Giant Lipofibromatous Hamartoma of Median Nerve in a Child
Lipofibromatous hamartoma (LFH) is a rare fibrofatty tumor of adipocytes within peripheral nerves, affecting mainly children. It typically presents as a palpable mass surrounding the nerves of the upper limbs, causing pain and neurological deficits in the affected nerve distribution. We report the...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS)
2023-05-01
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| Series: | Clinical and Biomedical Research |
| Online Access: | https://seer.ufrgs.br/index.php/hcpa/article/view/125914 |
| _version_ | 1797816524609683456 |
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| author | RICARDO VIEIRA TELES FILHO Guilherme de Matos Abe Paulo Henrique de Aquino Júnior Giovanni Ferreira Viggiano Bruna Ribas Teixeira Murilo Eugênio Oliveira |
| author_facet | RICARDO VIEIRA TELES FILHO Guilherme de Matos Abe Paulo Henrique de Aquino Júnior Giovanni Ferreira Viggiano Bruna Ribas Teixeira Murilo Eugênio Oliveira |
| author_sort | RICARDO VIEIRA TELES FILHO |
| collection | DOAJ |
| description |
Lipofibromatous hamartoma (LFH) is a rare fibrofatty tumor of adipocytes within peripheral nerves, affecting mainly children. It typically presents as a palpable mass surrounding the nerves of the upper limbs, causing pain and neurological deficits in the affected nerve distribution. We report the case of a child with a 2-years presentation of a mass in the right wrist associated with pain and paresthesia, who underwent investigation with magnetic resonance imaging (MR I). It showed thickening of the median nerve with spaghetti-like appearance associated with lipomatous tissue in a coaxial cable-like pattern, both features characteristic of LFH. This case illustrates the importance of MRI in the differential diagnosis of limb masses in the pediatric population.
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| first_indexed | 2024-03-13T08:38:59Z |
| format | Article |
| id | doaj.art-5142fc1b338f4e22b28376b426129e81 |
| institution | Directory Open Access Journal |
| issn | 2357-9730 |
| language | English |
| last_indexed | 2024-03-13T08:38:59Z |
| publishDate | 2023-05-01 |
| publisher | Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS) |
| record_format | Article |
| series | Clinical and Biomedical Research |
| spelling | doaj.art-5142fc1b338f4e22b28376b426129e812023-05-30T18:09:25ZengHospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS)Clinical and Biomedical Research2357-97302023-05-01431Giant Lipofibromatous Hamartoma of Median Nerve in a ChildRICARDO VIEIRA TELES FILHOGuilherme de Matos AbePaulo Henrique de Aquino JúniorGiovanni Ferreira ViggianoBruna Ribas TeixeiraMurilo Eugênio Oliveira Lipofibromatous hamartoma (LFH) is a rare fibrofatty tumor of adipocytes within peripheral nerves, affecting mainly children. It typically presents as a palpable mass surrounding the nerves of the upper limbs, causing pain and neurological deficits in the affected nerve distribution. We report the case of a child with a 2-years presentation of a mass in the right wrist associated with pain and paresthesia, who underwent investigation with magnetic resonance imaging (MR I). It showed thickening of the median nerve with spaghetti-like appearance associated with lipomatous tissue in a coaxial cable-like pattern, both features characteristic of LFH. This case illustrates the importance of MRI in the differential diagnosis of limb masses in the pediatric population. https://seer.ufrgs.br/index.php/hcpa/article/view/125914 |
| spellingShingle | RICARDO VIEIRA TELES FILHO Guilherme de Matos Abe Paulo Henrique de Aquino Júnior Giovanni Ferreira Viggiano Bruna Ribas Teixeira Murilo Eugênio Oliveira Giant Lipofibromatous Hamartoma of Median Nerve in a Child Clinical and Biomedical Research |
| title | Giant Lipofibromatous Hamartoma of Median Nerve in a Child |
| title_full | Giant Lipofibromatous Hamartoma of Median Nerve in a Child |
| title_fullStr | Giant Lipofibromatous Hamartoma of Median Nerve in a Child |
| title_full_unstemmed | Giant Lipofibromatous Hamartoma of Median Nerve in a Child |
| title_short | Giant Lipofibromatous Hamartoma of Median Nerve in a Child |
| title_sort | giant lipofibromatous hamartoma of median nerve in a child |
| url | https://seer.ufrgs.br/index.php/hcpa/article/view/125914 |
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