Mesenteric abscess caused by coinfection with Bacillus Calmette-Guérin and Phialemonium sp. in chronic granulomatous disease

Opportunistic infections are life-threatening conditions in immunocompromised patients including those with primary immunodeficiency. We describe a case of X-linked chronic granulomatous disease presenting with mesenteric abscess caused by a coinfection with Bacillus Calmette-Guérin (BCG) and Phiale...

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Main Authors: Hanae Miyazawa, Yusuke Matsuda, Seisho Sakai, Katsuhiko Kamei, Taizo Wada
Format: Article
Language:English
Published: Elsevier 2022-01-01
Series:IDCases
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2214250922000038
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author Hanae Miyazawa
Yusuke Matsuda
Seisho Sakai
Katsuhiko Kamei
Taizo Wada
author_facet Hanae Miyazawa
Yusuke Matsuda
Seisho Sakai
Katsuhiko Kamei
Taizo Wada
author_sort Hanae Miyazawa
collection DOAJ
description Opportunistic infections are life-threatening conditions in immunocompromised patients including those with primary immunodeficiency. We describe a case of X-linked chronic granulomatous disease presenting with mesenteric abscess caused by a coinfection with Bacillus Calmette-Guérin (BCG) and Phialemonium sp. The patient received BCG vaccination at 5 months old. He developed left axillary BCG lymphadenitis at 17 months of age, and 3 months later mesenteric abscess occurred. Concomitant use of rifampicin and itraconazole at 17 months of age might have reduced serum itraconazole concentrations and led to superinfection with Phialemonium sp. in our patient, which was susceptible to itraconazole and voriconazole in vitro. The patient was successfully treated with a combination of isoniazid, rifampicin, streptomycin, ciprofloxacin, prednisolone, interferon-γ, and an increased dose of itraconazole, followed by hematopoietic stem cell transplantation. Our results suggest that clinician need to be aware of rifampicin drug interactions, and that precise detection and identification of pathogens are essential to appropriate treatment.
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spelling doaj.art-551c7a5fdb3a4dab90288563337202ff2022-12-21T18:13:12ZengElsevierIDCases2214-25092022-01-0127e01375Mesenteric abscess caused by coinfection with Bacillus Calmette-Guérin and Phialemonium sp. in chronic granulomatous diseaseHanae Miyazawa0Yusuke Matsuda1Seisho Sakai2Katsuhiko Kamei3Taizo Wada4Department of Pediatrics, School of Medicine, Institute of Medical, Pharmaceutical and Health Sciences, Kanazawa University, 13-1 Takaramachi, Kanazawa 920-8641, Japan; Corresponding author.Department of Pediatrics, School of Medicine, Institute of Medical, Pharmaceutical and Health Sciences, Kanazawa University, 13-1 Takaramachi, Kanazawa 920-8641, JapanDepartment of Pediatric Surgery, Kanazawa University Hospital, 13-1 Takaramachi, Kanazawa 920-8641, JapanMedical Mycology Research Center, Chiba University, 1-8-1 Inohana, Chuo-ku, Chiba 260-8673, JapanDepartment of Pediatrics, School of Medicine, Institute of Medical, Pharmaceutical and Health Sciences, Kanazawa University, 13-1 Takaramachi, Kanazawa 920-8641, JapanOpportunistic infections are life-threatening conditions in immunocompromised patients including those with primary immunodeficiency. We describe a case of X-linked chronic granulomatous disease presenting with mesenteric abscess caused by a coinfection with Bacillus Calmette-Guérin (BCG) and Phialemonium sp. The patient received BCG vaccination at 5 months old. He developed left axillary BCG lymphadenitis at 17 months of age, and 3 months later mesenteric abscess occurred. Concomitant use of rifampicin and itraconazole at 17 months of age might have reduced serum itraconazole concentrations and led to superinfection with Phialemonium sp. in our patient, which was susceptible to itraconazole and voriconazole in vitro. The patient was successfully treated with a combination of isoniazid, rifampicin, streptomycin, ciprofloxacin, prednisolone, interferon-γ, and an increased dose of itraconazole, followed by hematopoietic stem cell transplantation. Our results suggest that clinician need to be aware of rifampicin drug interactions, and that precise detection and identification of pathogens are essential to appropriate treatment.http://www.sciencedirect.com/science/article/pii/S2214250922000038Bacillus Calmette-GuérinChronic granulomatous diseaseCoinfectionMesenteric abscessPhialemonium
spellingShingle Hanae Miyazawa
Yusuke Matsuda
Seisho Sakai
Katsuhiko Kamei
Taizo Wada
Mesenteric abscess caused by coinfection with Bacillus Calmette-Guérin and Phialemonium sp. in chronic granulomatous disease
IDCases
Bacillus Calmette-Guérin
Chronic granulomatous disease
Coinfection
Mesenteric abscess
Phialemonium
title Mesenteric abscess caused by coinfection with Bacillus Calmette-Guérin and Phialemonium sp. in chronic granulomatous disease
title_full Mesenteric abscess caused by coinfection with Bacillus Calmette-Guérin and Phialemonium sp. in chronic granulomatous disease
title_fullStr Mesenteric abscess caused by coinfection with Bacillus Calmette-Guérin and Phialemonium sp. in chronic granulomatous disease
title_full_unstemmed Mesenteric abscess caused by coinfection with Bacillus Calmette-Guérin and Phialemonium sp. in chronic granulomatous disease
title_short Mesenteric abscess caused by coinfection with Bacillus Calmette-Guérin and Phialemonium sp. in chronic granulomatous disease
title_sort mesenteric abscess caused by coinfection with bacillus calmette guerin and phialemonium sp in chronic granulomatous disease
topic Bacillus Calmette-Guérin
Chronic granulomatous disease
Coinfection
Mesenteric abscess
Phialemonium
url http://www.sciencedirect.com/science/article/pii/S2214250922000038
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