The confused puzzles in antineutrophil cytoplasmic antibody‐associated vasculitis activity evaluation: A case report

Abstract Antineutrophil cytoplasmic antibody (ANCA)‐associated vasculitis (AAV) is a group of chronic multisystem autoimmune diseases with substantial mortality and morbidity and frequent relapses. The complexity of the disease condition and treatment‐related adverse reactions as well as infections...

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Main Authors: Ai‐hua Zhang, Wei‐long Yao, Wen‐hu Liu
Format: Article
Language:English
Published: Wiley 2021-07-01
Series:Clinical Case Reports
Subjects:
Online Access:https://doi.org/10.1002/ccr3.4497
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author Ai‐hua Zhang
Wei‐long Yao
Wen‐hu Liu
author_facet Ai‐hua Zhang
Wei‐long Yao
Wen‐hu Liu
author_sort Ai‐hua Zhang
collection DOAJ
description Abstract Antineutrophil cytoplasmic antibody (ANCA)‐associated vasculitis (AAV) is a group of chronic multisystem autoimmune diseases with substantial mortality and morbidity and frequent relapses. The complexity of the disease condition and treatment‐related adverse reactions as well as infections play important roles in the poor outcomes. Unfortunately, the subjective symptoms and objective indicators are not fully parallel, and manifestations between disease activity and treatment‐related adverse reactions are often similar. Here, we describe a case of pulmonary mucormycosis in an old female patient with AAV to highlight these challenges.
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spelling doaj.art-530edbb8b97a499fa1eb863652d1d87c2023-03-27T08:34:51ZengWileyClinical Case Reports2050-09042021-07-0197n/an/a10.1002/ccr3.4497The confused puzzles in antineutrophil cytoplasmic antibody‐associated vasculitis activity evaluation: A case reportAi‐hua Zhang0Wei‐long Yao1Wen‐hu Liu2Department of Nephrology Affiliated Beijing Friendship Hospital Nephrology Faculty Capital Medical University Beijing ChinaDepartment of Nephrology Affiliated Beijing Friendship Hospital Nephrology Faculty Capital Medical University Beijing ChinaDepartment of Nephrology Affiliated Beijing Friendship Hospital Nephrology Faculty Capital Medical University Beijing ChinaAbstract Antineutrophil cytoplasmic antibody (ANCA)‐associated vasculitis (AAV) is a group of chronic multisystem autoimmune diseases with substantial mortality and morbidity and frequent relapses. The complexity of the disease condition and treatment‐related adverse reactions as well as infections play important roles in the poor outcomes. Unfortunately, the subjective symptoms and objective indicators are not fully parallel, and manifestations between disease activity and treatment‐related adverse reactions are often similar. Here, we describe a case of pulmonary mucormycosis in an old female patient with AAV to highlight these challenges.https://doi.org/10.1002/ccr3.4497adverse effectANCA‐associated vasculitisdisease activityimmunosuppressive therapyinfectionmucormycosis
spellingShingle Ai‐hua Zhang
Wei‐long Yao
Wen‐hu Liu
The confused puzzles in antineutrophil cytoplasmic antibody‐associated vasculitis activity evaluation: A case report
Clinical Case Reports
adverse effect
ANCA‐associated vasculitis
disease activity
immunosuppressive therapy
infection
mucormycosis
title The confused puzzles in antineutrophil cytoplasmic antibody‐associated vasculitis activity evaluation: A case report
title_full The confused puzzles in antineutrophil cytoplasmic antibody‐associated vasculitis activity evaluation: A case report
title_fullStr The confused puzzles in antineutrophil cytoplasmic antibody‐associated vasculitis activity evaluation: A case report
title_full_unstemmed The confused puzzles in antineutrophil cytoplasmic antibody‐associated vasculitis activity evaluation: A case report
title_short The confused puzzles in antineutrophil cytoplasmic antibody‐associated vasculitis activity evaluation: A case report
title_sort confused puzzles in antineutrophil cytoplasmic antibody associated vasculitis activity evaluation a case report
topic adverse effect
ANCA‐associated vasculitis
disease activity
immunosuppressive therapy
infection
mucormycosis
url https://doi.org/10.1002/ccr3.4497
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