A rare case of alveolar soft-part sarcoma of orbit
Alveolar soft-part sarcoma (ASPS) is a very rare, highly vascular, soft-tissue sarcoma predominantly seen in adolescents and young adults. Orbital involvement is rare, and only few case reports have been published. We report the case of a 12-year-old girl who presented with proptosis of the right ey...
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2020-01-01
|
| Series: | TNOA Journal of Ophthalmic Science and Research |
| Subjects: | |
| Online Access: | http://www.tnoajosr.com/article.asp?issn=2589-4528;year=2020;volume=58;issue=2;spage=115;epage=118;aulast=Rangarajan |
| Summary: | Alveolar soft-part sarcoma (ASPS) is a very rare, highly vascular, soft-tissue sarcoma predominantly seen in adolescents and young adults. Orbital involvement is rare, and only few case reports have been published. We report the case of a 12-year-old girl who presented with proptosis of the right eye of 2 months' duration. Magnetic resonance imaging showed a well-defined lesion in the superolateral right orbit, with the possibility of a hemangioma. Right-eye lateral orbitotomy with excision biopsy of the mass was done. Histopathology revealed ASPS, and the patient was referred for metastatic workup. |
|---|---|
| ISSN: | 2589-4528 2589-4536 |