Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case report
Pemphigus vulgaris (PV) is a rare autoimmune disorder characterized by blisters on the mucous membranes and skin. Autoimmunity is an important complication developing in predominantly antibody deficiencies, which is a subgroup of primary immunodeficiencies (PID). Herein, we present a patient with PV...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Galenos Publishing House
2022-06-01
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| Series: | Turkderm Turkish Archives of Dermatology and Venereology |
| Subjects: | |
| Online Access: | https://journal.turkderm.org.tr/jvi.aspx?pdir=turkderm&plng=eng&un=TURKDERM-81370&look4= |
| _version_ | 1797910440853897216 |
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| author | Uğur Hacı Musabak Tuba Erdoğan Mustafa Tunca |
| author_facet | Uğur Hacı Musabak Tuba Erdoğan Mustafa Tunca |
| author_sort | Uğur Hacı Musabak |
| collection | DOAJ |
| description | Pemphigus vulgaris (PV) is a rare autoimmune disorder characterized by blisters on the mucous membranes and skin. Autoimmunity is an important complication developing in predominantly antibody deficiencies, which is a subgroup of primary immunodeficiencies (PID). Herein, we present a patient with PV who had primary antibody deficiency and whose disease relapsed during the maintenance period of conventional immunosuppressive treatments but progressed to remission following high-dose intravenous immunoglobulin therapy. Thus, we aimed to create awareness for the study of primary immunodeficiencies in rare autoimmune bullous diseases. |
| first_indexed | 2024-04-10T11:24:23Z |
| format | Article |
| id | doaj.art-5309481f69e840b0b19a0d80e3996538 |
| institution | Directory Open Access Journal |
| issn | 2651-5164 |
| language | English |
| last_indexed | 2024-04-10T11:24:23Z |
| publishDate | 2022-06-01 |
| publisher | Galenos Publishing House |
| record_format | Article |
| series | Turkderm Turkish Archives of Dermatology and Venereology |
| spelling | doaj.art-5309481f69e840b0b19a0d80e39965382023-02-15T16:18:29ZengGalenos Publishing HouseTurkderm Turkish Archives of Dermatology and Venereology2651-51642022-06-01562808310.4274/turkderm.galenos.2022.81370Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case reportUğur Hacı Musabak0https://orcid.org/0000-0003-1511-7634Tuba Erdoğan1https://orcid.org/0000-0002-3143-2442Mustafa Tunca2https://orcid.org/0000-0003-4253-5110Başkent University Faculty of Medicine, Department of Immunology and Allergy, Ankara, TurkeyBaşkent University Faculty of Medicine, Department of Immunology and Allergy, Ankara, TurkeyUniversity of Health Sciences Turkey, Gülhane Faculty of Medicine, Department of Dermatology, Ankara, TurkeyPemphigus vulgaris (PV) is a rare autoimmune disorder characterized by blisters on the mucous membranes and skin. Autoimmunity is an important complication developing in predominantly antibody deficiencies, which is a subgroup of primary immunodeficiencies (PID). Herein, we present a patient with PV who had primary antibody deficiency and whose disease relapsed during the maintenance period of conventional immunosuppressive treatments but progressed to remission following high-dose intravenous immunoglobulin therapy. Thus, we aimed to create awareness for the study of primary immunodeficiencies in rare autoimmune bullous diseases.https://journal.turkderm.org.tr/jvi.aspx?pdir=turkderm&plng=eng&un=TURKDERM-81370&look4=pemphigus vulgarisprimary antibody deficiencyprimary immune deficiency |
| spellingShingle | Uğur Hacı Musabak Tuba Erdoğan Mustafa Tunca Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case report Turkderm Turkish Archives of Dermatology and Venereology pemphigus vulgaris primary antibody deficiency primary immune deficiency |
| title | Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case report |
| title_full | Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case report |
| title_fullStr | Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case report |
| title_full_unstemmed | Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case report |
| title_short | Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case report |
| title_sort | pemphigus vulgaris in a patient with primary hypogammaglobulinemia a case report |
| topic | pemphigus vulgaris primary antibody deficiency primary immune deficiency |
| url | https://journal.turkderm.org.tr/jvi.aspx?pdir=turkderm&plng=eng&un=TURKDERM-81370&look4= |
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