Cleidocranial dysplasia: a case report
Introdution: Cleido cranial Dysplasia (CCD) is a rare autosomal dominant disorder affecting skull and clavicle and may be accompanied by some other skeletal abnormalities. Additionally, delayed tooth development associated with presence of supernumerary teeth has been reported. It is an uncommon dis...
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Format: | Article |
Language: | fas |
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Isfahan University of Medical Sciences
2009-01-01
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Series: | مجله دانشکده دندانپزشکی اصفهان |
Subjects: | |
Online Access: | http://jids.mui.ac.ir/index.php/jids/article/view/144 |
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author | P Ghalyani N Sarrafan |
author_facet | P Ghalyani N Sarrafan |
author_sort | P Ghalyani |
collection | DOAJ |
description | Introdution: Cleido cranial Dysplasia (CCD) is a rare autosomal dominant disorder affecting skull and clavicle and may be accompanied by some other skeletal abnormalities. Additionally, delayed tooth development associated with presence of supernumerary teeth has been reported. It is an uncommon disorder with the prevalence being 0.5% per 100'000 live births.Case report: The patient was a 19-year old boy referred to the Department of Oral Medicine of Isfahan Dental College. His chief complaint was an unknown pain in the left side of Maxilla. His intraoral examination revealed presence of deciduous teeth and crowding, missing in permanent teeth. Upon general examination, it was found that he had an abnormal clavicle with hypertelorism and patent anterior fontanel. Panoramic radiography revealed multiple completely impacted supernumerary teeth.Conclusion: Clediocranial dyplasia is a rare skeletal disorder. However, its clinical and radiological manifestations are characteristic. Although this disorder is benign, it must be remembered that abnormal dentition may result in dental caries. For eruption of impacted teeth, especially in young patients, surgical exposure is preferred. Orthodontic occlusal movement must be done for restoring the compatible with normal dental. Keywords: Cliedocranial dysplasia, impacted teeth, multiple supernumerary teeth. |
first_indexed | 2024-03-12T19:59:45Z |
format | Article |
id | doaj.art-50a87147e31b4800aaad180ea73189a1 |
institution | Directory Open Access Journal |
issn | 1735-255X 2008-6989 |
language | fas |
last_indexed | 2024-03-12T19:59:45Z |
publishDate | 2009-01-01 |
publisher | Isfahan University of Medical Sciences |
record_format | Article |
series | مجله دانشکده دندانپزشکی اصفهان |
spelling | doaj.art-50a87147e31b4800aaad180ea73189a12023-08-02T02:29:23ZfasIsfahan University of Medical Sciencesمجله دانشکده دندانپزشکی اصفهان1735-255X2008-69892009-01-0144219222Cleidocranial dysplasia: a case reportP GhalyaniN SarrafanIntrodution: Cleido cranial Dysplasia (CCD) is a rare autosomal dominant disorder affecting skull and clavicle and may be accompanied by some other skeletal abnormalities. Additionally, delayed tooth development associated with presence of supernumerary teeth has been reported. It is an uncommon disorder with the prevalence being 0.5% per 100'000 live births.Case report: The patient was a 19-year old boy referred to the Department of Oral Medicine of Isfahan Dental College. His chief complaint was an unknown pain in the left side of Maxilla. His intraoral examination revealed presence of deciduous teeth and crowding, missing in permanent teeth. Upon general examination, it was found that he had an abnormal clavicle with hypertelorism and patent anterior fontanel. Panoramic radiography revealed multiple completely impacted supernumerary teeth.Conclusion: Clediocranial dyplasia is a rare skeletal disorder. However, its clinical and radiological manifestations are characteristic. Although this disorder is benign, it must be remembered that abnormal dentition may result in dental caries. For eruption of impacted teeth, especially in young patients, surgical exposure is preferred. Orthodontic occlusal movement must be done for restoring the compatible with normal dental. Keywords: Cliedocranial dysplasia, impacted teeth, multiple supernumerary teeth.http://jids.mui.ac.ir/index.php/jids/article/view/144Keywords: Cliedocranial dysplasiaimpacted teethmultiple supernumerary teeth. |
spellingShingle | P Ghalyani N Sarrafan Cleidocranial dysplasia: a case report مجله دانشکده دندانپزشکی اصفهان Keywords: Cliedocranial dysplasia impacted teeth multiple supernumerary teeth. |
title | Cleidocranial dysplasia: a case report |
title_full | Cleidocranial dysplasia: a case report |
title_fullStr | Cleidocranial dysplasia: a case report |
title_full_unstemmed | Cleidocranial dysplasia: a case report |
title_short | Cleidocranial dysplasia: a case report |
title_sort | cleidocranial dysplasia a case report |
topic | Keywords: Cliedocranial dysplasia impacted teeth multiple supernumerary teeth. |
url | http://jids.mui.ac.ir/index.php/jids/article/view/144 |
work_keys_str_mv | AT pghalyani cleidocranialdysplasiaacasereport AT nsarrafan cleidocranialdysplasiaacasereport |