analgesia in a patient with CCHS who underwent orthostatic surgery. Conclusions In patients with CCHS, anesthesia is used with the goal of minimizing respiratory depression to avoid prolonged mechanical ventilation. Regional anesthesia should be considered where appropriate. Continuous oxygen saturation and end-tidal carbon dioxide monitoring must be available. |
| first_indexed | 2024-12-23T20:43:19Z |
| format | Article |
| id | doaj.art-4f69e25b3403475aa5e9b5e8249f1a45 |
| institution | Directory Open Access Journal |
| issn | 2005-6419 2005-7563 |
| language | English |
| last_indexed | 2024-12-23T20:43:19Z |
| publishDate | 2019-08-01 |
| publisher | Korean Society of Anesthesiologists |
| record_format | Article |
| series | Korean Journal of Anesthesiology |
| spelling | doaj.art-4f69e25b3403475aa5e9b5e8249f1a452022-12-21T17:31:52ZengKorean Society of AnesthesiologistsKorean Journal of Anesthesiology2005-64192005-75632019-08-0172437538010.4097/kja.d.18.001188484Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case reportYongjoon ChoiSunam LeeJiyeon LeeSeongwon WooBackground Congenital central hypoventilation syndrome (CCHS) is a rare disorder characterized by alveolar hypoventilation and autonomic dysregulation. Patients with CCHS have adequate ventilation while awake but exhibit hypoventilation while asleep. More severely affected patients exhibit hypoventilation both when awake and when asleep. Case Here, we report a case of successful spinal anesthesia and postoperative epidural analgesia in a patient with CCHS who underwent orthostatic surgery. Conclusions In patients with CCHS, anesthesia is used with the goal of minimizing respiratory depression to avoid prolonged mechanical ventilation. Regional anesthesia should be considered where appropriate. Continuous oxygen saturation and end-tidal carbon dioxide monitoring must be available.http://ekja.org/upload/pdf/kja-d-18-00118.pdfautonomic dysregulationcongenital central hypoventilation syndromehypoxemiaondine’s cursespinal anesthesia |
| spellingShingle | Yongjoon Choi Sunam Lee Jiyeon Lee Seongwon Woo Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case report Korean Journal of Anesthesiology autonomic dysregulation congenital central hypoventilation syndrome hypoxemia ondine’s curse spinal anesthesia |
| title | Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case report |
| title_full | Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case report |
| title_fullStr | Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case report |
| title_full_unstemmed | Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case report |
| title_short | Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case report |
| title_sort | spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome a case report |
| topic | autonomic dysregulation congenital central hypoventilation syndrome hypoxemia ondine’s curse spinal anesthesia |
| url | http://ekja.org/upload/pdf/kja-d-18-00118.pdf |
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