A case report of anesthesia management in the liver transplantation recipient with porphyria -A case report-
Porphyrias are a group of diseases characterized by an enzyme deficiency in the heme biosynthesis pathway, resulting in accumulation of precursor molecules in the tissue. Some porphyric patients develop progressive liver disease that requires liver transplantation. This case report describes special...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Korean Society of Anesthesiologists
2012-01-01
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| Series: | Korean Journal of Anesthesiology |
| Subjects: | |
| Online Access: | http://ekja.org/upload/pdf/kjae-62-83.pdf |
| _version_ | 1818417280847970304 |
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| author | Hye Won Song Young Hee Shin Justin Sangwook Ko Mi Sook Gwak Gaab Soo Kim |
| author_facet | Hye Won Song Young Hee Shin Justin Sangwook Ko Mi Sook Gwak Gaab Soo Kim |
| author_sort | Hye Won Song |
| collection | DOAJ |
| description | Porphyrias are a group of diseases characterized by an enzyme deficiency in the heme biosynthesis pathway, resulting in accumulation of precursor molecules in the tissue. Some porphyric patients develop progressive liver disease that requires liver transplantation. This case report describes special anesthetic challenges, including careful selection of drugs and the use of special filters that can exclude harmful wavelengths of ultraviolet, in a patient with porphyria who underwent living donor liver transplantation. Understanding the patient's status and disease process, and avoiding triggering factors of porphyria attacks, are important for successful liver transplantation anesthesia in patients with porphyria. |
| first_indexed | 2024-12-14T12:04:17Z |
| format | Article |
| id | doaj.art-4f9440a13abc4918bed5bb2b75e79615 |
| institution | Directory Open Access Journal |
| issn | 2005-6419 2005-7563 |
| language | English |
| last_indexed | 2024-12-14T12:04:17Z |
| publishDate | 2012-01-01 |
| publisher | Korean Society of Anesthesiologists |
| record_format | Article |
| series | Korean Journal of Anesthesiology |
| spelling | doaj.art-4f9440a13abc4918bed5bb2b75e796152022-12-21T23:01:55ZengKorean Society of AnesthesiologistsKorean Journal of Anesthesiology2005-64192005-75632012-01-01621838610.4097/kjae.2012.62.1.837370A case report of anesthesia management in the liver transplantation recipient with porphyria -A case report-Hye Won Song0Young Hee Shin1Justin Sangwook Ko2Mi Sook Gwak3Gaab Soo Kim4Department of Anesthesiology and Pain Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.Department of Anesthesiology and Pain Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.Department of Anesthesiology and Pain Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.Department of Anesthesiology and Pain Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.Department of Anesthesiology and Pain Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.Porphyrias are a group of diseases characterized by an enzyme deficiency in the heme biosynthesis pathway, resulting in accumulation of precursor molecules in the tissue. Some porphyric patients develop progressive liver disease that requires liver transplantation. This case report describes special anesthetic challenges, including careful selection of drugs and the use of special filters that can exclude harmful wavelengths of ultraviolet, in a patient with porphyria who underwent living donor liver transplantation. Understanding the patient's status and disease process, and avoiding triggering factors of porphyria attacks, are important for successful liver transplantation anesthesia in patients with porphyria.http://ekja.org/upload/pdf/kjae-62-83.pdffiltersliver transplantationporphyria |
| spellingShingle | Hye Won Song Young Hee Shin Justin Sangwook Ko Mi Sook Gwak Gaab Soo Kim A case report of anesthesia management in the liver transplantation recipient with porphyria -A case report- Korean Journal of Anesthesiology filters liver transplantation porphyria |
| title | A case report of anesthesia management in the liver transplantation recipient with porphyria -A case report- |
| title_full | A case report of anesthesia management in the liver transplantation recipient with porphyria -A case report- |
| title_fullStr | A case report of anesthesia management in the liver transplantation recipient with porphyria -A case report- |
| title_full_unstemmed | A case report of anesthesia management in the liver transplantation recipient with porphyria -A case report- |
| title_short | A case report of anesthesia management in the liver transplantation recipient with porphyria -A case report- |
| title_sort | case report of anesthesia management in the liver transplantation recipient with porphyria a case report |
| topic | filters liver transplantation porphyria |
| url | http://ekja.org/upload/pdf/kjae-62-83.pdf |
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