Congenital extrahepatic Portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava: A rare case report
Congenital portosystemic shunt (CPS) is a rare vascular anomaly resulting in diversion of splanchnic or portal blood into the systemic circulation. Other vascular malformations associated with this entity are uncommon. A 4-year-old female child with a diagnosis of acute viral hepatitis had an incide...
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| Format: | Article |
| Language: | English |
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Elsevier
2023-08-01
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| Series: | Radiology Case Reports |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043323003321 |
| _version_ | 1797803925002256384 |
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| author | Tesfahunegn Hailemariam, MD Endalew Demilew, MD Tsegahun Manyazewal, PhD Samuel Sisay, MD |
| author_facet | Tesfahunegn Hailemariam, MD Endalew Demilew, MD Tsegahun Manyazewal, PhD Samuel Sisay, MD |
| author_sort | Tesfahunegn Hailemariam, MD |
| collection | DOAJ |
| description | Congenital portosystemic shunt (CPS) is a rare vascular anomaly resulting in diversion of splanchnic or portal blood into the systemic circulation. Other vascular malformations associated with this entity are uncommon. A 4-year-old female child with a diagnosis of acute viral hepatitis had an incidental finding of extrahepatic CPS on a Doppler abdominal ultrasound. Contrast-enhanced computed tomography showed a dilated portal vein having H-type side-to-side communication with a hypoplastic intrahepatic portion of the inferior vena cava and a prominent dilated azygos vein. There was retroaortic left renal vein drained into the IVC which was visualized in its entirety. Echocardiography findings were normal and the patient was discharged after symptomatic treatment that achieved improvement. With the expansion of abdominal imaging, incidental cases of CPS are increasingly being diagnosed in children. Although vascular malformations associated with CPS are rare, early diagnosis of cases helps avoid complications during shunt closure. |
| first_indexed | 2024-03-13T05:29:20Z |
| format | Article |
| id | doaj.art-5598c2ae21944f7e91d08bd5995838f6 |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-03-13T05:29:20Z |
| publishDate | 2023-08-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-5598c2ae21944f7e91d08bd5995838f62023-06-15T04:55:34ZengElsevierRadiology Case Reports1930-04332023-08-0118827502753Congenital extrahepatic Portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava: A rare case reportTesfahunegn Hailemariam, MD0Endalew Demilew, MD1Tsegahun Manyazewal, PhD2Samuel Sisay, MD3Addis Ababa University, School of Medicine, Department of Radiology, 9080, Addis Ababa, Ethiopia; Center for Innovative Drug Development and Therapeutic Trials for Africa (CDT-Africa), Addis Ababa University, College of Health Sciences, Addis Ababa, Ethiopia; Corresponding author.Addis Ababa University, School of Medicine, Department of Radiology, 9080, Addis Ababa, EthiopiaCenter for Innovative Drug Development and Therapeutic Trials for Africa (CDT-Africa), Addis Ababa University, College of Health Sciences, Addis Ababa, EthiopiaAddis Ababa University, School of Medicine, Department of Radiology, 9080, Addis Ababa, EthiopiaCongenital portosystemic shunt (CPS) is a rare vascular anomaly resulting in diversion of splanchnic or portal blood into the systemic circulation. Other vascular malformations associated with this entity are uncommon. A 4-year-old female child with a diagnosis of acute viral hepatitis had an incidental finding of extrahepatic CPS on a Doppler abdominal ultrasound. Contrast-enhanced computed tomography showed a dilated portal vein having H-type side-to-side communication with a hypoplastic intrahepatic portion of the inferior vena cava and a prominent dilated azygos vein. There was retroaortic left renal vein drained into the IVC which was visualized in its entirety. Echocardiography findings were normal and the patient was discharged after symptomatic treatment that achieved improvement. With the expansion of abdominal imaging, incidental cases of CPS are increasingly being diagnosed in children. Although vascular malformations associated with CPS are rare, early diagnosis of cases helps avoid complications during shunt closure.http://www.sciencedirect.com/science/article/pii/S1930043323003321Congenital portosystemic shuntExtrahepatic portosystemic shuntHypoplasiaContrast‐enhanced computed tomography |
| spellingShingle | Tesfahunegn Hailemariam, MD Endalew Demilew, MD Tsegahun Manyazewal, PhD Samuel Sisay, MD Congenital extrahepatic Portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava: A rare case report Radiology Case Reports Congenital portosystemic shunt Extrahepatic portosystemic shunt Hypoplasia Contrast‐enhanced computed tomography |
| title | Congenital extrahepatic Portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava: A rare case report |
| title_full | Congenital extrahepatic Portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava: A rare case report |
| title_fullStr | Congenital extrahepatic Portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava: A rare case report |
| title_full_unstemmed | Congenital extrahepatic Portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava: A rare case report |
| title_short | Congenital extrahepatic Portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava: A rare case report |
| title_sort | congenital extrahepatic portosystemic shunt with hypoplasia of the intrahepatic inferior vena cava a rare case report |
| topic | Congenital portosystemic shunt Extrahepatic portosystemic shunt Hypoplasia Contrast‐enhanced computed tomography |
| url | http://www.sciencedirect.com/science/article/pii/S1930043323003321 |
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