Cleidocranial dysplasia: a case report

Introdution: Cleido cranial Dysplasia (CCD) is a rare autosomal dominant disorder affecting skull and clavicle and may be accompanied by some other skeletal abnormalities. Additionally, delayed tooth development associated with presence of supernumerary teeth has been reported. It is an uncommon dis...

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Main Authors: P Ghalyani, N Sarrafan
Format: Article
Language:fas
Published: Isfahan University of Medical Sciences 2009-01-01
Series:مجله دانشکده دندانپزشکی اصفهان
Subjects:
Online Access:http://jids.mui.ac.ir/index.php/jids/article/view/144
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author P Ghalyani
N Sarrafan
author_facet P Ghalyani
N Sarrafan
author_sort P Ghalyani
collection DOAJ
description Introdution: Cleido cranial Dysplasia (CCD) is a rare autosomal dominant disorder affecting skull and clavicle and may be accompanied by some other skeletal abnormalities. Additionally, delayed tooth development associated with presence of supernumerary teeth has been reported. It is an uncommon disorder with the prevalence being 0.5% per 100'000 live births.Case report: The patient was a 19-year old boy referred to the Department of Oral Medicine of Isfahan Dental College. His chief complaint was an unknown pain in the left side of Maxilla. His intraoral examination revealed presence of deciduous teeth and crowding, missing in permanent teeth. Upon general examination, it was found that he had an abnormal clavicle with hypertelorism and patent anterior fontanel. Panoramic radiography revealed multiple completely impacted supernumerary teeth.Conclusion: Clediocranial dyplasia is a rare skeletal disorder. However, its clinical and radiological manifestations are characteristic. Although this disorder is benign, it must be remembered that abnormal dentition may result in dental caries. For eruption of impacted teeth, especially in young patients, surgical exposure is preferred. Orthodontic occlusal movement must be done for restoring the compatible with normal dental. Keywords: Cliedocranial dysplasia, impacted teeth, multiple supernumerary teeth.
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spelling doaj.art-50a87147e31b4800aaad180ea73189a12023-08-02T02:29:23ZfasIsfahan University of Medical Sciencesمجله دانشکده دندانپزشکی اصفهان1735-255X2008-69892009-01-0144219222Cleidocranial dysplasia: a case reportP GhalyaniN SarrafanIntrodution: Cleido cranial Dysplasia (CCD) is a rare autosomal dominant disorder affecting skull and clavicle and may be accompanied by some other skeletal abnormalities. Additionally, delayed tooth development associated with presence of supernumerary teeth has been reported. It is an uncommon disorder with the prevalence being 0.5% per 100'000 live births.Case report: The patient was a 19-year old boy referred to the Department of Oral Medicine of Isfahan Dental College. His chief complaint was an unknown pain in the left side of Maxilla. His intraoral examination revealed presence of deciduous teeth and crowding, missing in permanent teeth. Upon general examination, it was found that he had an abnormal clavicle with hypertelorism and patent anterior fontanel. Panoramic radiography revealed multiple completely impacted supernumerary teeth.Conclusion: Clediocranial dyplasia is a rare skeletal disorder. However, its clinical and radiological manifestations are characteristic. Although this disorder is benign, it must be remembered that abnormal dentition may result in dental caries. For eruption of impacted teeth, especially in young patients, surgical exposure is preferred. Orthodontic occlusal movement must be done for restoring the compatible with normal dental. Keywords: Cliedocranial dysplasia, impacted teeth, multiple supernumerary teeth.http://jids.mui.ac.ir/index.php/jids/article/view/144Keywords: Cliedocranial dysplasiaimpacted teethmultiple supernumerary teeth.
spellingShingle P Ghalyani
N Sarrafan
Cleidocranial dysplasia: a case report
مجله دانشکده دندانپزشکی اصفهان
Keywords: Cliedocranial dysplasia
impacted teeth
multiple supernumerary teeth.
title Cleidocranial dysplasia: a case report
title_full Cleidocranial dysplasia: a case report
title_fullStr Cleidocranial dysplasia: a case report
title_full_unstemmed Cleidocranial dysplasia: a case report
title_short Cleidocranial dysplasia: a case report
title_sort cleidocranial dysplasia a case report
topic Keywords: Cliedocranial dysplasia
impacted teeth
multiple supernumerary teeth.
url http://jids.mui.ac.ir/index.php/jids/article/view/144
work_keys_str_mv AT pghalyani cleidocranialdysplasiaacasereport
AT nsarrafan cleidocranialdysplasiaacasereport